[Papuloerythroderma of Ofuji with urticarial lesions].
Papuloerythroderma of Ofuji is a rare disease that mainly affects older men of Asiatic origin. Clinically, it is marked by highly pruritic papules which form larger plaques or may give rise to erythroderma. Larger body folds of the abdomen are typically spared (deckchair sign). There is a dispute whether papuloerythroderma of Ofuji represents an own entity or should be regarded as a variant of other inflammatory, neoplastic, or paraneoplastic dermatoses. We present a case of papuloerythroderma of Ofuji in a European patient in which the clinical course as well as the laboratory and histology suggested a relation to mycosis fungoides. Our patient developed pruritic urticarial plaques when systemic corticosteroids were tapered, but cleared complete with cyclosporin A.
Pullmann
Susanne
S
Klinik und Poliklinik für Hautkrankheiten des Universitätsklinikums Münster. pullmann@uni-muenster.de
Luger
Thomas
T
Metze
Dieter
D
D000305:Adrenal Cortex Hormones / Q000627:therapeutic use; D000368:Aged; D016572:Cyclosporine / Q000627:therapeutic use; D003873:Dermatitis, Exfoliative / Q000150:complications* / Q000473:pathology*; D006801:Humans; D007166:Immunosuppressive Agents / Q000627:therapeutic use; D008297:Male; D010257:Paraneoplastic Syndromes / Q000150:complications* / Q000175:diagnosis / Q000473:pathology*; D017444:Skin Diseases, Papulosquamous / Q000150:complications* / Q000188:drug therapy / Q000473:pathology*; D014581:Urticaria / Q000150:complications* / Q000188:drug therapy / Q000473:pathology*
D000305:Adrenal Cortex Hormones; D007166:Immunosuppressive Agents; D016572:Cyclosporine