Diffuse type pulmonary arteriovenous malformations: report of one case.
Pulmonary arteriovenous malformations are direct communications between pulmonary arteries and veins via a tortuous vascular space. They can cause severe pulmonary and neurologic complications. Most PAVMs are located in the lower lobes and can be seen on radiography or angiography. However, a few patients with PAVMs have a more severe and diffuse pattern of disease. These patients generally present with more profound cyanosis and a poorer prognosis. The widespread distribution and small size of these lesions make both diagnosis and management very difficult. We report a 12-year-old patient with diffuse bilateral PAVMs confirmed by contrast echocardiography and technetium-labeled macroaggregated albumin perfusion scan.
Yu
Chang-Hsien
CH
Department of Pediatrics, Mackay Memorial Hospital, Taipei, Taiwan.
Chen
Ming-Ren
MR
Lin
Shuan-Pei
SP
Shih
Bing-Fu
BF
D001165:Arteriovenous Malformations / Q000150:complications / Q000175:diagnosis* / Q000473:pathology; D002648:Child; D003490:Cyanosis / Q000175:diagnosis / Q000209:etiology; D004844:Epistaxis / Q000175:diagnosis / Q000209:etiology; D005260:Female; D006801:Humans; D011651:Pulmonary Artery / Q000002:abnormalities*; D011667:Pulmonary Veins / Q000002:abnormalities*