[Intimal sarcoma of the inferior vena cava].
BACKGROUND
Primary sarcomas of the great vessels, that is, the aorta, pulmonary artery, and inferior vena cava, are rare. They can be classified according to the location of the sarcoma in the vessel wall and by their gross appearance. Most often they are leiomyosarcomas or fibrosarcomas.


METHODS
We report here a case of an intimal sarcoma of the inferior vena cava. Histological and immunohistochemical findings confirmed the diagnosis for this 17-year-old girl and distinguished it from leiomyosarcoma and angiosarcoma, both of which have better prognoses.


CONCLUSIONS
Intimal sarcoma of the inferior vena cava is rare and difficult to diagnose before surgery or biopsy. Histologically, it is a poorly differentiated tumor with the worst prognosis among the primary vascular sarcomas. Pathologic findings and immunohistochemical staining are useful for a positive diagnosis.
Rouas
L
L
Service d'anatomie pathologique, Hôpital Avicenne, Rabat, Maroc. rouaslamiab@yahoo.fr
Mahassini
N
N
Jahid
A
A
Saïdi
H
H
Zouaïdia
F
F
Nabih
N
N
Bernoussi
Z
Z
Mansouri
F
F
El Hachimi
A
A
D000293:Adolescent; D001323:Autoantibodies / Q000032:analysis; D019917:Blood Vessel Prosthesis Implantation; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D012509:Sarcoma / Q000175:diagnosis* / Q000601:surgery; D017539:Tunica Intima / Q000473:pathology* / Q000601:surgery; D019043:Vascular Neoplasms / Q000175:diagnosis* / Q000601:surgery; D014682:Vena Cava, Inferior / Q000473:pathology* / Q000601:surgery; D014746:Vimentin / Q000276:immunology
D001323:Autoantibodies; D014746:Vimentin