title: Hypoplasia of the left heart with discordant ventriculoarterial connections.
abstract: We report the rare combination of a severely hypoplastic left ventricle and discordant ventriculoarterial connections, with associated subpulmonary obstruction of the left ventricular outflow tract. The long tortuous arterial duct originated at an acute angle from the aorta, suggesting that the subpulmonary obstruction developed early in fetal life. Residual flow via the hypoplastic left ventricle to the pulmonary circulation after insertion of an aortopulmonary shunt resulted in haemodynamic deterioration, which was instantly reversed by closing the pulmonary trunk.
authors.affiliation: Pediatric Cardiology, University Children's Hospital, Tübingen, Germany. tbruhns.chalumeau@t-online.de
authors.forename: Thomas
authors.initials: T
authors.lastname: Borth-Bruhns
authors.forename: Gerhard
authors.initials: G
authors.lastname: Ziemer
authors.forename: Michael
authors.initials: M
authors.lastname: Hofbeck
mesh_terms: D003330:Coronary Vessel Anomalies / Q000175:diagnosis* / Q000601:surgery*; D006801:Humans; D018636:Hypoplastic Left Heart Syndrome / Q000175:diagnosis* / Q000601:surgery*; D007231:Infant, Newborn; D008297:Male; D014694:Ventricular Outflow Obstruction / Q000151:congenital* / Q000175:diagnosis / Q000601:surgery