title: [Osteogenesis imperfecta--operative treatment on lower extremities in children with osteogenesis imperfecta].
abstract: The group of 141 children with osteogenesis imperfecta was treated in Orthopaedic Department of the University Children Hospital in Krakow, Poland. In 77 (54.6%) children from this group, we operated on lower extremities. Prophylactic operations, that were intramedullary Rush rodding, we performed in 19 cases (14 femurs and 11 tibias). Sofield-Millar procedures we performed in 58 children. We operated 321 times - there are 4 operations on average in one child. Average follow-up period was 6.7 years. We operated 473 long bones: 234 femurs and 239 tibias. We did 479 osteotomies. First operations were done at the age of 9 years on average (1.5-21 years). Further operations, 3 in each patient on average, we performed in period 37 months from one to another on tibias and 49 months on femurs. In all operated children we achieved full axis correction and their activity after operation improved. In order to assess that, we used the Bleck scale. In general, before operation, 54 (70%) children did not walk, and, in contrast, after operations 53 (69%) started walking. Operative treatment of the lower extremities in children with osteogenesis imperfecta improves their clinical physical abilities, quality of life and allows increase in activities.
authors.affiliation: Oddział Ortopedyczno-Urazowy Katedry i Kliniki Chirurgii Pediatryicznej, Uniwersytecki Szpital Dzieciecy, Uniwersytetu Jagiellońskiego.
authors.forename: Jerzy
authors.initials: J
authors.lastname: Sułko
authors.forename: Wojciech
authors.initials: W
authors.lastname: Radło
mesh_terms: D000293:Adolescent; D000328:Adult; D002648:Child; D002675:Child, Preschool; D005260:Female; D005593:Fracture Fixation, Internal; D006801:Humans; D007223:Infant; D038061:Lower Extremity Deformities, Congenital / Q000000981:diagnostic imaging / Q000601:surgery*; D008297:Male; D019637:Orthopedic Procedures / Q000379:methods*; D010013:Osteogenesis Imperfecta / Q000000981:diagnostic imaging / Q000601:surgery*; D011379:Prognosis; D011859:Radiography; D013997:Time Factors; D016896:Treatment Outcome; D016138:Walking