title: Remission of protein-losing enteropathy after nodal lymphoma treatment in a patient with primary intestinal lymphangiectasia.
abstract: Primary intestinal lymphangiectasia (PIL), so-called Waldmann's disease, is an uncommon condition, characterized by dilated intestinal submucosal and subserosal lymphatics of the gastrointestinal tract. Protein-losing enteropathy is the most common manifestation of this supposed congenital disease. Since the initial description in 1961, 11 cases of lymphoma have been reported suggesting that PIL predisposes to lymphoma. Here, we report the first case of primary nodal location lymphoma during PIL with recovery of the protein-losing enteropathy after its treatment by radiochemotherapy.
authors.affiliation: Service d'Hepatogastroentérologie, Hôpital Haut-Leveque, Pessac, France. david.laharie@chu-bordeaux.fr
authors.forename: David
authors.initials: D
authors.lastname: Laharie
authors.forename: Valerie
authors.initials: V
authors.lastname: Degenne
authors.forename: Hortense
authors.initials: H
authors.lastname: Laharie
authors.forename: Sophie
authors.initials: S
authors.lastname: Cazorla
authors.forename: Genevieve
authors.initials: G
authors.lastname: Belleannee
authors.forename: Patrice
authors.initials: P
authors.lastname: Couzigou
authors.forename: Michel
authors.initials: M
authors.lastname: Amouretti
mesh_terms: D000328:Adult; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D008201:Lymphangiectasis, Intestinal / Q000150:complications* / Q000473:pathology; D016393:Lymphoma, B-Cell / Q000209:etiology* / Q000628:therapy; D016403:Lymphoma, Large B-Cell, Diffuse / Q000209:etiology* / Q000628:therapy; D011504:Protein-Losing Enteropathies / Q000209:etiology*