Unusual presentation of a patient with arrhythmogenic right ventricular dysplasia treated with a Glenn shunt.
Clinically, arrhythmogenic right ventricular dysplasia (ARVD) usually presents with ventricular arrhythmias, and unusual presentations were reported as acute coronary syndrome, heart failure and electrical storm. Taking all this different presentations and treatments in to account, we report a case of ARVD presenting with central cyanosis and clubbing simulating congenital heart disease. Besides this unusual presentation, the patient underwent also an unusual operation for this kind of abnormality, which cured the cyanosis completely.
Gorgulu
Sevket
S
Nurkalem
Zekeriya
Z
Celebi
Ahmet
A
Bilal
Mehmet Salih
MS
Yalcin
Yalim
Y
Cine
Nihat
N
Eren
Mehmet
M
D000293:Adolescent; D019571:Arrhythmogenic Right Ventricular Dysplasia / Q000175:diagnosis* / Q000601:surgery*; D001166:Arteriovenous Shunt, Surgical; D005260:Female; D006801:Humans; D011651:Pulmonary Artery / Q000601:surgery; D014683:Vena Cava, Superior / Q000601:surgery