Renal calculi in a patient with Erdheim-Chester disease.
Erdheim-Chester Disease (ECD) is a non-inherited multifocal lipid storing histiocytosis. It is a rare disease characterised by lipid-laden monocyte infiltration of long bones causing cortical sclerosis and characteristic X-ray appearances. It also involves extraskeletal tissue in up to 50% of cases including retroperitoneal and renal infiltration. We report a patient with long standing ECD with widespread extraskeletal involvement, including significant renal infiltration, presenting with left hydronephrosis secondery obstruction from a proximal ureteric calculas.
Dundee
Philip
P
Department of Urology, Royal Melbourne Hospital, Parkville, Melbourne, Australia. pdundee@amavic.com
Bouchier-Hayes
David
D
Iles
Linda
L
Costello
Anthony
A
D031249:Erdheim-Chester Disease / Q000150:complications* / Q000473:pathology; D006801:Humans; D006869:Hydronephrosis / Q000209:etiology; D008297:Male; D008875:Middle Aged; D014514:Ureteral Calculi / Q000209:etiology* / Q000473:pathology