Cor triatriatum with single atrium presenting in adulthood.
We present the case of an asymptomatic 21-year-old woman referred because of an abnormal routine electrocardiogram. Transthoracic and transesophageal echocardiography revealed a complete absence of the atrial septum, a common atrium septated posteriorly from the pulmonary venous chamber, a partial atrioventricular canal, a cleft mitral valve and a persistent left superior vena cava draining into an enlarged coronary sinus. These findings were confirmed during surgical correction. Our patient presented with an unusual and fascinating combination of congenital malformations that remained well tolerated and undiscovered into adulthood.
Avula
Satyanarayana
S
Division of Cardiology, Saint Vincent Catholic Medical Centers of New York, Staten Island Region, 355 Bard Avenue, Staten Island, New York 10310, USA.
Salazar
Manuel
M
Alturk
Najib
N
Kukafka
Sheldon
S
Ritter
Samuel
S
Grodman
Richard S
RS
D000328:Adult; D006328:Cardiac Catheterization / Q000379:methods; D003310:Cor Triatriatum / Q000175:diagnosis* / Q000601:surgery; D015150:Echocardiography, Doppler / Q000379:methods; D017548:Echocardiography, Transesophageal / Q000379:methods; D005260:Female; D006325:Heart Atria / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000601:surgery; D006801:Humans; D008943:Mitral Valve / Q000002:abnormalities / Q000000981:diagnostic imaging / Q000601:surgery; D035583:Rare Diseases