[Dermatofibrosarcoma protuberans. About 18 cases].
Dermatofibrosarcoma protuberans (DFSP) is a rare mesenchyma skin tumor. It is characterized by a slow growth with a high rate of recurrence but limited potential for metastasis. We report the result of a retrospective study of 18 cases of DFSP collected over 16 years in the dermatology department of La Rabta Hospital. The mean age was 32 years with a sex ratio of 1.57. The site of predilection was the trunk (77.5%). Histological features were typical in all cases with positivity for CD34 in 14 cases. Treatment was surgical in 13 cases. DFSP is a tumor of intermediate malignancy, which can have aggressive course. This tumor is best treated with surgery in which large excision are necessary to reduce the risk of recurrence.
Zaraa
I
I
Service de dermatologie, Hôpital La Rabta, Tunis.
Cherif
E
E
Ferchichi
L
L
Ben Romdhane
K
K
Kchir
N
N
Mokni
M
M
Dhahri
A Ben Osman
AB
D000328:Adult; D000368:Aged; D002648:Child; D018223:Dermatofibrosarcoma / Q000473:pathology* / Q000601:surgery*; D018450:Disease Progression; D005260:Female; D006801:Humans; D008297:Male; D008875:Middle Aged; D011379:Prognosis; D012008:Recurrence; D012189:Retrospective Studies; D012307:Risk Factors; D012744:Sex Ratio