title: Pulmonary artery sarcoma misdiagnosed as chronic thromboembolic pulmonary hypertension.
abstract: Pulmonary artery sarcomas are rare neoplasms of the pulmonary artery that are often confused with chronic thromboembolic disease, as both diseases have similar presentations. In patients with presumed chronic thromboembolic pulmonary hypertension, certain clinical and imaging characteristics may suggest the alternative diagnosis of pulmonary artery sarcoma. In this article we present a case of a man initially diagnosed with chronic thromboembolic pulmonary hypertension, but who was later found to have pulmonary artery sarcoma. We review the distinguishing characteristics of the two diseases and discuss possible treatment strategies.
authors.affiliation: Cardiovascular Institute, Department of Medicine, Mount Sinai School of Medicine, New York, NY 10029, USA.
authors.forename: Eric
authors.initials: E
authors.lastname: Widera
authors.forename: Roxana
authors.initials: R
authors.lastname: Sulica
mesh_terms: D000368:Aged; D003951:Diagnostic Errors; D006801:Humans; D006976:Hypertension, Pulmonary / Q000175:diagnosis*; D007890:Leiomyosarcoma / Q000175:diagnosis*; D008297:Male; D011651:Pulmonary Artery / Q000000981:diagnostic imaging; D011655:Pulmonary Embolism / Q000175:diagnosis*; D011859:Radiography; D019043:Vascular Neoplasms / Q000175:diagnosis*; D014692:Ventilation-Perfusion Ratio