title: Cor triatriatum with single atrium presenting in adulthood.
abstract: We present the case of an asymptomatic 21-year-old woman referred because of an abnormal routine electrocardiogram. Transthoracic and transesophageal echocardiography revealed a complete absence of the atrial septum, a common atrium septated posteriorly from the pulmonary venous chamber, a partial atrioventricular canal, a cleft mitral valve and a persistent left superior vena cava draining into an enlarged coronary sinus. These findings were confirmed during surgical correction. Our patient presented with an unusual and fascinating combination of congenital malformations that remained well tolerated and undiscovered into adulthood.
authors.affiliation: Division of Cardiology, Saint Vincent Catholic Medical Centers of New York, Staten Island Region, 355 Bard Avenue, Staten Island, New York 10310, USA.
authors.forename: Satyanarayana
authors.initials: S
authors.lastname: Avula
authors.forename: Manuel
authors.initials: M
authors.lastname: Salazar
authors.forename: Najib
authors.initials: N
authors.lastname: Alturk
authors.forename: Sheldon
authors.initials: S
authors.lastname: Kukafka
authors.forename: Samuel
authors.initials: S
authors.lastname: Ritter
authors.forename: Richard S
authors.initials: RS
authors.lastname: Grodman
mesh_terms: D000328:Adult; D006328:Cardiac Catheterization / Q000379:methods; D003310:Cor Triatriatum / Q000175:diagnosis* / Q000601:surgery; D015150:Echocardiography, Doppler / Q000379:methods; D017548:Echocardiography, Transesophageal / Q000379:methods; D005260:Female; D006325:Heart Atria / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000601:surgery; D006801:Humans; D008943:Mitral Valve / Q000002:abnormalities / Q000000981:diagnostic imaging / Q000601:surgery; D035583:Rare Diseases