title: Proteus syndrome with giant myelolipoma in the pelvis.
abstract: Proteus syndrome is a very rare and complex disorder with malformations and overgrowth of multiple tissues. This disorder was designated Proteus syndrome by Wiedemann et al. to denote its variable clinical expression. Our patient presented with macrodactyly, cerebriform appearance and a huge abdominal mass. A biopsy under laparotomy was performed, and histopathological examination revealed myelolipoma. Tumor resection was performed. To our knowledge, no case of Proteus syndrome presenting a myelolipoma in the retroperitoneal cavity has been reported before.
authors.affiliation: Department of Urology, The University of Tokyo Hospital, Tokyo, Japan. MATSUMOTO-URO@h.u-tokyo.ac.jp
authors.forename: Shinya
authors.initials: S
authors.lastname: Matsumoto
authors.forename: Satoru
authors.initials: S
authors.lastname: Takahashi
authors.forename: Takahiro
authors.initials: T
authors.lastname: Goto
authors.forename: Kyoichi
authors.initials: K
authors.lastname: Tomita
authors.forename: Takumi
authors.initials: T
authors.lastname: Takeuchi
authors.forename: Tadaichi
authors.initials: T
authors.lastname: Kitamura
mesh_terms: D006801:Humans; D008297:Male; D008875:Middle Aged; D018209:Myelolipoma / Q000175:diagnosis* / Q000601:surgery; D016715:Proteus Syndrome / Q000175:diagnosis*; D012186:Retroperitoneal Neoplasms / Q000175:diagnosis* / Q000601:surgery