Portosystemic shunt with polysplenia and hypoplastic left heart syndrome.
We report a unique case of portosystemic shunt with polysplenia and hypoplastic left heart syndrome. The abnormal vessel connected the right renal vein and the splenic vein. The shunt flow was from the systemic vein to the portal vein before the Fontan-type operation, but it reversed and ran from portal vein to systemic vein after the Fontan-type operation.
Ikeda
H
H
Division of Pediatric Cardiology, Chiba Children's Hospital, Chiba, Japan. hike@cam.hi-ho.ne.jp
Aotsuka
H
H
Nakajima
H
H
Sawada
M
M
D000015:Abnormalities, Multiple; D000792:Angiography; D005500:Follow-Up Studies; D018729:Fontan Procedure / Q000379:methods; D006801:Humans; D018636:Hypoplastic Left Heart Syndrome / Q000175:diagnosis* / Q000601:surgery; D007231:Infant, Newborn; D008297:Male; D011169:Portal Vein / Q000002:abnormalities*; D011667:Pulmonary Veins / Q000002:abnormalities*; D013154:Spleen / Q000002:abnormalities*; D013158:Splenic Diseases / Q000151:congenital / Q000175:diagnosis* / Q000601:surgery; D014656:Vascular Surgical Procedures / Q000379:methods; D014684:Venae Cavae / Q000002:abnormalities*