title: [Intraoperative and postoperative analgesia with a caudal catheter in a child suffering from Schwartz-Jampel syndrome].
abstract: The Schwartz-Jampel syndrome, also known as myotonia chondrodystrophica, is a rare autosomal recessive disorder characterized by bone dysplasia, growth retardation and generalized myotonia. Laryngoscopy and intubation may be difficult because of micrognathia and limited mouth opening due to myotonia of the masseter muscles. As regional anaesthesia reduces myotonic contractions and avoids administration of opioids causing respiratory depression, it appears to be the ideal method for postoperative analgesia. We report on a 5-year-old girl who underwent osteotomy of both hips and received intraoperative and postoperative analgesia via a caudal catheter. Excellent analgesia without myoclonic episodes could be achieved by continuous infusion of ropivacaine.
authors.affiliation: Klinik für Anästhesiologie, Universitätsklinikum, Düsseldorf, Germany. markus.stevens@med.uni-duesseldorf.de
authors.forename: M F
authors.initials: MF
authors.lastname: Stevens
authors.forename: E
authors.initials: E
authors.lastname: Golla
authors.forename: P
authors.initials: P
authors.lastname: Lipfert
mesh_terms: D000577:Amides / Q000009:adverse effects / Q000627:therapeutic use; D000763:Anesthesia, Caudal; D000779:Anesthetics, Local / Q000009:adverse effects / Q000627:therapeutic use; D002404:Catheterization; D002675:Child, Preschool; D005260:Female; D006615:Hip / Q000601:surgery; D006801:Humans; D007442:Intubation, Intratracheal; D007828:Laryngoscopy; D010009:Osteochondrodysplasias / Q000150:complications*; D010027:Osteotomy; D010149:Postoperative Pain / Q000188:drug therapy*; D011229:Preanesthetic Medication; D011596:Psychomotor Disorders / Q000150:complications / Q000235:genetics; D000077212:Ropivacaine
chemical_list: D000577:Amides; D000779:Anesthetics, Local; D000077212:Ropivacaine