[Inborn and acquired von Willebrand disease].
Von Willebrand disease (VWD) is known for its marked heterogeneity which was already recognized by von Willebrand in 1926. The basis of phenotypic differentiation are quantitative and qualitative or functional differences between the different types and subtypes of VWD. Clinical relevant facts for the practitioner on diagnosis and therapy of von Willebrand disease and von Willebrand syndrome are presented.
Schneppenheim
R
R
Klinik für Pädiatrische Hämatologie und Onkologie, Universitäts-Klinikum Hamburg-Eppendorf, Martinistr. 52, 20246 Hamburg. schneppenheim@uke.uni-hamburg.de
Barthels
M
M
Budde
U
U
D003894:Deamino Arginine Vasopressin / Q000627:therapeutic use; D006490:Hemostatics / Q000627:therapeutic use; D006801:Humans; D010641:Phenotype; D014842:von Willebrand Diseases / Q000145:classification / Q000235:genetics* / Q000628:therapy*; D014841:von Willebrand Factor / Q000235:genetics
D006490:Hemostatics; D014841:von Willebrand Factor; D003894:Deamino Arginine Vasopressin