[Solitary fibrous tumor of the orbit: an unusual cause of unilateral proptosis. Case report with a review of the literature].
BACKGROUND
The solitary fibrous tumor (SFT) is a spindle-cell tumor that very rarely involves the orbit. We report a new case that we compare to reports in the literature.


METHODS
A 72-year-old woman presented a conjunctival inflammation of the right eye developing over 5 months with progressive proptosis. Magnetic resonance imaging revealed an extraconal and homogeneous mass, which showed hypointensity on T1-weighted images and hyperintensity on T2-weighted images, without specificity. Histological examination of the lesion removed by anterior orbitotomy confirmed the diagnosis of the SFT of the orbit. The patient was doing well without recurrence after 9 months.


CONCLUSIONS
The diagnosis of SFT is histological. It is a mesenchymal tumor. Immunohistochemically, the tumor cells are strongly positive for CD34 and vimentin.


CONCLUSIONS
The SFT of the orbit is a very rare and generally benign tumor. It must be immunohistochemically differentiated from other spindle-cell tumors of the orbit. The treatment is a complete surgical excision, and long-term follow-up is necessary because recurrence may appear long after treatment.
Dériot
J-B
JB
Service d'Ophtalmologie, Hôpital Gabriel Monpied, CHU Clermont-Ferrand, 58, rue Montalembert, BP69, 63003 Clermont-Ferrand cedex 1, France.
Ledoux-Pilon
A
A
Pilon
F
F
Ravel
A
A
Déchelotte
P
P
Rigal
D
D
Chiambaretta
F
F
D000368:Aged; D005094:Exophthalmos / Q000209:etiology*; D005260:Female; D006801:Humans; D009918:Orbital Neoplasms / Q000150:complications* / Q000473:pathology