Coil reduction of the right ventricular cavity in a boy with pulmonary atresia, intact ventricular septum, and an aneurysmal coronary sinusoid.
Coronary sinusoids are often found in patients with pulmonary atresia and intact ventricular septum. We report on a 4-year-old boy with such pathology in whom, after completion of the Fontan-circulation, the pulsatile flow through a major sinusoid significantly increased the size of a coronary artery up to aneurysmal dimensions. Because percutaneous closure of the sinusoid was unsuccessful, the right ventricular cavity was partially obliterated with coils. This resulted in a significant decrease of right ventricular stroke volume, regression of the pulsatility and of the coronary size, with good clinical result at 1.5 years of follow-up.
Vanagt
Ward Y
WY
Department of Pediatrics, Division of Pediatric Cardiology, University Hospital Maastricht, Maastricht, The Netherlands.
Delhaas
Tammo
T
Maleux
Geert
G
Gewillig
Marc
M
D002675:Child, Preschool; D017023:Coronary Angiography; D004621:Embolization, Therapeutic / Q000379:methods*; D018729:Fontan Procedure; D006322:Heart Aneurysm / Q000628:therapy*; D006330:Heart Defects, Congenital / Q000601:surgery / Q000628:therapy*; D006801:Humans; D008297:Male; D018633:Pulmonary Atresia / Q000601:surgery; D011673:Pulsatile Flow