[Idiopathic intrahepatic portosytemic shunts in 4 children].
Intrahepatic portosystemic anastomoses are macroscopic communications between the venous portal system and the systemic circulation and located partly in the liver. We report 4 new cases of type II shunts, which illustrate the circumstances of the diagnosis of these exceptional anomalies. For 2 children, the diagnosis was done antenataly by US and spontaneous involution in a few months was observed. In the third case the malformation was evidenced fortuitously at 3 weeks of life, and this 6-year-old child remains completely asymptomatic so far. Then, in the fourth case, a cerebral venous thrombosis was fortuitously and antenatally evidenced in an otherwise uneventful pregnancy and portosystemic shunt was demonstrated postnataly in the extensive work up of the neonate.
Rouveyrol
F
F
Service de pédiatrie, Hôtel-Dieu, CHU de Clermont-Ferrand, France.
Meyer
M
M
Lusson
J R
JR
Dauphin
C
C
Vanlieferinghen
P
P
Déchelotte
P
P
Laurichesse
H
H
Guibaud
L
L
Pracros
P
P
Campagne
D
D
Gaspard
F
F
Lachaux
A
A
Stéphan
J-L
JL
D005500:Follow-Up Studies; D006503:Hepatic Veins / Q000002:abnormalities*; D006801:Humans; D007231:Infant, Newborn; D020767:Intracranial Thrombosis / Q000150:complications / Q000175:diagnosis; D008297:Male; D011168:Portal System / Q000002:abnormalities*; D011169:Portal Vein / Q000002:abnormalities*; D013997:Time Factors; D016216:Ultrasonography, Prenatal; D016157:Vascular Fistula / Q000150:complications