A congenital teratoma with a cleft palate: report of a case.
Teratomas are benign tumors containing cells from ectodermal, mesodermal and endodermal layers. They occur in about 1 in every 4000 births and most commonly in the sacrococcygeal region, followed by the ovaries. Congenital epignathus teratomas are rare embryological neoplasms localised in the region of head and neck. An epignathus is found in approximately 1:35,000 to 1:200,000 live births. This accounts for 2-9% of all teratomas. Size and location of the neoplasm in the oronasopharynx is variable. Teratomas are partly undiagnosed at the time of birth. They may exist with an intracranial extension or as small polyps. Large epignathi can lead to difficult management during and after birth. The case of a newborn girl with a combination of an epignathus and a cleft palate is described. The epignathus presented as a huge mass extending out of the mouth of the infant girl. On the day of birth debulking of the extraoral portion of the tumor, followed by intraoral exstirpation, was performed. The results of the histologic examination indicated a congenital epignathus. Six months later a recurrence was found.
Becker
S
S
Department of Oral-, Maxillo- and Craniofacial Surgery, Albert-Ludwigs-University Freiburg, Hugstetter Strasse 55, D-79106 Freiburg, Germany. silke.becker@uniklinik-freiburg.de
Schön
R
R
Gutwald
R
R
Otten
J E
JE
Maier
W
W
Hentschel
R
R
Jüttner
E
E
Gellrich
N C
NC
D002972:Cleft Palate / Q000209:etiology*; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D007231:Infant, Newborn; D009364:Neoplasm Recurrence, Local / Q000473:pathology; D009669:Nose Neoplasms / Q000151:congenital / Q000473:pathology; D019292:Skull Base Neoplasms / Q000151:congenital*; D013724:Teratoma / Q000151:congenital* / Q000473:pathology