Double lung transplantation in a patient with tracheobronchomegaly (Mounier-Kuhn syndrome).
Mounier-Kuhn syndrome is a rare condition characterized by marked dilation of the trachea and main bronchi resulting in bronchiectasis and emphysema. We report a case in which a patient underwent successful double lung transplantation for COPD that was found on pathologic examination of the explanted lungs to be Mounier Kuhn syndrome. To our knowledge this is the first case reporting lung transplantation in this syndrome.
Drain
Andrew J
AJ
Papworth Hospital, Cambridge, United Kingdom. andrewdrain@doctors.org.uk
Perrin
Felicity
F
Tasker
Angela
A
Stewart
Susan
S
Wells
Francis
F
Tsui
Steven
S
Sivasothy
Siva
S
D004646:Emphysema / Q000209:etiology / Q000601:surgery; D006801:Humans; D008168:Lung / Q000473:pathology; D016040:Lung Transplantation; D008297:Male; D008875:Middle Aged; D029424:Pulmonary Disease, Chronic Obstructive / Q000209:etiology / Q000601:surgery; D014137:Tracheobronchomegaly / Q000150:complications / Q000601:surgery*; D016896:Treatment Outcome