title: Double lung transplantation in a patient with tracheobronchomegaly (Mounier-Kuhn syndrome).
abstract: Mounier-Kuhn syndrome is a rare condition characterized by marked dilation of the trachea and main bronchi resulting in bronchiectasis and emphysema. We report a case in which a patient underwent successful double lung transplantation for COPD that was found on pathologic examination of the explanted lungs to be Mounier Kuhn syndrome. To our knowledge this is the first case reporting lung transplantation in this syndrome.
authors.affiliation: Papworth Hospital, Cambridge, United Kingdom. andrewdrain@doctors.org.uk
authors.forename: Andrew J
authors.initials: AJ
authors.lastname: Drain
authors.forename: Felicity
authors.initials: F
authors.lastname: Perrin
authors.forename: Angela
authors.initials: A
authors.lastname: Tasker
authors.forename: Susan
authors.initials: S
authors.lastname: Stewart
authors.forename: Francis
authors.initials: F
authors.lastname: Wells
authors.forename: Steven
authors.initials: S
authors.lastname: Tsui
authors.forename: Siva
authors.initials: S
authors.lastname: Sivasothy
mesh_terms: D004646:Emphysema / Q000209:etiology / Q000601:surgery; D006801:Humans; D008168:Lung / Q000473:pathology; D016040:Lung Transplantation; D008297:Male; D008875:Middle Aged; D029424:Pulmonary Disease, Chronic Obstructive / Q000209:etiology / Q000601:surgery; D014137:Tracheobronchomegaly / Q000150:complications / Q000601:surgery*; D016896:Treatment Outcome