Meningioangiomatosis with meningioma: an uncommon association of a rare entity--report of a case and review of the literature.
BACKGROUND
Meningioangiomatosis (MA) is a rare lesion, probably of malformative origin, consisting of meningovascular proliferation and leptomeningeal calcification. Patients with MA usually present with seizures or persistent headaches. Neurofibromatosis may be associated in a variable proportion of patients, while in others it may be sporadic. Surgical treatment is usually recommended, and is gratifying in most cases. Rarely, MA has been described coexisting with meningiomas, arteriovenous malformations, encephaloceles, oligodendrogliomas, meningeal haemangiopericytomas and orbital erosion. Among these, meningiomatosis with meningioma is the most frequent combination.


METHODS
We report a case of MA with meningioma in an 18-month-old girl, who presented with recurrent seizures.


CONCLUSIONS
In these situations, it is extremely important for the pathologist to be aware of this entity and to distinguish it from other lesions, like cortical invasion by a meningioma, intraparenchymal meningioma and intracerebral schwannoma, which it may mimic.
Deb
Prabal
P
Department of Pathology, All India Institute of Medical Sciences, AIIMS, Ansari Nagar, New Delhi, 110029, India.
Gupta
Aditya
A
Sharma
Mehar Chand
MC
Gaikwad
Shailesh
S
Singh
V P
VP
Sarkar
Chitra
C
D000798:Angiomatosis / Q000150:complications* / Q000601:surgery; D005260:Female; D006801:Humans; D007223:Infant; D008279:Magnetic Resonance Imaging / Q000379:methods; D008577:Meningeal Neoplasms / Q000150:complications* / Q000601:surgery; D008578:Meninges / Q000473:pathology* / Q000601:surgery; D008579:Meningioma / Q000150:complications* / Q000601:surgery; D009493:Neurosurgery; D012196:Review Literature as Topic; D014057:Tomography, X-Ray Computed / Q000379:methods