Primary Sjögren's syndrome associated with pneumatosis cystoides coli.
We report the case of a 43-year-old woman with primary Sjögren's syndrome, according to Americano-European criteria. Eighteen months after the diagnosis, the patient presented pneumatosis cystoides coli (PCC), which resolved with medical treatment consisting of diet and cisapride. Four years after this episode, the patient has not developed clinical features of another systemic inflammatory rheumatic disease and PCC has not relapsed. To the best of our knowledge, the association between primary Sjögren' syndrome and PCC has never been reported. Physiopathology and treatment of PCC are discussed.
Vandergheynst
F
F
Internal Medicine Department, Erasme University Hospital, Université Libre de Bruxelles, 808, route de Lennik, B-1070 Brussels, Belgium. fvdgheyn@ulb.ac.be
Van Gansbeke
D
D
Steinfeld
S
S