A case of Henoch-Schönlein purpura with rare complications: necrosis of the small intestine, neurological symptoms, and pericardial tamponade.
A case of Henoch-Schönlein purpura (HSP) with necrosis of the small intestine, neurological symptoms, and pericardial tamponade after frequent recurrence is described. Neurological symptoms were controlled well with steroid pulse therapy, and pericardial tamponade was treated successfully with pericardiocentesis and steroid pulse therapy. To treat necrosis of the small intestine, the necrotic tissue was excised and artificial anuses were constructed. Five months later, the small intestine was anastomosed in a curative operation. Periodic administration of coagulation factor XIII was required from the onset of symptoms until curative surgery, but the activity of this factor returned to normal levels after surgery operation. We report a case of Henoch-Schönlein purpura with extremely rare complications: necrosis of the small intestine, neurological symptoms, and pericardial tamponade.
Migita
Makoto
M
Department of Pediatrics, Nippon Medical School, Tokyo, Japan. Migita-Makoto-bmb@nms.ac.jp
Hayakawa
Jun
J
Shima
Hideki
H
Kobayashi
Hiroyuki
H
Yamataka
Atsutaka
A
Murakami
Mutsumi
M
Miyano
Takeshi
T
Fukunaga
Yoshitaka
Y
D015746:Abdominal Pain / Q000188:drug therapy; D002305:Cardiac Tamponade / Q000150:complications* / Q000628:therapy; D002648:Child; D005176:Factor XIII / Q000737:chemistry / Q000627:therapeutic use; D006801:Humans; D011695:IgA Vasculitis / Q000150:complications* / Q000188:drug therapy; D007421:Intestine, Small / Q000473:pathology* / Q000601:surgery; D008297:Male; D009336:Necrosis
D005176:Factor XIII