Malignant retroperitoneal tumor arising in a multicystic dysplastic kidney of a girl with Schinzel-Giedion syndrome.
We report the first case of malignant retroperitoneal tumor arising in a multicystic dysplastic kidney of an 8-year-old girl with Schinzel-Giedion syndrome. Although conservative treatment has been regarded as the standard management for asymptomatic multicystic dysplastic kidney, prophylactic surgical removal should be considered for selected children with potential risk of malignancy.
Matsumoto
Fumi
F
Osaka Medical Center and Research Institute for Maternal and Child Health, Urology, Osaka, Japan. fumim@mch.pref.osaka.jp
Tohda
Akira
A
Shimada
Kenji
K
Okamoto
Nobuhiko
N
D000015:Abnormalities, Multiple; D002648:Child; D003025:Clubfoot / Q000150:complications*; D019465:Craniofacial Abnormalities / Q000150:complications*; D017809:Fatal Outcome; D005260:Female; D006330:Heart Defects, Congenital / Q000150:complications*; D006801:Humans; D021782:Multicystic Dysplastic Kidney / Q000150:complications*; D012186:Retroperitoneal Neoplasms / Q000209:etiology*; D013577:Syndrome; D014517:Ureteral Obstruction / Q000150:complications*