Extensive cervical-mediastinal cystic lymphatic malformation treated with sclerotherapy in a child with Klippel-Trenaunay syndrome.
Klippel-Trenaunay syndrome is a rare congenital disorder characterized by combined vascular malformations, varicosities, and limb enlargement. A child case of Klippel-Trenaunay syndrome with a large cervicomediastinal cystic lymphatic malformation and a vascular mass on the chest wall has been presented to demonstrate combined use of conservative and surgical approaches in this syndrome. Cystic lymphatic malformation was treated by sclerotherapies including ultrasound-guided transthoracic bleomycin injection into mediastinal cyst, which was tried for the first time in the literature, and vascular chest wall tumor necessitated surgical excision.
Duman
Levent
L
Department of Pediatric Surgery, Hacettepe University Faculty of Medicine, 06100 Ankara, Turkey.
Karnak
Ibrahim
I
Akinci
Devrim
D
Tanyel
F Cahit
FC
D003560:Cysts / Q000601:surgery / Q000628:therapy*; D006801:Humans; D007223:Infant; D007715:Klippel-Trenaunay-Weber Syndrome / Q000150:complications*; D008206:Lymphatic Diseases / Q000601:surgery / Q000628:therapy*; D008297:Male; D008482:Mediastinum / Q000473:pathology; D009333:Neck / Q000473:pathology; D015911:Sclerotherapy