Covered exstrophy with visceral sequestration: case report and review of literature.
We report a case of a male newborn with asymmetrical epispadic diphallia and congenital urethral fistula, and exomphalos minor. A segment of bowel was attached in the region of the pubis; with no communication to the underlying bowel. This was excised; histological examination revealed this to be a colonic remnant. The excision of the examphalos minor and approximation of the pubis and the rectus sheath over the bladder was also done; urethroplasty is planned at a later date. A comprehensive review of the available literature revealed only eight such cases before this; the possible embryology is discussed.
Sarin
Y K
YK
Department of Pediatric Surgery, Maulana Azad Medical College and associated Lok Nayak Hospital, New Delhi, India.
Sinha
A
A
Ojha
S
S
D001746:Bladder Exstrophy / Q000196:embryology / Q000601:surgery*; D003106:Colon / Q000002:abnormalities*; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D014522:Urethral Diseases / Q000151:congenital*; D014548:Urinary Fistula / Q000151:congenital*