title: Malignant retroperitoneal tumor arising in a multicystic dysplastic kidney of a girl with Schinzel-Giedion syndrome.
abstract: We report the first case of malignant retroperitoneal tumor arising in a multicystic dysplastic kidney of an 8-year-old girl with Schinzel-Giedion syndrome. Although conservative treatment has been regarded as the standard management for asymptomatic multicystic dysplastic kidney, prophylactic surgical removal should be considered for selected children with potential risk of malignancy.
authors.affiliation: Osaka Medical Center and Research Institute for Maternal and Child Health, Urology, Osaka, Japan. fumim@mch.pref.osaka.jp
authors.forename: Fumi
authors.initials: F
authors.lastname: Matsumoto
authors.forename: Akira
authors.initials: A
authors.lastname: Tohda
authors.forename: Kenji
authors.initials: K
authors.lastname: Shimada
authors.forename: Nobuhiko
authors.initials: N
authors.lastname: Okamoto
mesh_terms: D000015:Abnormalities, Multiple; D002648:Child; D003025:Clubfoot / Q000150:complications*; D019465:Craniofacial Abnormalities / Q000150:complications*; D017809:Fatal Outcome; D005260:Female; D006330:Heart Defects, Congenital / Q000150:complications*; D006801:Humans; D021782:Multicystic Dysplastic Kidney / Q000150:complications*; D012186:Retroperitoneal Neoplasms / Q000209:etiology*; D013577:Syndrome; D014517:Ureteral Obstruction / Q000150:complications*