[Stewart-Treves syndrome].
Lymphangiosarcoma is an uncommon vascular tumor that usually develops in longstanding lymphedema. We gathered the cases of lymphangioma observed in a hospital and attempted to analyze their characteristics: age, sex, localization, treatment and follow-up data. We studied five cases: three cases of Stewart-Treves syndrome after mastectomy and radiotherapy and two cases that developed in patients with late-onset congenital lymphedema. There were four women and one man. Radical surgery was performed in four patients. The techniques employed were: above-knee amputation (one patient), hip disarticulation (one patient), scapulo-humeral disarticulation (two patients) and gemcitabine and radiotherapy in one patient with metastatic disease at diagnosis. Three patients died in the first 14 months of follow-up, while two are disease free after 46 and 86 months respectively. This study confirms the poor prognosis of patients with Steward-Treves syndrome.
Echenique-Elizondo
Miguel
M
Unidad Docente de Medicina, Facultad de Medicina, Universidad del País Vasco, San Sebastián, Guipúzcoa, Spain. gepecelm@sc.ehu.es
Tuneu-Valls
Ana
A
Zubizarreta
José
J
Lobo
Carmen
C
D000328:Adult; D000368:Aged; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D008204:Lymphangiosarcoma / Q000175:diagnosis / Q000628:therapy; D008297:Male; D008875:Middle Aged; D013577:Syndrome