title: Treatment of multiple hereditary osteochondromas of the forearm in children: a study of surgical procedures.
abstract: We have evaluated the clinical outcomes of simple excision, ulnar lengthening and the Sauvé-Kapandji procedure in the treatment of deformities of the forearm in patients with multiple hereditary osteochondromas. The medical records of 29 patients (33 forearms) were reviewed; 22 patients (22 forearms) underwent simple excision (four with ulnar lengthening) and seven the Sauvé-Kapandji procedure. Simple excision increased the mean supination of the forearm from 63.2 degrees to 75.0 degrees (p = 0.049). Ulnar lengthening did not significantly affect the clinical outcome. The Sauvé-Kapandji technique improved the mean pronation from 33.6 degrees to 55.0 degrees (p = 0.047) and supination from 70.0 degrees to 81.4 degrees (p = 0.045). Simple excision may improve the range of movement of the forearm but will not halt the progression of disease, particularly in younger patients. No discernable clinical or radiological improvement was noted with ulnar lengthening. The Sauvé-Kapandji procedure combined with simple excision of osteochondromas can improve stability of the wrist, movement of the forearm and the radiological appearance.
authors.affiliation: Department of Orthopaedic Surgery UCLA, Centre for Health Sciences, 10833 LeConte Avenue, Los Angeles 90095, California, USA. eshin@mednet.ucla.edu
authors.forename: E K
authors.initials: EK
authors.lastname: Shin
authors.forename: N F
authors.initials: NF
authors.lastname: Jones
authors.forename: J F
authors.initials: JF
authors.lastname: Lawrence
mesh_terms: D000293:Adolescent; D000328:Adult; D002648:Child; D002675:Child, Preschool; D005097:Exostoses, Multiple Hereditary / Q000000981:diagnostic imaging / Q000503:physiopathology / Q000601:surgery*; D005542:Forearm / Q000000981:diagnostic imaging / Q000601:surgery*; D006801:Humans; D019637:Orthopedic Procedures / Q000379:methods; D011403:Pronation / Q000502:physiology; D011859:Radiography; D011884:Radius / Q000002:abnormalities / Q000601:surgery; D016059:Range of Motion, Articular / Q000502:physiology; D012086:Reoperation; D013484:Supination / Q000502:physiology; D016896:Treatment Outcome; D014457:Ulna / Q000002:abnormalities / Q000601:surgery