Idiopathic infantile arterial calcification: imaging evaluation and the usefulness of MR angiography.
Idiopathic infantile arterial calcification (IIAC) is a rare condition characterized by extensive calcification and stenosis of large and medium-size arteries. The etiology of the disease is unknown. However, the inheritance pattern has been shown to be autosomal recessive. The clinical presentation is variable, including cardiac failure (most common clinical finding), hypertension, and respiratory failure. Plain radiography, sonography and MRI can aid in the diagnosis. We present a case in which contrast-enhanced MR angiography with breath-hold and cardiac gating techniques allowed complete evaluation of the extent of this disease.
Tran
Kim H
KH
Department of Radiological Sciences, Pediatric Radiology, David Geffen School of Medicine at UCLA, 10833 Le Conte Ave, Box 951721, Los Angeles, CA 90095-1721, USA.
Boechat
M Ines
MI
D000328:Adult; D001157:Arterial Occlusive Diseases / Q000175:diagnosis* / Q000000981:diagnostic imaging; D002114:Calcinosis / Q000175:diagnosis* / Q000000981:diagnostic imaging; D003287:Contrast Media; D003937:Diagnosis, Differential; D005260:Female; D019786:Gadolinium DTPA; D006801:Humans; D007231:Infant, Newborn; D018810:Magnetic Resonance Angiography; D008297:Male; D011247:Pregnancy; D014463:Ultrasonography
D003287:Contrast Media; C064925:gadodiamide; D019786:Gadolinium DTPA