Juvenile amyopathic dermatomyositis.
A 3-year-old girl presented with a 6-month history of multiple, light-pink, flat-topped papules over the dorsal aspects of the metacarpophalangeal and interphalangeal joints of the hands and feet. Nailfold telangiectases, ragged cuticles, and a heliotrope color of the upper eyelids were also evident, but there was no clinical evidence of muscle weakness and levels of muscle enzymes were normal. A biopsy specimen from one of the papules showed a vacuolar interface dermatitis consistent with a diagnosis of dermatomyositis. This report draws attention to juvenile amyopathic dermatomyositis, which is an uncommon subtype of dermatomyositis with an excellent prognosis.
Henning
J Scott
JS
Department of Dermatology, New York University School of Medicine, USA.
Witkiewicz
Agnieszka
A
Schaffer
Julie V
JV
Orlow
Seth J
SJ
D002675:Child, Preschool; D003882:Dermatomyositis / Q000175:diagnosis / Q000473:pathology*; D003937:Diagnosis, Differential; D005260:Female; D005533:Foot Dermatoses / Q000473:pathology; D006229:Hand Dermatoses / Q000175:diagnosis / Q000473:pathology; D006801:Humans; D012867:Skin / Q000473:pathology; D014860:Warts / Q000175:diagnosis