title: Anesthesia for an adult with mucopolysaccharidosis I.
abstract: We describe the anesthetic management difficulties of a man with mucopolysaccharidosis I. We also briefly review the anesthesia literature related to this disease.
authors.affiliation: Department of Anesthesiology, New York University Medical Center, New York, NY 10016, USA.
authors.forename: John L
authors.initials: JL
authors.lastname: Ard
authors.forename: Alex
authors.initials: A
authors.lastname: Bekker
authors.forename: Anthony K
authors.initials: AK
authors.lastname: Frempong-Boadu
mesh_terms: D000759:Adjuvants, Anesthesia / Q000008:administration & dosage; D000328:Adult; D000768:Anesthesia, General / Q000379:methods*; D018685:Anesthetics, Inhalation / Q000008:administration & dosage; D018686:Anesthetics, Intravenous / Q000008:administration & dosage; D000779:Anesthetics, Local / Q000008:administration & dosage; D001279:Atracurium / Q000008:administration & dosage / Q000031:analogs & derivatives; D004329:Droperidol / Q000008:administration & dosage; D005283:Fentanyl / Q000008:administration & dosage; D005336:Fiber Optic Technology; D006024:Glycopyrrolate / Q000008:administration & dosage; D006801:Humans; D007442:Intubation, Intratracheal / Q000379:methods; D007530:Isoflurane / Q000008:administration & dosage; D008012:Lidocaine / Q000008:administration & dosage; D008297:Male; D008059:Mucopolysaccharidosis I / Q000601:surgery*; D009466:Neuromuscular Blocking Agents / Q000008:administration & dosage; D009809:Odontoid Process / Q000601:surgery; D015742:Propofol / Q000008:administration & dosage; D012601:Scopolamine / Q000008:administration & dosage; D013123:Spinal Fusion / Q000379:methods; D014139:Tracheostomy / Q000379:methods
chemical_list: D000759:Adjuvants, Anesthesia; D018685:Anesthetics, Inhalation; D018686:Anesthetics, Intravenous; D000779:Anesthetics, Local; D009466:Neuromuscular Blocking Agents; D001279:Atracurium; D008012:Lidocaine; D007530:Isoflurane; D012601:Scopolamine; D004329:Droperidol; C101584:cisatracurium; D005283:Fentanyl; D006024:Glycopyrrolate; D015742:Propofol