Congenital chylothorax associated with isolated congenital hypoplastic superior caval vein: a case report.
Congenital absence, or hypoplasia, of the superior vena cava (SVC) with situs solitus is quite uncommon. Most cases have been found incidentally and concomitant with left persistent SVC or other cardiac disorders. Congenital chylothorax may be associated with cardiac anomalies, various syndromes, thoracic ductal or venous thrombosis, birth trauma or local compression of the thoracic duct, but it is rarely caused directly by congenital SVC anomalies.


CONCLUSIONS
We report a rare case of congenital chylothorax associated with isolated congenital hypoplastic SVC and underdeveloped collateral circulation.
Lee
Chune-Yi
CY
Department of Paediatrics, Taichung Veterans General Hospital, Taichung, Taiwan.
Jan
Sheng-Ling
SL
Wang
Teh-Ming
TM
Chi
Ching-Shiang
CS
D000015:Abnormalities, Multiple / Q000175:diagnosis; D001964:Bromhexine; D002916:Chylothorax / Q000151:congenital* / Q000209:etiology; D003097:Collateral Circulation; D005260:Female; D006801:Humans; D007231:Infant, Newborn; D011859:Radiography; D014683:Vena Cava, Superior / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000473:pathology*
D001964:Bromhexine