title: Atrioventricular septal defect with intact septal structures presenting as left atrioventricular valvar insufficiency.
abstract: We describe the findings in a six-year-old girl who presented with signs of left atrioventricular valvar insufficiency. The echocardiogram showed a common atrioventricular junction, intact atrial and ventricular septal structures. At surgery, the left-sided atrioventricular valve was found to be tri-foliate, and corrected by valvoplasty. To the best of our knowledge, this is the first case of atrioventricular septal defect with common atrioventricular junction and intact septal structures diagnosed during life.
authors.affiliation: Pediatric Cardiac Surgery, Hospital de Base da Faculdade de Medicina de São José do Rio Preto, and Laboratory of Pathology, Heart Institute (InCor), University of São Paulo, Brazil.
authors.forename: Ulisses Alexandre
authors.initials: UA
authors.lastname: Croti
authors.forename: Carlos Henrique
authors.initials: CH
authors.lastname: De Marchi
authors.forename: Vera Demarchi
authors.initials: VD
authors.lastname: Aiello
mesh_terms: D006348:Cardiac Surgical Procedures / Q000379:methods; D002648:Child; D003937:Diagnosis, Differential; D004452:Echocardiography; D004562:Electrocardiography; D005260:Female; D006343:Heart Septal Defects / Q000150:complications / Q000175:diagnosis* / Q000601:surgery; D006349:Heart Valve Diseases / Q000150:complications / Q000175:diagnosis / Q000601:surgery; D006351:Heart Valves / Q000002:abnormalities* / Q000601:surgery; D006801:Humans; D013536:Suture Techniques