Mesenteric fibromatosis in a patient with Camurati-Engelmann disease. A case report and literature review.
Mesenteric fibromatosis is a rare type of desmoid tumor characterized by local aggressiveness and a tendency to relapse. In view of these characteristics it may be considered a low-grade fibrosarcoma. Camurati-Engelmann disease is a very rare form of bone dysplasia characterized by osteosclerosis of the diaphyses of the long bones. Here we describe the case of a male patient affected by these two rare diseases in association with chronic inflammatory intestinal disease.
Ballardini
Pierluigi
P
Unità Operativa di Medicina Interna, Ospedale del Delta, Lagosanto, Ferrara, Italy. p.ballardini@ausl.fe.it
Gulmini
Loretta
L
Margutti
Guido
G
Lelli
Giorgio
G
D000328:Adult; D003966:Camurati-Engelmann Syndrome / Q000150:complications*; D005350:Fibroma / Q000150:complications*; D006801:Humans; D015212:Inflammatory Bowel Diseases / Q000150:complications; D008297:Male; D008643:Mesentery; D010534:Peritoneal Neoplasms / Q000150:complications*