Salt wasting disorder in the newborn.
The clinical presentation of pseudohypoaldosteronism (PHA) mimics congenital adrenal hyperplasia (CAH). Poor response of the dehydration and electrolyte abnormalities to steroid therapy should make one suspect PHA. The treatment is supportive in the form of salt replacement and sodium resonium. We report a case of PHA that presented as salt wasting on the second day of life, initially appearing like CAH. The baby responded well to sodium resonium and salt replacement.
Ranjith
G
G
Kerala Institute of Medical Sciences,Trivandrum, Kerala, India.
Uthup
Susan
S
Satish
B
B
Jain
Naveen
N
D000312:Adrenal Hyperplasia, Congenital; D002411:Cation Exchange Resins / Q000627:therapeutic use; D016861:Cyclooxygenase Inhibitors / Q000627:therapeutic use; D003937:Diagnosis, Differential; D006801:Humans; D007213:Indomethacin / Q000627:therapeutic use; D007231:Infant, Newborn; D008297:Male; D011137:Polystyrenes / Q000627:therapeutic use; D011546:Pseudohypoaldosteronism / Q000175:diagnosis* / Q000188:drug therapy / Q000503:physiopathology; D012462:Saline Solution, Hypertonic / Q000627:therapeutic use
D002411:Cation Exchange Resins; D016861:Cyclooxygenase Inhibitors; D011137:Polystyrenes; D012462:Saline Solution, Hypertonic; C003321:polystyrene sulfonic acid; D007213:Indomethacin