Inoperable aggressive mesenteric fibromatosis with ureteric fistula. Case report and literature review.
The purpose of our report is to illustrate an aggressive case of mesenteric fibromatosis in a 17-year-old girl with a ureteric fistula and to review imaging and pathological features, natural history and treatment options of this disease. Our patient underwent computed tomography that revealed a widespread intra-abdominal mass. The necrotic centre of this mass had a fistulous communication with the right ureter. Fibromatoses represent a spectrum of uncommon benign conditions characterised by proliferating fibrous tissue. The deep intra-abdominal form of mesenteric fibromatosis (MF), one of the rare subtypes of the 'fibromatoses' or 'desmoid tumours', grows rapidly and may become extensive. Surgery provides good results in limited disease and non-surgical modalities in cases of unresectable and residual disease.
Lath
Chinar
C
Radiology Department, Nanavati Hospital, Mumbai, India. paritoshkhanna@hotmail.com
Khanna
Paritosh C
PC
Gadewar
Swapna B
SB
Agrawal
Dilpesh
D
D000293:Adolescent; D001706:Biopsy; D017809:Fatal Outcome; D005260:Female; D018221:Fibromatosis, Abdominal / Q000000981:diagnostic imaging*; D018222:Desmoid Tumors / Q000000981:diagnostic imaging*; D006801:Humans; D008643:Mesentery / Q000473:pathology*; D015641:Radiography, Interventional; D014057:Tomography, X-Ray Computed; D014515:Ureteral Diseases / Q000000981:diagnostic imaging*; D014548:Urinary Fistula / Q000000981:diagnostic imaging*