Fibrodysplasia ossificans progressiva. An unusual cause of restricted mandibular movement.
A 9-year-old girl is presented who was initially misdiagnosed and finally diagnosed with fibrodysplasia ossificans progressiva only after presentation with progressive limitation of her mouth opening. The clinical, histopathological, and molecular biological aspects of this uncommon disorder will be discussed. Furthermore, dental and surgical guidelines will be described.
Department of Oral and Maxillofacial Surgery/Oral Pathology, Academic Centre for Dentistry Amsterdam (ACTA)/Vrije Universiteit Medical Centre, Amsterdam, The Netherlands. ehvandermeij@hotmail.com
E H
EH
van der Meij
A G
AG
Becking
I
I
van der Waal
D002648:Child; D003937:Diagnosis, Differential; D003951:Diagnostic Errors; D005097:Exostoses, Multiple Hereditary / Q000175:diagnosis; D005260:Female; D006801:Humans; D008334:Mandible / Q000503:physiopathology; D009221:Myositis Ossificans / Q000175:diagnosis*; D016059:Range of Motion, Articular; D013703:Temporal Muscle / Q000473:pathology*; D013705:Temporomandibular Joint Disorders / Q000175:diagnosis* / Q000503:physiopathology; D014313:Trismus / Q000175:diagnosis* / Q000503:physiopathology