Late presentation of alveolar capillary dysplasia in an infant.
OBJECTIVE
To report a case of late presentation of alveolar capillary dysplasia and misalignment of pulmonary veins.


METHODS
Descriptive case report.


METHODS
Pediatric intensive care unit of a tertiary care children's hospital.


METHODS
Seven-week-old female infant with severe hypoxemic respiratory failure.


CONCLUSIONS
Alveolar capillary dysplasia with misalignment of pulmonary veins is a cause of primary pulmonary hypertension in newborns that can rarely present past the newborn period. Early lung biopsy can be helpful in establishing the diagnosis and avoiding ineffective, futile, and expensive therapeutic interventions.
Shankar
Venkat
V
Divisions of Pediatric Critical Care Medicine, Monroe Carell Jr. Children's Hospital at Vanderbilt, Nashville, TN, USA.
Haque
Anwarul
A
Johnson
Joyce
J
Pietsch
John
J
D000015:Abnormalities, Multiple; D002196:Capillaries / Q000002:abnormalities; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D006976:Hypertension, Pulmonary / Q000209:etiology*; D007223:Infant; D015278:Intensive Care Units, Pediatric; D011650:Pulmonary Alveoli / Q000098:blood supply*; D011667:Pulmonary Veins / Q000002:abnormalities