Thoracic myelocystoceles--two variants.
Myelocystoceles are rare lesions. Rarer still are thoracic myelocystoceles. Two patients with thoracic myelocystoceles are being reported. The first patient presented with swelling in the thoracic region with paraplegia and incontinence. MR with MR myelography revealed the malformation to be a thoracic myelocystocele. The second patient presented with a midline cutaneous mass lesion without neurological deficit. MRI revealed a Type I split cord malformation, a CSF containing sac in the thoracic region that communicated through a stalk-like structure to the hydromyelic hemicord. Surgery in both these patients did not produce any change in the neurological status. The importance of recognizing thoracic myelocystoceles, their clinical presentation, embryology, value of MR myelography in the diagnosis and role of surgery are discussed. The differences between terminal myelocystoceles and thoracic myelocystoceles are also highlighted.
Muthukumar
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Department of Neurosurgery, Madurai Medical College, Madurai, India. prasan86@eth.net
D001139:Arnold-Chiari Malformation / Q000209:etiology / Q000503:physiopathology / Q000601:surgery; D019299:Decompression, Surgical; D005260:Female; D006801:Humans; D006849:Hydrocephalus / Q000209:etiology / Q000503:physiopathology / Q000601:surgery; D007223:Infant; D008279:Magnetic Resonance Imaging; D008297:Male; D008591:Meningomyelocele / Q000175:diagnosis* / Q000503:physiopathology / Q000601:surgery; D019635:Neurosurgical Procedures; D010264:Paraplegia / Q000209:etiology / Q000503:physiopathology; D016137:Spina Bifida Cystica / Q000175:diagnosis* / Q000503:physiopathology / Q000601:surgery; D013116:Spinal Cord / Q000002:abnormalities* / Q000473:pathology / Q000503:physiopathology; D013904:Thoracic Vertebrae / Q000002:abnormalities* / Q000473:pathology; D017211:Treatment Failure; D014549:Urinary Incontinence / Q000209:etiology / Q000503:physiopathology; D017287:Ventriculoperitoneal Shunt