MR features of angiosarcoma in a patient with Maffucci's syndrome.
Maffucci's syndrome is a rare sporadic congenital disorder associated with multiple enchondromas and soft tissue hemangiomas. These bone and soft tissue tumors have the potential of malignant transformation to various histologic types: chondrosarcoma, osteosarcoma, fibrosarcoma, and angiosarcoma. We report a rare case of Maffucci's syndrome with soft tissue angiosarcoma of the leg to illustrate MRI findings with pathologic correlations.
Miyake
Mototaka
M
Division of Diagnostic Radiology and Nuclear Medicine, National Cancer Center Hospital, Tokyo, Japan.
Tateishi
Ukihide
U
Maeda
Tetsuo
T
Arai
Yasuaki
Y
Hasegawa
Tadashi
T
Sugimura
Kazuro
K
D000293:Adolescent; D001706:Biopsy; D003287:Contrast Media; D004687:Enchondromatosis / Q000000981:diagnostic imaging / Q000473:pathology; D019786:Gadolinium DTPA; D006394:Hemangiosarcoma / Q000175:diagnosis* / Q000473:pathology / Q000601:surgery; D006801:Humans; D007866:Leg; D008279:Magnetic Resonance Imaging / Q000379:methods*; D008297:Male; D011859:Radiography; D012983:Soft Tissue Neoplasms / Q000175:diagnosis* / Q000473:pathology / Q000601:surgery; D013577:Syndrome
D003287:Contrast Media; D019786:Gadolinium DTPA