Pars plana vitrectomy for juxtapapillary capillary retinal angioma.
OBJECTIVE
To describe the treatment of juxtapapillary capillary angioma by pars plana vitrectomy (PPV) and tumor excision.


METHODS
Interventional case report.


METHODS
A 6-year-old girl with symptomatic juxtapapillary capillary retinal angioma with associated epiretinal membrane (ERM) underwent PPV and extraction of the tumor and ERM. A clinical and molecular genetic workup for the presence of von Hippel-Lindau disease (VHL) was performed.


RESULTS
A favorable functional result without tumor recurrence was achieved. Capillary retinal angioma was confirmed by histology of the surgical specimen, and familial VHL was revealed.


CONCLUSIONS
PPV and extraction of the tumor is applicable in juxtapapillary capillary retinal angioma with associated ERM. A workup for the presence of VHL is pertinent in patients presenting with this tumor entity.
Kreusel
Klaus-Martin
KM
Augenklinik, Charité-Universitätsmedizin Berlin, Campus Benjamin Franklin, Gurnemanzpfad 93, 13465 Berlin, Germany. KMKreusel@aol.com
Bechrakis
Nikolaos E
NE
Neumann
Hartmut P H
HP
Foerster
Michael H
MH
D002648:Child; D019773:Epiretinal Membrane / Q000473:pathology / Q000601:surgery; D005260:Female; D005451:Fluorescein Angiography; D018324:Hemangioma, Capillary / Q000235:genetics / Q000473:pathology / Q000601:surgery*; D006801:Humans; D019572:Retinal Neoplasms / Q000235:genetics / Q000473:pathology / Q000601:surgery*; D014792:Visual Acuity; D014821:Vitrectomy / Q000379:methods*; D051794:Von Hippel-Lindau Tumor Suppressor Protein / Q000235:genetics; D006623:von Hippel-Lindau Disease / Q000235:genetics
D051794:Von Hippel-Lindau Tumor Suppressor Protein; C497446:VHL protein, human