[Susac syndrome: case reports and review of the literature].
BACKGROUND
Susac syndrome is a rare disease of unknown pathogenesis. It consists of retinal arterial occlusion, hearing loss and encephalopathy (triad).


METHODS
The features of two cases of this syndrome are presented.


CONCLUSIONS
A high percentage of patients do not have the clinical triad at the time of onset of symptoms and, therefore, this disease may be under-diagnosed. Any patient with unexplained encephalopathy should thus be examined by an ophthalmologist and have an audiogram performed.
Augenklinik, Klinikum der Universität München. Ingrid.Reiniger@med.uni-muenchen.de
I W
IW
Reiniger
S
S
Thurau
C
C
Haritoglou
E
E
Hilgert
M
M
Dichgans
T
T
Klopstock
A
A
Kampik
D000328:Adult; D001927:Brain Diseases / Q000175:diagnosis* / Q000628:therapy*; D003937:Diagnosis, Differential; D005260:Female; D034381:Hearing Loss / Q000175:diagnosis* / Q000628:therapy*; D006801:Humans; D015356:Retinal Artery Occlusion / Q000175:diagnosis* / Q000628:therapy*; D013577:Syndrome