[Marfan syndrome].
Marfan syndrome is a hereditary disease of connective tissue with predominant involvement of cardiovascular system, skeleton and eyes. Timely diagnosis and adequate management can substantially decrease mortality in this condition. The review summarizes data of clinical observations and studies of etiology, pathogenesis, diagnosis and treatment of Marfan syndrome.
Vatutin
N T
NT
Skliannaia
E V
EV
Keting
E V
EV
D000319:Adrenergic beta-Antagonists / Q000627:therapeutic use; D006348:Cardiac Surgical Procedures / Q000379:methods; D003937:Diagnosis, Differential; D004452:Echocardiography; D004562:Electrocardiography; D006801:Humans; D008279:Magnetic Resonance Imaging; D008382:Marfan Syndrome / Q000175:diagnosis / Q000209:etiology / Q000628:therapy; D011379:Prognosis
D000319:Adrenergic beta-Antagonists