MR features of angiosarcoma in a patient with Maffucci's syndrome.
Maffucci's syndrome is a rare sporadic congenital disorder associated with multiple enchondromas and soft tissue hemangiomas. These bone and soft tissue tumors have the potential of malignant transformation to various histologic types: chondrosarcoma, osteosarcoma, fibrosarcoma, and angiosarcoma. We report a rare case of Maffucci's syndrome with soft tissue angiosarcoma of the leg to illustrate MRI findings with pathologic correlations.
Division of Diagnostic Radiology and Nuclear Medicine, National Cancer Center Hospital, Tokyo, Japan.
Mototaka
M
Miyake
Ukihide
U
Tateishi
Tetsuo
T
Maeda
Yasuaki
Y
Arai
Tadashi
T
Hasegawa
Kazuro
K
Sugimura
D000293:Adolescent; D001706:Biopsy; D003287:Contrast Media; D004687:Enchondromatosis / Q000000981:diagnostic imaging / Q000473:pathology; D019786:Gadolinium DTPA; D006394:Hemangiosarcoma / Q000175:diagnosis* / Q000473:pathology / Q000601:surgery; D006801:Humans; D007866:Leg; D008279:Magnetic Resonance Imaging / Q000379:methods*; D008297:Male; D011859:Radiography; D012983:Soft Tissue Neoplasms / Q000175:diagnosis* / Q000473:pathology / Q000601:surgery; D013577:Syndrome
D003287:Contrast Media; D019786:Gadolinium DTPA