title: Life-threatening gross hematuria due to genitourinary manifestation of Klippel-Trenaunay syndrome.
abstract: The Klippel-Trenaunay Syndrome (KTS) is defined as a triad of cutaneous capillary malformations, venous varicosities, bone and soft tissue hemi-hypertrophy. The urinary tract is involved in up to 10%. We report the clinical presentation and surgical management of a 9-year-old boy with extensive lympho-venous malformations of the bladder which led to massive recurrent gross hematuria.
authors.affiliation: Department of Urology, Julius-Maximilians-University Medical School, Würzburg, Germany. Rubenwolf_P@klinik.uni-wuerzburg.de
authors.forename: Peter
authors.initials: P
authors.lastname: Rubenwolf
authors.forename: Alexander
authors.initials: A
authors.lastname: Roosen
authors.forename: Elmar W
authors.initials: EW
authors.lastname: Gerharz
authors.forename: Antje
authors.initials: A
authors.lastname: Kirchhoff-Moradpour
authors.forename: Kassa
authors.initials: K
authors.lastname: Darge
authors.forename: Hubertus
authors.initials: H
authors.lastname: Riedmiller
mesh_terms: D002648:Child; D015653:Cystectomy; D006417:Hematuria / Q000209:etiology* / Q000601:surgery; D006801:Humans; D007715:Klippel-Trenaunay-Weber Syndrome / Q000150:complications* / Q000601:surgery; D008297:Male; D001745:Urinary Bladder Diseases / Q000209:etiology* / Q000601:surgery