[Intrathoracic localisation of desmoid tumours: a familial case of isolated desmoid tumours and current published data].
We present the case of large desmoid tumor of the anterior chest wall with pleural involvement, which persistently progressed despite hormonotherapy, chemotherapy and surgery. After many years of therapeutic failures, given the tumor size and its hemodynamic repercussions, the patient was presumed to be incurable and only supportive measures were given. One year later, the desmoid tumor had completely disappeared. Even though wide surgical excision is an essential element in the treatment of desmoid tumors, spontaneous regression may occur in very advanced disease.
Benoit
L
L
Service de chirurgie digestive, thoracique et cancérologique, CHU du Bocage, 2, boulevard Mal de Lattre de Tassigny, 21079 Dijon cedex, France. laurent.benoit@dijon-chu.fr
Cheynel
N
N
Arnould
L
L
Gouy
S
S
Fraisse
J
J
Cuisenier
J
J
D000328:Adult; D005260:Female; D018222:Desmoid Tumors / Q000000981:diagnostic imaging / Q000235:genetics / Q000601:surgery / Q000628:therapy; D005500:Follow-Up Studies; D006801:Humans; D008297:Male; D009365:Neoplasm Regression, Spontaneous; D010641:Phenotype; D010997:Pleural Neoplasms / Q000000981:diagnostic imaging / Q000235:genetics / Q000601:surgery / Q000628:therapy; D013902:Radiography, Thoracic; D013899:Thoracic Neoplasms / Q000000981:diagnostic imaging / Q000235:genetics / Q000601:surgery / Q000628:therapy; D035441:Thoracic Wall; D013997:Time Factors; D014057:Tomography, X-Ray Computed