Extranodal Rosai-Dorfman disease as a pelvic mass.
Rosai-Dorfman disease (RDD) is a rare histiocytic disorder of unknown cause. RDD most commonly involves the cervical lymph nodes, but extranodal involvement has been described. We report the case of a patient with extranodal RDD that presented as a retroperitoneal mass obstructing the left ureter. The patient underwent surgical resection of the mass, followed by a 5-month course of vinblastine. There was no evidence of progressive disease 22 months after surgery.
Leiva
B J L
BJ
Department of Obstetrics, Mayo Clinic, Jacksonville, Florida 32224, USA.
Bofill
R M
RM
Sevin
B-U
BU
Geiger
X J
XJ
D000972:Antineoplastic Agents, Phytogenic / Q000627:therapeutic use; D005260:Female; D013509:Gynecologic Surgical Procedures; D015618:Histiocytosis, Sinus / Q000150:complications / Q000175:diagnosis* / Q000628:therapy; D006801:Humans; D008875:Middle Aged; D010386:Pelvic Neoplasms / Q000175:diagnosis* / Q000209:etiology / Q000628:therapy; D012186:Retroperitoneal Neoplasms / Q000175:diagnosis* / Q000209:etiology / Q000628:therapy; D014517:Ureteral Obstruction / Q000209:etiology / Q000628:therapy; D014747:Vinblastine / Q000627:therapeutic use
D000972:Antineoplastic Agents, Phytogenic; D014747:Vinblastine