Extradural spinal cord and intraabdominal ganglioneuroblastoma.
We report a rare case of a giant extradural and intraabdominal ganglioneuroblastoma in a young Malay girl who presented to a paediatrician initially at 5 days of life with a palpable abdominal mass. Unfortunately, the parents refused any form of surgical intervention until the child was 3 years old. She subsequently underwent vascular embolisation followed by the removal of this large tumour both via the abdomen and through a laminectomy approach and subsequently refused chemotherapy. The c-myc amplication in this patient was absent and there were no chromosomal aberrations, During the 2 year folow-up the patient remained well, and ambulatory with no tumour recurrence.
Kanakaraj
G
G
Department of Neurosciences, School of Medical Sciences, Universiti Sains Malaysia, Kubang Kerian, Kelantan.
Zamzuri
I
I
Abdullah
J
J
Mohd Ghazali
M
M
Mahamood
Z
Z
Shafiee
A
A
Madhavan
M
M
Rahman
M T
MT
D000008:Abdominal Neoplasms / Q000000981:diagnostic imaging / Q000473:pathology* / Q000601:surgery; D002675:Child, Preschool; D005260:Female; D018305:Ganglioneuroblastoma / Q000000981:diagnostic imaging / Q000473:pathology* / Q000601:surgery; D006801:Humans; D009361:Neoplasm Invasiveness; D011859:Radiography; D013120:Spinal Cord Neoplasms / Q000000981:diagnostic imaging / Q000473:pathology* / Q000601:surgery