Suspected familial odontogenic keratocysts related to Gorlin Goltz syndrome.
This report represents the suspected familial case series of odontogenic keratocysts OKCs related to Gorlin Goltz syndrome GGS, a rare genetic disorder characterized mainly by multiple basal cell carcinomas, OKCs and other less frequent skeletal and neurological manifestations. Familial cases included grandmother's father, grandmother, father and son. Although they had all OKCs, father additionally possessed some of the other characteristics of GGS. We described all the patients' diagnoses, treatments and long-term follow-ups under the light of current literature.
Yucetas
Sule
S
Department of Oral and Maxillofacial Surgery, Faculty of Dentistry, Gazi University, Ankara, Turkey.
Cetiner
Sedat
S
Oygur
Tulin
T
D001478:Basal Cell Nevus Syndrome / Q000235:genetics*; D002648:Child; D005260:Female; D006801:Humans; D008297:Male; D008336:Mandibular Diseases / Q000235:genetics; D009807:Odontogenic Cysts / Q000235:genetics*