title: Caroli's syndrome with autosomal recessive polycystic kidney disease in a two month old infant.
abstract: Caroli's syndrome is a rare congenital disorder that involves intrahepatic bile duct ectasia and congenital hepatic fibrosis, frequently seen with concomitant autosomal recessive polycystic kidney disease (ARPKD). Literature on infants with ARPKD is rare. Here, we present a case of a two month old boy who was diagnosed with Caroli's syndrome and ARPKD.
authors.affiliation: Institute of Kidney Disease, Department of Pediatrics, Yonsei University College of Medicine, Seodaemun-gu, Seoul 120-752, Korea.
authors.forename: Jeong Tae
authors.initials: JT
authors.lastname: Kim
authors.forename: Yoon Jeong
authors.initials: YJ
authors.lastname: Hur
authors.forename: Jee Min
authors.initials: JM
authors.lastname: Park
authors.forename: Myung Joon
authors.initials: MJ
authors.lastname: Kim
authors.forename: Young Nyun
authors.initials: YN
authors.lastname: Park
authors.forename: Jae Seung
authors.initials: JS
authors.lastname: Lee
mesh_terms: D016767:Caroli Disease / Q000150:complications / Q000175:diagnosis* / Q000473:pathology; D006500:Hepatic Duct, Common / Q000000981:diagnostic imaging / Q000473:pathology; D006801:Humans; D007223:Infant; D007668:Kidney / Q000000981:diagnostic imaging; D008297:Male; D017044:Polycystic Kidney, Autosomal Recessive / Q000150:complications / Q000175:diagnosis* / Q000473:pathology; D014463:Ultrasonography