Undifferentiated embryonal sarcoma of the liver mimicking acute appendicitis. Case report and review of the literature.
BACKGROUND
Undifferentiated embryonal sarcoma (UES) of liver is a rare malignant neoplasm, which affects mostly the pediatric population accounting for 13% of pediatric hepatic malignancies, a few cases has been reported in adults.


METHODS
We report a case of undifferentiated embryonal sarcoma of the liver in a 20-year-old Caucasian male. The patient was referred to us for further investigation after a laparotomy in a district hospital for spontaneous abdominal hemorrhage, which was due to a liver mass. After a through evaluation with computed tomography scan and magnetic resonance imaging of the liver and taking into consideration the previous history of the patient, it was decided to surgically explore the patient. Resection of I-IV and VIII hepatic lobe. Patient developed disseminated intravascular coagulation one day after the surgery and died the next day.


CONCLUSIONS
It is a rare, highly malignant hepatic neoplasm, affecting almost exclusively the pediatric population. The prognosis is poor but recent evidence has shown that long-term survival is possible after complete surgical resection with or without postoperative chemotherapy.
Sakellaridis
Timothy
T
1st Surgical Department, 401 Army Force General Hospital of Athens, Greece. SakellaridisT@in.gr
Panagiotou
Ioannis
I
Georgantas
Themistoclis
T
Micros
George
G
Rontogianni
Dimitra
D
Antiochos
Christos
C