Ectodermal dysplasia: Retrospective study of fifteen cases.
The aim of this article is to review possible cranio-maxillofacial deformative consequences associated with hypohidrotic ectodermal dysplasia and embryonic malformations, which include dental ageneses, and describe the oral habilitation. Hypohidrotic ectodermal dysplasia patients had a clinical examination and underwent radiographic and Steiner's analyses and a respiratory capability test before assessment and treatment. Fifteen patients (eight males and seven females, aged 5-45 years) had tooth ageneses (from hypodontia to anodontia) associated with cutaneous dyshydrosis and hair and nail dystrophy. Most patients had sparse or absent hair, a short face with an unusual facial concavity, a maxillary retrusion and a relative mandibular protrusion. Dentists must conduct a comprehensive and multidisciplinary approach to these patients in order to improve their dental, masticatory, growth and orthognathic conditions.
Yavuz
Izzet
I
Department of Pediatrics, Fuculty of Dentistry, Dicle University, Diyarbakir, Turkey. iyavuz@dicle.edu.tr
Baskan
Zelal
Z
Ulku
Refik
R
Dulgergil
Turksel Coruh
TC
Dari
Osman
O
Ece
Aydin
A
Yavuz
Yasemin
Y
Dari
Kadriye Oya
KO
D000293:Adolescent; D000328:Adult; D002508:Cephalometry; D002648:Child; D002675:Child, Preschool; D004476:Ectodermal Dysplasia / Q000150:complications* / Q000000981:diagnostic imaging / Q000473:pathology*; D005260:Female; D006801:Humans; D008297:Male; D008875:Middle Aged; D009262:Nails / Q000473:pathology; D010375:Pedigree; D011859:Radiography; D012189:Retrospective Studies; D012867:Skin / Q000473:pathology; D014070:Tooth / Q000000981:diagnostic imaging / Q000473:pathology