Life-threatening gross hematuria due to genitourinary manifestation of Klippel-Trenaunay syndrome.
The Klippel-Trenaunay Syndrome (KTS) is defined as a triad of cutaneous capillary malformations, venous varicosities, bone and soft tissue hemi-hypertrophy. The urinary tract is involved in up to 10%. We report the clinical presentation and surgical management of a 9-year-old boy with extensive lympho-venous malformations of the bladder which led to massive recurrent gross hematuria.
Rubenwolf
Peter
P
Department of Urology, Julius-Maximilians-University Medical School, Würzburg, Germany. Rubenwolf_P@klinik.uni-wuerzburg.de
Roosen
Alexander
A
Gerharz
Elmar W
EW
Kirchhoff-Moradpour
Antje
A
Darge
Kassa
K
Riedmiller
Hubertus
H
D002648:Child; D015653:Cystectomy; D006417:Hematuria / Q000209:etiology* / Q000601:surgery; D006801:Humans; D007715:Klippel-Trenaunay-Weber Syndrome / Q000150:complications* / Q000601:surgery; D008297:Male; D001745:Urinary Bladder Diseases / Q000209:etiology* / Q000601:surgery