Hemiconvulsion, hemiplegia, epilepsy syndrome and inherited protein S deficiency.
A nine-year-old Nepalese girl developed hemiconvulsion, hemiplegia, epilepsy syndrome (HHE syndrome) after an episode of right-sided focal status epilepticus following acute gastroenteritis. She had left middle cerebral artery (MCA) territory infracts due to inherited protein S deficiency.
Mondal
R K
RK
Department of Pediatrics Medicine, IPGMER and SSKM Hospital, Bangur Institute of Neurology, Kolkata, India. rkm1971@indiatimes.com
Chakravorty
D
D
Das
S
S
D002648:Child; D004827:Epilepsy / Q000209:etiology*; D005260:Female; D005759:Gastroenteritis / Q000150:complications; D006429:Hemiplegia / Q000209:etiology*; D006801:Humans; D020244:Infarction, Middle Cerebral Artery / Q000209:etiology; D018455:Protein S Deficiency / Q000150:complications* / Q000175:diagnosis; D012640:Seizures / Q000209:etiology; D013577:Syndrome