[Budd-Chiari syndrome with medullar compression].
We report a case of Budd-Chiari syndrome caused by protein C deficiency. The association of thrombosis of the the inferior vein cava of the hepatic vein resulted in the development of epidural varices and a central and peripheral neurological syndrome. These symptoms, which are atypical in this disease, resolved after surgical treatment of the Budd-Chiari syndrome (cavoatrial and mesocaval stenting).
Borentain
Patrick
P
Service d'Hépato-Gastroentérologie, Hôpital de la Conception, Marseille.
Mugnier
Bénédicte
B
Barrantes
Carlos
C
Hardwigsen
Jean
J
Schleinitz
Nicolas
N
Gérolami
René
R
Letreut
Yves Patrice
YP
Botta-Fridlund
Danielle
D
D000293:Adolescent; D006502:Budd-Chiari Syndrome / Q000150:complications* / Q000209:etiology / Q000601:surgery*; D005260:Female; D006801:Humans; D008099:Liver / Q000098:blood supply*; D009422:Nervous System Diseases / Q000209:etiology; D020151:Protein C Deficiency / Q000150:complications*; D013577:Syndrome; D013927:Thrombosis; D014648:Varicose Veins / Q000209:etiology*; D014682:Vena Cava, Inferior