title: Scimitar syndrome; an unusual congenital abnormality occasionally seen in adults.
abstract: Scimitar syndrome a very rare and variable congenital disorder characterized by an anomalous connection of the pulmonary vein with the IVC. The syndrome is mostly seen in very early infancy, but was now recognized in a 46-year-old woman, who was referred to the outpatient clinic of the department of cardiology with complaints of dizziness. Contrast enhanced computer tomography (CT) showed dextroposition of the heart and a large right pulmonary vein joined the inferior vena cava (IVC) just above the level of the diaphragm. The typical features of the syndrome are discussed.
authors.affiliation: Department of cardiology, Atrium medical centre, Heerlen, the Netherlands.
authors.forename: R J P
authors.initials: RJ
authors.lastname: Haest
authors.forename: C J M
authors.initials: CJ
authors.lastname: van den Berg
authors.forename: R
authors.initials: R
authors.lastname: Goei
authors.forename: L H B
authors.initials: LH
authors.lastname: Baur
mesh_terms: D005260:Female; D006801:Humans; D008875:Middle Aged; D011667:Pulmonary Veins / Q000002:abnormalities / Q000000981:diagnostic imaging*; D012587:Scimitar Syndrome / Q000000981:diagnostic imaging*; D014057:Tomography, X-Ray Computed; D014682:Vena Cava, Inferior / Q000002:abnormalities / Q000000981:diagnostic imaging*