Anesthetic management of a patient with Gerstmann-Sträussler-Scheinker syndrome (mutation of prion protein).
Gerstmann-Sträussler-Scheinker Syndrome (GSS) is a rare, infectious syndrome related to a mutation in the prion protein. A 60-yr-old, 152-cm, 31-kg woman with GSS was scheduled for open gastrostomy. This is the first report about an anesthetic experience in a patient with GSS. We describe our experience and precautions in the anesthetic management of a GSS patient.
Department of Anesthesiology, University of Occupational and Environmental Health, School of Medicine, Fukuoka, Japan.
Motohiro
M
Nakamura
Masanori
M
Ogata
Yumiko
Y
Matsuo
Takeyoshi
T
Sata
D000402:Airway Obstruction / Q000517:prevention & control; D000758:Anesthesia / Q000379:methods*; D004866:Equipment Contamination / Q000517:prevention & control; D005260:Female; D016098:Gerstmann-Straussler-Scheinker Disease / Q000235:genetics / Q000601:surgery*; D006801:Humans; D007442:Intubation, Intratracheal / Q000295:instrumentation / Q000379:methods; D008875:Middle Aged; D009154:Mutation / Q000235:genetics*; D011328:Prions / Q000235:genetics*
D011328:Prions