Enlarged left vitelline vein remnant as a cause of cyanosis after the Fontan procedure: resolution with an Amplatzer vascular plug.
A 6-year-old girl with heterotaxy and a functional single ventricle had persistent cyanosis 4 years after a fenestrated Fontan procedure. Cardiac catheterization revealed a large venous fistula from a left-sided hepatic vein to the coronary sinus, resulting in desaturation. The anomalous vein was occluded with an Amplatzer vascular plug.
Rothman
A
A
Children's Heart Center and the Department of Pediatrics, University of Nevada School of Medicine, 3006 S. Maryland Parkway #690, Las Vegas, NV 89109, USA. rothman@childrensheartcenter.com
Acherman
R J
RJ
Luna
C F
CF
Restrepo
H
H
D002648:Child; D003097:Collateral Circulation / Q000502:physiology; D017023:Coronary Angiography; D003326:Coronary Circulation / Q000502:physiology; D003490:Cyanosis / Q000209:etiology* / Q000628:therapy*; D005260:Female; D018729:Fontan Procedure / Q000009:adverse effects*; D006503:Hepatic Veins / Q000000981:diagnostic imaging; D006801:Humans; D019736:Prostheses and Implants; D011652:Pulmonary Circulation; D016157:Vascular Fistula / Q000150:complications / Q000209:etiology* / Q000628:therapy*; D014680:Veins / Q000196:embryology