[Total urogenital sinus mobilization in the repair of ambiguous genitalia in children with congenital adrenal hyperplasia].
The surgical approach to patients with congenital adrenal hyperplasia (CAH) has been a challenge and it is still controversial. The aim of this study was to review 10 children with 46,XX CAH who underwent one-stage total urogenital sinus mobilization (TUM). Age at operation ranged from 11 to 78 months (mean= 32) and the follow-up from 15 to 36 months (mean= 26). Cosmetic results were good in 7 patients and satisfactory in 3. After a mean follow-up of 26 months, our results showed that TUM was a good option to repair ambiguous genitalia in children with CAH.
Braga
Luís Henrique P
LH
Serviço de Cirurgia Pediátrica, Hospital das Clínicas, Universidade Federal de Minas Gerais, Belo Horizonte, MG. wrbraga.bhz@terra.com.br
Silva
Ivani Novato
IN
Tatsuo
Edson Samesima
ES
D000312:Adrenal Hyperplasia, Congenital / Q000145:classification / Q000601:surgery*; D047808:Adrenogenital Syndrome / Q000601:surgery*; D002648:Child; D002675:Child, Preschool; D005260:Female; D005500:Follow-Up Studies; D013509:Gynecologic Surgical Procedures / Q000379:methods*; D006801:Humans; D007223:Infant; D016896:Treatment Outcome; D014770:Virilism / Q000601:surgery