Enlarged left vitelline vein remnant as a cause of cyanosis after the Fontan procedure: resolution with an Amplatzer vascular plug.
A 6-year-old girl with heterotaxy and a functional single ventricle had persistent cyanosis 4 years after a fenestrated Fontan procedure. Cardiac catheterization revealed a large venous fistula from a left-sided hepatic vein to the coronary sinus, resulting in desaturation. The anomalous vein was occluded with an Amplatzer vascular plug.
Children's Heart Center and the Department of Pediatrics, University of Nevada School of Medicine, 3006 S. Maryland Parkway #690, Las Vegas, NV 89109, USA. rothman@childrensheartcenter.com
A
A
Rothman
R J
RJ
Acherman
C F
CF
Luna
H
H
Restrepo
D002648:Child; D003097:Collateral Circulation / Q000502:physiology; D017023:Coronary Angiography; D003326:Coronary Circulation / Q000502:physiology; D003490:Cyanosis / Q000209:etiology* / Q000628:therapy*; D005260:Female; D018729:Fontan Procedure / Q000009:adverse effects*; D006503:Hepatic Veins / Q000000981:diagnostic imaging; D006801:Humans; D019736:Prostheses and Implants; D011652:Pulmonary Circulation; D016157:Vascular Fistula / Q000150:complications / Q000209:etiology* / Q000628:therapy*; D014680:Veins / Q000196:embryology