Poland's syndrome: report of a variant.
Poland's syndrome is a rare congenital anomaly consisting of unilateral partial or total absence of a breast and/or pectoralis major muscle, and ipsilateral symbrachydactyly. Many structural and functional abnormalities have been described in association with the syndrome. However, only a few hemostatic disorders have been reported. The case of a 12-year-old secondary school girl with unilateral hypoplasia of the breast, absence of anterior axillary fold and absence of the pectoralis major muscle is hereby presented. She also had thrombocytopenia and several episodes of spontaneous bleeding from the ipsilateral anterior chest wall. She did well on medical treatment, with no recurrence of bleeding 10 months after treatment. The author is not aware of any previously reported case of Poland's syndrome associated with bleeding disorder in Africa. This case is presented to alert clinicians of its existence and possible association with hematological disorders.
Plastic and Reconstructive Surgery Unit, Department of Surgery, Usmanu Danfodiyo University Teaching Hospital, PMB 2370, Sokoto 840001, Nigeria. legboj@yahoo.co.uk
Jacob Ndas
JN
Legbo
D002648:Child; D005260:Female; D006801:Humans; D011045:Poland Syndrome / Q000175:diagnosis* / Q000628:therapy