Pseudohypoparathyroidism: a series of three cases and an unusual presentation of ocular tetany.
Pseudohypoparathyroidism is a heterogeneous group of disorders characterised by hypocalcaemia, hyperphosphataemia, increased serum parathormone and insensitivity to the biological activity of parathormone. These patients may present for incidental surgery, procedures related to kidney stones, cataract removals and renal transplants. No particular anaesthetic agent or technique is indicated except that respiratory alkalosis should be avoided as it may further decrease ionised calcium levels and thereby precipitate tetany. In this report, we present the peri-operative management of three patients with this rare condition and describe an unusual presentation of hypocalcaemic extra-ocular muscle spasm.
Department of Anaesthesiology, All India Institute of Medical Sciences, New Delhi, India, 110029. rani_kannan2000@yahoo.com
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D000293:Adolescent; D000768:Anesthesia, General / Q000379:methods; D002387:Cataract Extraction; D002675:Child, Preschool; D005260:Female; D006801:Humans; D006996:Hypocalcemia / Q000150:complications; D007223:Infant; D007431:Intraoperative Complications; D008297:Male; D015835:Ocular Motility Disorders / Q000209:etiology*; D009801:Oculomotor Muscles; D011547:Pseudohypoparathyroidism / Q000150:complications*; D013746:Tetany / Q000209:etiology*