Proteus syndrome with huge tonsillar mass causing dysphagia: a rare case.
Proteus syndrome is a rare and highly variable hamartomatous syndrome that can affect multiple organ systems. It is characterized by hyperplasia of connective tissue, vascular malformations, epidermal naevi and hyperostosis. Most of the cases present to plastic and orthopaedic surgeons. Otolaryngologic presentations are minimal. We report such a rare case, which presented with a huge unilateral tonsillar mass causing dysphagia.
Sahni
J K
JK
Department of ENT and Head & Neck Surgery, Lady Hardinge Medical College, New Delhi, India.
Kumar
S
S
Wadhwa
V
V
Kathuria
G
G
D002675:Child, Preschool; D003680:Deglutition Disorders / Q000473:pathology* / Q000601:surgery; D006801:Humans; D006984:Hypertrophy; D008297:Male; D014066:Palatine Tonsil / Q000473:pathology* / Q000601:surgery; D016715:Proteus Syndrome / Q000473:pathology* / Q000601:surgery