[Feminizing genitoplasty and congenital adrenal hyperplasia: analysis of anatomical results].
OBJECTIVE
To evaluate the anatomical and cosmetic results of feminizing genitoplasty in girls with ambiguous genitalia due to Congenital Adrenal Hyperplasia (CAH).


METHODS
Twenty-seven females with genital ambiguity (Prader III-V) due to CAH underwent an one-stage feminizing genitoplasty and were followed for a mean time of 4 years. In twelve girls, two cutaneous labioscrotal island-flaps were associated with the conventional genitoplasty, to decrease the excess of labia majora and to enlarge the vaginal introitus. Urinary tract infections were observed in sixteen girls in the preoperative and in only seven in the postoperative period. The cosmetic results were obtained by the systematic anatomical evaluation of the different structures that compose the genitalia.


RESULTS
The results of clitoroplasty were considered good in 63% of the cases; however, 4 girls developed clitoral atrophy. An excess of labia majora was present in 25% and persistence of the urogenital sinus occurred in 11% (three children without labioscrotal island flap). The labioscrotal island flap was considered technically feasible and reproducible. Five girls had to be re-operated. The cosmetic results were considered excellent or good in 63% of the cases, satisfactory in 18.5% and unsatisfactory or bad in 18.5%.


CONCLUSIONS
The anatomical and cosmetic results were good in majority of the cases; however, some technical aspects should be adjusted, to avoid irreversible sequels and re-operations.
Miranda
Márcio Lopes
ML
Departamento de Cirurgia, Faculdade de Ciências Médicas, Hospital de Clínicas, UNICAMP, Campinas, SP. marciomiranda@terra.com.br
Oliveira Filho
Antônio G de
AG
Lemos-Marini
Sofia H V de
SH
Bustorff-Silva
Joaquim M
JM
Guerra-Júnior
Gil
G
D000312:Adrenal Hyperplasia, Congenital / Q000150:complications*; D002675:Child, Preschool; D012734:Disorders of Sex Development / Q000209:etiology* / Q000601:surgery*; D005260:Female; D005836:Genitalia, Female / Q000033:anatomy & histology / Q000601:surgery; D013509:Gynecologic Surgical Procedures / Q000379:methods; D006801:Humans; D007223:Infant