[Multiple focal nodular hyperplasia of the liver associated with congenital absence of the portal vein].
We report the 32nd case of congenital absence of portal vein in an 18-year-old female adult associated with multiple focal nodular hyperplasia of the liver. The association of various hepatic tumors has been observed in half of the publications about congenital absence of portal vein. Hepatic tumors seem to result from systemic diversion of portal vein flow with a resultant increase of arterial flow causing important vascular and nutritif changes the liver and consequent parenchymal transformation.
Schmidt
Sabine
S
Clinique des Maladies du Foie, Hôpital de l'Archet II, CHU, Nice. sabine.schmidt@chuv.hospvd.ch
Saint-Paul
Marie-Christine
MC
Anty
Rodolphe
R
Bruneton
Jean-Noël
JN
Gugenheim
Jean
J
Chevallier
Patrick
P
D000293:Adolescent; D005260:Female; D020518:Focal Nodular Hyperplasia / Q000175:diagnosis* / Q000601:surgery; D006801:Humans; D011169:Portal Vein / Q000002:abnormalities*