Decade of experience with vascular rings at a single institution.
OBJECTIVE
Over the past decade, the diagnostic workup of vascular rings has changed at our institution. Despite surgical intervention, we have observed long-term aerodigestive issues in some patients. In an effort to better characterize these pre- and postoperative issues, we reviewed a decade of experience at our institution.


METHODS
We performed a complete chart review of all patients identified as having surgical intervention for vascular ring between January 1993 and December 2003. A questionnaire was mailed to the family of each patient to ascertain a subjective assessment of long-term postoperative issues.


RESULTS
Thirty-eight patients were reviewed and categorized as to specific arch anomaly. Associated cardiac anomalies were present in 29% of patients. Chronic feeding difficulties persisted in 18% of patients, and airway issues remained in nearly half of the patients. Patients with underlying genetic syndromes had less resolution of symptoms compared with nonsyndromic children. Chronic respiratory symptoms were present in 80% of patients operated <6 months, 15% if operated between 6 months and 3 years, and 42% of patients operated after 3 years of age.


CONCLUSIONS
Aerodigestive issues may persist after vascular ring division despite initial improvement. Accurate preoperative anatomic imaging is imperative to surgical planning.
Department of Pediatrics, Children's Hospital, Creighton University, Omaha, NE 68114-4113, USA.
Carrie
C
Humphrey
Kim
K
Duncan
Scott
S
Fletcher
D000015:Abnormalities, Multiple; D000293:Adolescent; D000328:Adult; D001013:Aorta, Thoracic / Q000002:abnormalities*; D001015:Aortic Arch Syndromes / Q000150:complications / Q000175:diagnosis* / Q000601:surgery; D002648:Child; D002675:Child, Preschool; D003680:Deglutition Disorders / Q000209:etiology; D005260:Female; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D008297:Male; D012120:Respiration Disorders / Q000209:etiology; D014656:Vascular Surgical Procedures