Infantile clivus chordoma without clivus involvement: case report and review of the literature.
BACKGROUND
We present a giant clival chordoma with disseminated disease but without involvement of the clivus. To our knowledge, this is the youngest child and only the second case, presenting without base of skull involvement, in paediatric literature and the fourth reported case of a chordoma in a patient with tuberous sclerosis.


CONCLUSIONS
We discuss the subtle presentation, difficulties in diagnosis and management and also review the literature.
Department of Neurosurgery, Birmingham Children's Hospital, Steelhouse Lane, Birmingham, B4 6NH, UK.
D
D
Kombogiorgas
E J
EJ
St George
S
S
Chapman
M
M
English
G A
GA
Solanki
D000293:Adolescent; D002817:Chordoma / Q000150:complications* / Q000473:pathology; D003388:Cranial Fossa, Posterior / Q000473:pathology*; D006801:Humans; D008297:Male; D019292:Skull Base Neoplasms / Q000150:complications* / Q000473:pathology; D014057:Tomography, X-Ray Computed / Q000379:methods; D014402:Tuberous Sclerosis / Q000150:complications / Q000473:pathology