Cardiac fibroma as an inherited manifestation of nevoid basal-cell carcinoma syndrome.
We report the case of an 8-month-old male infant presenting with life-threatening ventricular tachycardia. Echocardiography revealed a left ventricular tumor. The tumor was resected through a left ventriculotomy, and the left ventricle was reconstructed after a partial ventriculectomy Histologic investigation showed a completely resected benign fibroma. The 30-year-old mother was known to have nevoid basal-cell carcinoma syndrome, which can be associated with cardiac fibromas. We believe that this is an interesting addition to the medical literature.
Bossert
Torsten
T
Department of Cardiac Surgery, Heart Center, University of Leipzig, 04289 Leipzig, Germany. TBossert11@aol.com
Walther
Thomas
T
Vondrys
David
D
Gummert
Jan Fritz
JF
Kostelka
Martin
M
Mohr
Friedrich Wilhelm
FW
D001478:Basal Cell Nevus Syndrome / Q000175:diagnosis / Q000235:genetics* / Q000601:surgery; D005350:Fibroma / Q000175:diagnosis / Q000235:genetics* / Q000601:surgery; D006338:Heart Neoplasms / Q000175:diagnosis / Q000235:genetics* / Q000601:surgery; D006801:Humans; D007223:Infant; D008297:Male