Adaptive and maladaptive behavior in children with Smith-Magenis Syndrome.
Children with Smith-Magenis Syndrome (SMS) exhibit deficits in adaptive behavior but systematic studies using objective measures are lacking. This descriptive study assessed adaptive functioning in 19 children with SMS using the Vineland Adaptive Behavior Scales (VABS). Maladaptive behavior was examined through parent questionnaires and the Childhood Autism Rating Scale. Cognitive functioning was evaluated with an age-appropriate test. Children scored below average on VABS Communication, Daily Living Skills, and Socialization scales. Learning problems and hyperactivity scales on the Conner's Parent Rating Scale were elevated, and girls were more impulsive than boys. Stereotypic and self-injurious behaviors were present in all children. Cognitive functioning was delayed and consistent with communication and daily living skills, while socialization scores were higher than IQ.
Martin
Staci C
SC
HIV and AIDS Malignancy Branch, National Cancer Institute, Bethesda, MD 20892-8200, USA. martins@mail.nih.gov
Wolters
Pamela L
PL
Smith
Ann C M
AC
D000203:Activities of Daily Living; D000223:Adaptation, Psychological; D000275:Adjustment Disorders / Q000453:epidemiology / Q000523:psychology*; D002648:Child; D002675:Child, Preschool; D003072:Cognition Disorders / Q000453:epidemiology; D003142:Communication; D005260:Female; D006801:Humans; D008297:Male; D016728:Self-Injurious Behavior / Q000453:epidemiology; D012919:Social Behavior; D012951:Socialization; D011795:Surveys and Questionnaires; D013577:Syndrome