Ovarian adrenal rest tissue in congenital adrenal hyperplasia--a patient report.
We report a young girl who died in an Addisonian crisis due to previously undiagnosed congenital adrenal hyperplasia (CAH), in whom ovarian adrenal rest tissue was detected at postmortem histopathological examination. This is a very rare complication in female patients with CAH with only two previously reported cases.
Department of Metabolic and Endocrine Disease and Radboud University, Nijmegen Medical Center, The Netherlands. H.Claahsen@cukz.umcn.nl
H L
HL
Claahsen-van der Grinten
C A
CA
Hulsbergen-van de Kaa
B J
BJ
Otten
D000224:Addison Disease / Q000150:complications* / Q000473:pathology; D000312:Adrenal Hyperplasia, Congenital / Q000150:complications* / Q000473:pathology; D000314:Adrenal Rest Tumor / Q000150:complications* / Q000473:pathology; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D007223:Infant; D010051:Ovarian Neoplasms / Q000150:complications* / Q000473:pathology