Segmental multicystic dysplasia and ureteropelvic junction obstruction in a nonduplicated kidney.
A 2-month-old child presented for evaluation of prenatal hydronephrosis. Imaging studies were consistent with a right duplex system with a dysplastic, nonfunctioning upper pole and lower pole ureteropelvic junction obstruction. We proceeded with removal of the upper pole and pyeloplasty and were surprised to find a single collecting system with a cystic, dysplastic upper pole segment and the absence of an upper pole pelvis or ureter. The rare diagnosis of a segmental multicystic dysplastic kidney with ipsilateral ureteropelvic junction obstruction was made. We present a review of the case and of previous literature on this topic.
Department of Urology, University of Miami, Miami, FL 33101, USA.
Adrienne J K
AJ
Carmack
Miguel
M
Castellan
Marcos
M
Perez-Brayfield
Rafael
R
Gosalbez
D005260:Female; D006801:Humans; D007223:Infant; D007682:Kidney Pelvis; D021782:Multicystic Dysplastic Kidney / Q000150:complications / Q000175:diagnosis / Q000601:surgery; D014517:Ureteral Obstruction / Q000150:complications / Q000175:diagnosis / Q000601:surgery