Cardiac fibroma as an inherited manifestation of nevoid basal-cell carcinoma syndrome.
We report the case of an 8-month-old male infant presenting with life-threatening ventricular tachycardia. Echocardiography revealed a left ventricular tumor. The tumor was resected through a left ventriculotomy, and the left ventricle was reconstructed after a partial ventriculectomy Histologic investigation showed a completely resected benign fibroma. The 30-year-old mother was known to have nevoid basal-cell carcinoma syndrome, which can be associated with cardiac fibromas. We believe that this is an interesting addition to the medical literature.
Department of Cardiac Surgery, Heart Center, University of Leipzig, 04289 Leipzig, Germany. TBossert11@aol.com
Torsten
T
Bossert
Thomas
T
Walther
David
D
Vondrys
Jan Fritz
JF
Gummert
Martin
M
Kostelka
Friedrich Wilhelm
FW
Mohr
D001478:Basal Cell Nevus Syndrome / Q000175:diagnosis / Q000235:genetics* / Q000601:surgery; D005350:Fibroma / Q000175:diagnosis / Q000235:genetics* / Q000601:surgery; D006338:Heart Neoplasms / Q000175:diagnosis / Q000235:genetics* / Q000601:surgery; D006801:Humans; D007223:Infant; D008297:Male