Splenic malformation in a patient with Klippel-Trenaunay syndrome: a case report.
A 22-year-old woman with a diagnosis of Klippel-Trenaunay syndrome presented with pain in the left hypochondrium and vomiting. Investigations revealed a huge splenomegaly with multiple hypodense lesions and irregular, linearly enhanced areas. She underwent splenectomy and had good postoperative recovery. Histopathology showed hemangioma/lymphangioma of the spleen.
Jindal
Ravul
R
Department of Vascular Surgery, St Mary's Hospital, Paddington, London, United Kingdom. jravul@yahoo.com
Sullivan
Rebecca
R
Rodda
Bruce
B
Arun
Dhilanthy
D
Hamady
Mohamad
M
Cheshire
Nicholas J W
NJ
D000015:Abnormalities, Multiple / Q000175:diagnosis / Q000628:therapy; D000328:Adult; D001707:Biopsy, Needle; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D007150:Immunohistochemistry; D007715:Klippel-Trenaunay-Weber Syndrome / Q000175:diagnosis*; D018570:Risk Assessment; D013154:Spleen / Q000002:abnormalities* / Q000473:pathology / Q000601:surgery*; D013156:Splenectomy / Q000379:methods; D013163:Splenomegaly / Q000473:pathology / Q000601:surgery; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome