title: Tracheal cartilaginous sleeve with cricoid cartilage involvement in Pfeiffer syndrome.
abstract: Pfeiffer syndrome is one of a group of craniosynostosis syndromes in which rare tracheal anomalies have been described. This group of patients have a poor prognosis, and mortality can be related to airway complications and respiratory distress. We report a case of type II Pfeiffer syndrome with tracheal cartilaginous sleeve and cricoid cartilage involvement. We discuss our strategy for the management of the airway of this patient.
authors.affiliation: Department of Paediatric Otolaryngology, Great Ormond Street Hospital for Children, London, UK. mdelloy@yahoo.com
authors.forename: Marianne Dawn
authors.initials: MD
authors.lastname: Elloy
authors.forename: Lesley Ann
authors.initials: LA
authors.lastname: Cochrane
authors.forename: Michelle
authors.initials: M
authors.lastname: Wyatt
mesh_terms: D000168:Acrocephalosyndactylia / Q000150:complications* / Q000601:surgery; D000402:Airway Obstruction / Q000209:etiology* / Q000601:surgery; D002675:Child, Preschool; D003413:Cricoid Cartilage / Q000002:abnormalities*; D005260:Female; D006801:Humans; D015619:Respiratory System Abnormalities / Q000150:complications*; D014132:Trachea / Q000002:abnormalities*; D014139:Tracheostomy; D014140:Tracheotomy