title: Spontaneous mesenteric hemorrhage associated with Ehlers-Danlos syndrome.
abstract: The vascular type of Ehlers-Danlos syndrome is a genetic disorder of connective tissue and is frequently associated with catastrophic arterial complications. Its surgical treatment is extremely difficult because of the fragility of vessels. This article describes three patients with vascular type of Ehlers-Danlos syndrome who developed mesenteric hemorrhage due to spontaneous arterial rupture. The clinical and molecular characteristics of the disease are briefly reviewed.
authors.affiliation: Division of Vascular Surgery, Department of Surgery, Graduate School of Medicine, University of Tokyo, Japan.
authors.forename: Akihiro
authors.initials: A
authors.lastname: Hosaka
authors.forename: Tetsuro
authors.initials: T
authors.lastname: Miyata
authors.forename: Hiroshi
authors.initials: H
authors.lastname: Shigematsu
authors.forename: Jun-o
authors.initials: JO
authors.lastname: Deguchi
authors.forename: Hideo
authors.initials: H
authors.lastname: Kimura
authors.forename: Hirokazu
authors.initials: H
authors.lastname: Nagawa
authors.forename: Osamu
authors.initials: O
authors.lastname: Sato
authors.forename: Takehiko
authors.initials: T
authors.lastname: Sakimoto
authors.forename: Tomoyuki
authors.initials: T
authors.lastname: Mochizuki
mesh_terms: D034841:Abdominal Cavity; D000328:Adult; D000783:Aneurysm / Q000209:etiology; D000784:Aortic Dissection / Q000209:etiology; D017544:Aortic Aneurysm, Abdominal / Q000209:etiology; D004535:Ehlers-Danlos Syndrome / Q000150:complications*; D017809:Fatal Outcome; D005500:Follow-Up Studies; D006406:Hematoma / Q000209:etiology; D006470:Hemorrhage / Q000209:etiology*; D006499:Hepatic Artery / Q000473:pathology; D006801:Humans; D007083:Iliac Artery / Q000473:pathology; D007583:Jejunum / Q000098:blood supply; D008297:Male; D008638:Mesenteric Arteries / Q000473:pathology; D017537:Mesenteric Artery, Inferior / Q000473:pathology; D012077:Renal Artery / Q000473:pathology; D012422:Rupture, Spontaneous; D013157:Splenic Artery / Q000473:pathology