title: [Anesthetic management of an infant with Cornelia de Lange syndrome].
abstract: We report anesthetic management of an infant with Cornelia de Lange syndrome. A 12-month-old girl with Cornelia de Lange syndrome was scheduled for ureterocystoneostomy because of vesicoureteral reflux. Preoperative physical examination suggested difficult tracheal intubation. After induction of anesthesia with sevoflurane (5%) in nitrous oxide (70%) and oxygen, a laryngeal mask airway (# 1.5) was inserted. A guide wire was inserted in the trachea through a laryngeal mask airway under direct vision of a fiberoptic bronchoscope. A tube-exchanger stylet was inserted around the guide wire after the laryngeal mask airway and fiberoptic bronchoscope had been removed. An endotracheal tube (ID 4.0 mm) was easily intubated around the tube-exchanger stylet. During the surgery, anesthesia was maintained with sevoflurane (2-3%) in nitrous oxide (50%) and oxygen. There was no perioperative pulmonary complication.
authors.affiliation: Department of Anesthesiology, Fukuoka University School of Medicine, Fukuoka 814-0180.
authors.forename: Takanao
authors.initials: T
authors.lastname: Hirai
authors.forename: Keiichi
authors.initials: K
authors.lastname: Nitahara
authors.forename: Kazuo
authors.initials: K
authors.lastname: Higa
authors.forename: Shigenori
authors.initials: S
authors.lastname: Iwakiri
authors.forename: Shinjiro
authors.initials: S
authors.lastname: Shono
authors.forename: Kiyoshi
authors.initials: K
authors.lastname: Katori
mesh_terms: D000758:Anesthesia / Q000379:methods*; D001999:Bronchoscopy; D003635:De Lange Syndrome / Q000150:complications; D005260:Female; D005336:Fiber Optic Technology; D006801:Humans; D007223:Infant; D007442:Intubation, Intratracheal / Q000379:methods*; D017214:Laryngeal Masks; D014513:Ureter / Q000601:surgery; D001743:Urinary Bladder / Q000601:surgery; D014718:Vesico-Ureteral Reflux / Q000151:congenital / Q000601:surgery