Enamel dysplasia with odontogenic fibroma-like hamartomas: review of the literature and report of a case.
This article reports on a case presenting with a rare syndrome characterized by enamel dysplasia and multiple unerupted teeth with large solid fibrous pericoronal lesions manifesting with odontogenic fibroma-like features. Our case shows in addition to these findings an anterior open bite malocclusion and gingival overgrowths. These overgrowths exhibit the microscopic features of the multiple pericoronal odontogenic fibroma-like lesions that appear to be the hallmark of this syndrome. This unusual case brings the total number documented in the literature to 5, all of which were reported from South Africa.
Feller
Liviu
L
Department of Periodontology and Oral Medicine, Medunsa Oral Health Centre, Faculty Of Dentistry, University Of Limpopo, South Africa. lfeller@ul.ac.za
Jadwat
Yusuf
Y
Bouckaert
Michael
M
Buskin
Archie
A
Raubenheimer
Erich J
EJ
D044383:Black People; D002648:Child; D003744:Dental Enamel Hypoplasia / Q000473:pathology*; D019214:Gingival Overgrowth / Q000473:pathology; D006222:Hamartoma / Q000473:pathology*; D006801:Humans; D008297:Male; D009059:Mouth Diseases / Q000473:pathology*; D024343:Open Bite / Q000473:pathology; D013019:South Africa; D013577:Syndrome; D019228:Tooth Crown / Q000473:pathology; D014097:Tooth, Unerupted / Q000473:pathology