Pulmonary vein stenosis following repair of total anomalous pulmonary venous connection.
Pulmonary vein stenosis may occur following the repair of total anomalous pulmonary venous connection and carries a poor prognosis. Conventional surgical therapies have been complicated by a high rate of re-stenosis. Sutureless pericardial marsupialization has been introduced as a technique to reduce the rate of re-stenosis. This report describes a retrospective review of a group of patients undergoing repair of acquired pulmonary vein stenosis. Presence of single-ventricle anatomy was found to be the primary preoperative risk factor for a poor outcome. The use of sutureless pericardial marsupialization was found to be associated with a significant improvement in disease-free survival.
Devaney
Eric J
EJ
Section of Cardiac Surgery, Division of Pediatric Cardiac Surgery, University of Michigan School of Medicine, Ann Arbor, MI 48109, USA. edevaney@umich.edu
Ohye
Richard G
RG
Bove
Edward L
EL
D000714:Anastomosis, Surgical / Q000009:adverse effects; D006348:Cardiac Surgical Procedures / Q000009:adverse effects*; D002675:Child, Preschool; D003251:Constriction, Pathologic; D005260:Female; D006325:Heart Atria / Q000601:surgery; D006330:Heart Defects, Congenital / Q000601:surgery*; D006801:Humans; D007223:Infant; D008297:Male; D011667:Pulmonary Veins / Q000002:abnormalities* / Q000601:surgery*; D011668:Pulmonary Veno-Occlusive Disease / Q000209:etiology / Q000601:surgery*; D016019:Survival Analysis; D016896:Treatment Outcome