title: [Congenital cystic dilatation of bile ducts].
abstract: Congenital cystic dilatation of bile ducts is a rare condition. We report a retrospective study about 18 patients having congenital bile duct cysts. According to Todani's classification, 11 cases were type I and 7 were type V. Six patients from the first group had a pancreatobiliary maljunction. A total resection of the cyst was conducted in the type I cysts. Anatomopathologic examination showed an adenocarcinoma of a common bile duct cyst. In one case, a cancer of the gall bladder associated to a common bile duct cyst in another case. Three patients with segmental dilatation of intrahepatic bile ducts (type V) underwent liver resection. Four patients had a diffuse form, one of them was treated by percutaneous drainage, and in the other cases a hepatojejunostomy was performed. Postoperative course was complicated with acute cholangitis in these four cases. Percutaneous drainage and antibiotics allowed a positive outcome in most of the cases. In one case, secondary biliary cirrhosis occurred as a long-term complication. Congenital cystic dilatation of bile ducts is considered to be a precancer state. Enterocystic anastomosis is proscribed and the resection has to be as complete as possible.
authors.affiliation: Service de Chirurgie Générale, Hôpital Mongi-Slim, 1004 Tunis, Tunisie. saberchir@yahoo.fr
authors.forename: S
authors.initials: S
authors.lastname: Mannai
authors.forename: T
authors.initials: T
authors.lastname: Kraïem
authors.forename: L
authors.initials: L
authors.lastname: Gharbi
authors.forename: N
authors.initials: N
authors.lastname: Haoues
authors.forename: H
authors.initials: H
authors.lastname: Mestiri
authors.forename: M-T
authors.initials: MT
authors.lastname: Khalfallah
mesh_terms: D000208:Acute Disease; D000293:Adolescent; D000328:Adult; D000368:Aged; D000369:Aged, 80 and over; D000714:Anastomosis, Surgical; D001649:Bile Duct Diseases / Q000151:congenital* / Q000175:diagnosis / Q000601:surgery; D001652:Bile Ducts / Q000002:abnormalities*; D001653:Bile Ducts, Intrahepatic / Q000002:abnormalities; D016767:Caroli Disease / Q000175:diagnosis / Q000601:surgery; D002648:Child; D002675:Child, Preschool; D002761:Cholangitis / Q000209:etiology; D002764:Cholecystitis / Q000150:complications; D015529:Choledochal Cyst / Q000175:diagnosis / Q000601:surgery; D003560:Cysts / Q000151:congenital* / Q000601:surgery; D004106:Dilatation; D004108:Dilatation, Pathologic / Q000151:congenital; D004322:Drainage; D005260:Female; D006498:Hepatectomy; D006801:Humans; D007583:Jejunum / Q000601:surgery; D008099:Liver / Q000601:surgery; D008297:Male; D008875:Middle Aged; D011183:Postoperative Complications; D012189:Retrospective Studies