Gorham-Stout syndrome in a male adolescent-case report and review of the literature.
Gorham-Stout syndrome is a rare disease characterized by vascular proliferation in the bones, effecting osteolysis. When it is complicated by chylothorax, the prognosis is poor. The present case illustrates successful management of chylothorax by a combination of surgery (thoracic duct ligation and excision of lymphangiomatous tissue combined with pleurodesis) and treatment with alpha-2b interferon. Treatment in 38 published cases is reviewed.
Pfleger
Andreas
A
Respiratory and Allergic Disease Division, Institute of Pathology, Auenbruggerplatz 30, 8036 Graz, Styria, Austria. Andreas.Pfleger@meduni-graz.at
Schwinger
Wolfgang
W
Maier
Alfred
A
Tauss
Josef
J
Popper
Helmut H
HH
Zach
Maximilian S
MS