Anesthesia in a child with fibrodysplasia ossificans progressiva.
We describe the anesthesia management of a 12-year-old girl, diagnosed with fibrodysplasia ossificans progressiva (FOP), who presented with a submandibular abscess. FOP is a rare, inherited disorder with heterotopic bone formation and progressive musculoskeletal disability. This disability ultimately confines patients to a wheelchair. Minor trauma following dental treatment may lead to ankylosis of the jaw. Subsequent to this disability, which resulted in poor dental hygiene, our patient developed a dental abscess. This spread along the mandibular margin and under the tongue. She presented with an impending airway compromise in an already difficult situation. The options for airway management in a child with limited mouth opening are discussed.
Vashisht
Rita
R
Anaesthetic Department, Royal Manchester Children's Hospital, Pendlebury, Manchester, UK. VAshokKum@aol.com
Prosser
Dylan
D
D000556:Ambulatory Surgical Procedures; D000758:Anesthesia / Q000379:methods*; D002648:Child; D005260:Female; D006801:Humans; D007442:Intubation, Intratracheal / Q000379:methods; D008334:Mandible / Q000601:surgery*; D009221:Myositis Ossificans / Q000150:complications*