Deficient activity of von Willebrand factor-cleaving protease in thrombotic thrombocytopenic purpura in the setting of adult-onset Still's disease.
Hirata
S
S
Okamoto
H
H
Ohta
S
S
Kobashigawa
T
T
Uesato
M
M
Kawaguchi
Y
Y
Tateishi
M
M
Hara
M
M
Kamatani
N
N
Tsai
H-M
HM
D051722:ADAM Proteins / Q000172:deficiency*; D000071120:ADAMTS13 Protein; D000328:Adult; D001327:Autoimmune Diseases / Q000201:enzymology*; D005260:Female; D006801:Humans; D011697:Purpura, Thrombotic Thrombocytopenic / Q000201:enzymology*; D016706:Still's Disease, Adult-Onset / Q000201:enzymology*
D051722:ADAM Proteins; D000071120:ADAMTS13 Protein; C099604:ADAMTS13 protein, human