title: Primary Ewing sarcoma of the petrous temporal bone: an exceptional cause of facial palsy and deafness in a nursling.
abstract: BACKGROUND
  Primary Ewing sarcoma affecting the skull base in general and the petrous bone in particular is extremely rare with only 4 reports of Ewing sarcoma arising in the petrous temporal bone in the international medical literature.
  
  
  METHODS
  The authors report for the first time a case of a primary Ewing sarcoma of the petrous temporal bone in a 5-month-old nursling, which became apparent with a complete peripheral facial palsy and ipsilateral surdity.
  
  
  RESULTS
  The neoformation was treated by systemic chemotherapy and radiation of the tumor region. The diagnostic steps, therapy, and development of the child are described in detail; the literature concerning Ewing sarcoma originating from the skull in general and from the petrous temporal bone in particular is reviewed.
  
  
  CONCLUSIONS
  The highlights of this case are an extremely uncommon location, an unusual age of presentation, as well as a unique set of symptoms.
authors.affiliation: Department of Otorhinolaryngology, Head and Neck Surgery, Freiburg Medical School, Killianstrasse 5, 79106 Freiburg, Germany. pfeiffer@hno.ukl.uni-freiburg.de
authors.forename: Jens
authors.initials: J
authors.lastname: Pfeiffer
authors.forename: Carsten Christof
authors.initials: CC
authors.lastname: Boedeker
authors.forename: Gerd Jürgen
authors.initials: GJ
authors.lastname: Ridder
mesh_terms: D000971:Antineoplastic Combined Chemotherapy Protocols / Q000627:therapeutic use; D002675:Child, Preschool; D003131:Combined Modality Therapy; D003638:Deafness / Q000209:etiology*; D005158:Facial Paralysis / Q000209:etiology*; D006801:Humans; D008297:Male; D010579:Petrous Bone; D011879:Radiotherapy Dosage; D012512:Sarcoma, Ewing / Q000150:complications* / Q000175:diagnosis / Q000188:drug therapy / Q000532:radiotherapy; D012888:Skull Neoplasms / Q000150:complications* / Q000175:diagnosis / Q000188:drug therapy / Q000532:radiotherapy; D016896:Treatment Outcome