Giant mesenteric fibromatosis presenting as small bowel obstruction.
Mesenteric fibromatosis is a proliferative fibroblastic neoplasia of the small intestine mesentery that may occur as a unique or multiple formation. Mesenteric fibromatosis is a rare, locally aggressive neoplasm and may present with abdominal discomfort, abdominal pain, weight loss, or symptoms of ureteral obstruction, mesenteric ischemia, or intestinal obstruction. It is of the utmost importance to distinguish mesenteric fibromatosis from gastrointestinal stromal tumors. Histopathology accurately differentiates between these two distinct entities. The preferred treatment is local surgical excision with a margin of uninvolved tissue. The involvement of important structures like the superior mesenteric artery and the superior mesenteric vein may pose a challenge during resection, but these tumors can be excised and the vessels repaired primarily.
Holubar
Stefan
S
Department of Surgery, North Shore University/Long Island Jewish Medical Center, Manhasset, New York, USA.
Dwivedi
Amit J
AJ
O'Connor
James
J
D003937:Diagnosis, Differential; D018221:Fibromatosis, Abdominal / Q000150:complications* / Q000175:diagnosis* / Q000000981:diagnostic imaging / Q000473:pathology; D046152:Gastrointestinal Stromal Tumors / Q000473:pathology; D006801:Humans; D007415:Intestinal Obstruction / Q000209:etiology*; D008297:Male; D008643:Mesentery; D008875:Middle Aged; D009361:Neoplasm Invasiveness; D011859:Radiography