Primary Ewing sarcoma of the petrous temporal bone: an exceptional cause of facial palsy and deafness in a nursling.
BACKGROUND
Primary Ewing sarcoma affecting the skull base in general and the petrous bone in particular is extremely rare with only 4 reports of Ewing sarcoma arising in the petrous temporal bone in the international medical literature.


METHODS
The authors report for the first time a case of a primary Ewing sarcoma of the petrous temporal bone in a 5-month-old nursling, which became apparent with a complete peripheral facial palsy and ipsilateral surdity.


RESULTS
The neoformation was treated by systemic chemotherapy and radiation of the tumor region. The diagnostic steps, therapy, and development of the child are described in detail; the literature concerning Ewing sarcoma originating from the skull in general and from the petrous temporal bone in particular is reviewed.


CONCLUSIONS
The highlights of this case are an extremely uncommon location, an unusual age of presentation, as well as a unique set of symptoms.
Pfeiffer
Jens
J
Department of Otorhinolaryngology, Head and Neck Surgery, Freiburg Medical School, Killianstrasse 5, 79106 Freiburg, Germany. pfeiffer@hno.ukl.uni-freiburg.de
Boedeker
Carsten Christof
CC
Ridder
Gerd Jürgen
GJ
D000971:Antineoplastic Combined Chemotherapy Protocols / Q000627:therapeutic use; D002675:Child, Preschool; D003131:Combined Modality Therapy; D003638:Deafness / Q000209:etiology*; D005158:Facial Paralysis / Q000209:etiology*; D006801:Humans; D008297:Male; D010579:Petrous Bone; D011879:Radiotherapy Dosage; D012512:Sarcoma, Ewing / Q000150:complications* / Q000175:diagnosis / Q000188:drug therapy / Q000532:radiotherapy; D012888:Skull Neoplasms / Q000150:complications* / Q000175:diagnosis / Q000188:drug therapy / Q000532:radiotherapy; D016896:Treatment Outcome