title: [Ocular manifestations of pseudoxanthoma elasticum].
abstract: BACKGROUND
  Pseudoxanthoma elasticum (PXE) is a hereditary disease characterized by skin, ocular, and cardiovascular lesions. Its prognosis depends mainly on the ocular and vascular lesions.
  
  
  METHODS
  This study included 11 patients with PXE. All patients had an ophthalmologic examination.
  
  
  RESULTS
  All patients had ocular lesions. Seven (63%) had angioid streaks and two, macular lesions. One patient had bilateral intrapapillary drusen (of the optic nerve head).
  
  
  CONCLUSIONS
  Ocular lesions in PXE had substantial diagnostic value. Ocular complications affect functional prognosis. These patients must undergo routine ophthalmologic examinations to look for ocular manifestations and their complications.
authors.affiliation: Service d'ophtalmologie, CHU Habib Bourguiba, Sfax, Tunisie.
authors.forename: Bourane
authors.initials: B
authors.lastname: Kamoun
authors.forename: Héla
authors.initials: H
authors.lastname: Khlif
authors.forename: Madiha
authors.initials: M
authors.lastname: Mseddi
authors.forename: Imène
authors.initials: I
authors.lastname: Sayadi
authors.forename: Hamida
authors.initials: H
authors.lastname: Turki
authors.forename: Abdelmagid
authors.initials: A
authors.lastname: Zahaf
authors.forename: Jamel
authors.initials: J
authors.lastname: Feki
mesh_terms: D000293:Adolescent; D000328:Adult; D005128:Eye Diseases / Q000209:etiology*; D005260:Female; D006801:Humans; D008297:Male; D011561:Pseudoxanthoma Elasticum / Q000150:complications*