Congenital insensitivity-to-pain with anhidrosis (CIPA): a case report with 4-year follow-up.
Congenital Insensitivity-to-pain with anhidrosis (CIPA) is a rare disorder in which pain perception is absent from birth, despite the fact that all other sensory modalities remain intact or minimally impaired and tendon reflexes are present. The challenge in dentistry is to manage the self-mutilation behavior avoiding serious damages especially to oral structures, hands and fingers. A Brazilian case of CIPA is presented and discussed with clinical documentation of the oral-related problems over a 4-year follow-up. A conservative treatment (mouthguard-like appliance) was proposed with the objective to avoid full mouth extraction.
Schalka
Mariângela Milena Santos
MM
FUNDECTO-University of São Paulo, São Paulo, Brazil. marischalka@terra.com.br
Corrêa
Maria Salete Nahás Pires
MS
Ciamponi
Ana Lídia
AL
D003241:Consanguinity; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D007007:Hypohidrosis / Q000150:complications*; D007223:Infant; D009064:Mouth Protectors; D019226:Oral Ulcer / Q000209:etiology*; D000699:Pain Insensitivity, Congenital / Q000150:complications*; D012652:Self Mutilation / Q000209:etiology* / Q000517:prevention & control; D014084:Tooth Avulsion / Q000209:etiology*