A familial variant of the Scimitar syndrome with a meandering pulmonary vein.
We report a rare variant of the Scimitar syndrome, in which the right lower pulmonary vein takes a meandering course before finally connecting in normal fashion to the left atrium. The pulmonary parenchymal segment drained by the tortuous vein is supplied by a systemic collateral artery, which was coiled via a catheter. We also closed the intracardiac defects by surgery. The elder brother of the patient had classical Scimitar syndrome.
Al-Naami
Ghassan H
GH
Cardiac Science Department, Pediatric Cardiology Division, King AbdulAziz Medical City, Riyadh, Saudi Arabia. naamig@ngha.med.sa
Abu-Sulaiman
Riyadh M
RM
D000015:Abnormalities, Multiple; D000792:Angiography; D006348:Cardiac Surgical Procedures / Q000379:methods; D004452:Echocardiography; D006801:Humans; D007223:Infant; D008297:Male; D011667:Pulmonary Veins / Q000002:abnormalities* / Q000601:surgery; D012587:Scimitar Syndrome / Q000175:diagnosis* / Q000601:surgery