[Filiation hamartoma polyposis dysplasia and small bowel adenocarcinoma].
Peutz-Jeghers syndrome is a hereditary affection with dominant autosomal transmission. The risk of cancerisation is largely higher than that in the general population. Dysplasia is rare. Transformation of the polyposis hamartoma into a site of dysplasia then into adenocarcinoma has been rarely reported. The authors report the case of a 14 year-old patient, having a severe dysplasia on ileal polyposis hamartoma related to the syndrome of Peutz-Jeghers.
Khelifi
Slim
S
Service de chirurgie générale, Hopital Habib Thameur, Tunis.
Bouhafa
Ahmed
A
Agrebi
Wajdi
W
Cherif
Abderraouf
A
Ben
Maamer
M
Khayat
Olfa
O
Letaief
Abedelmajid
A
D000230:Adenocarcinoma / Q000150:complications* / Q000473:pathology; D000293:Adolescent; D006801:Humans; D007078:Ileal Neoplasms / Q000150:complications* / Q000473:pathology; D008297:Male; D010580:Peutz-Jeghers Syndrome / Q000150:complications / Q000175:diagnosis*