Hunter syndrome (MPS II-B): a report of bilateral vitreous floaters and maculopathy.
OBJECTIVE
To describe bilateral vitreous opacities and maculopathy in a child with Hunter syndrome.


METHODS
A case involving fundus examination, photography, and optical coherence tomography. Medline and Embase searches found no reference to vitreous or macular abnormalities in Hunter syndrome.


RESULTS
A two-year-old boy with Hunter syndrome was found to have asymmetric, bilateral, free-floating vitreous opacities that remained stable over six years. Amblyopia and exotropia improved with occlusion therapy and spectacle correction. Visual acuity decreased when bilateral maculopathy supervened.


CONCLUSIONS
Screening for vitreous abnormalities and maculopathy may be important in diagnosing, treating, and explaining visual loss in Hunter syndrome.
Anawis
Monique A
MA
Department of Surgery, Weiss Memorial Hospital/University of Chicago, Division of Ophthalmology, Chicago, IL, USA. moniqueanawis@earthlink.net
D002675:Child, Preschool; D005128:Eye Diseases / Q000175:diagnosis*; D006801:Humans; D008266:Macula Lutea / Q000473:pathology*; D008297:Male; D016532:Mucopolysaccharidosis II / Q000175:diagnosis*; D012164:Retinal Diseases / Q000175:diagnosis*; D041623:Tomography, Optical Coherence; D014822:Vitreous Body / Q000473:pathology*