title: [Filiation hamartoma polyposis dysplasia and small bowel adenocarcinoma].
abstract: Peutz-Jeghers syndrome is a hereditary affection with dominant autosomal transmission. The risk of cancerisation is largely higher than that in the general population. Dysplasia is rare. Transformation of the polyposis hamartoma into a site of dysplasia then into adenocarcinoma has been rarely reported. The authors report the case of a 14 year-old patient, having a severe dysplasia on ileal polyposis hamartoma related to the syndrome of Peutz-Jeghers.
authors.affiliation: Service de chirurgie générale, Hopital Habib Thameur, Tunis.
authors.forename: Slim
authors.initials: S
authors.lastname: Khelifi
authors.forename: Ahmed
authors.initials: A
authors.lastname: Bouhafa
authors.forename: Wajdi
authors.initials: W
authors.lastname: Agrebi
authors.forename: Abderraouf
authors.initials: A
authors.lastname: Cherif
authors.forename: Maamer
authors.initials: M
authors.lastname: Ben
authors.forename: Olfa
authors.initials: O
authors.lastname: Khayat
authors.forename: Abedelmajid
authors.initials: A
authors.lastname: Letaief
mesh_terms: D000230:Adenocarcinoma / Q000150:complications* / Q000473:pathology; D000293:Adolescent; D006801:Humans; D007078:Ileal Neoplasms / Q000150:complications* / Q000473:pathology; D008297:Male; D010580:Peutz-Jeghers Syndrome / Q000150:complications / Q000175:diagnosis*