Persistent fetal vasculature associated with orbital lymphangioma.
Persistent fetal vasculature (PFV), also known as persistent hyperplastic primary vitreous (PHPV), is a failure of regression of the primary vitreous, which usually occurs in isolation. Orbital lymphangiomas present in early life with eyelid swelling or proptosis and are not associated with intraocular abnormalities. We report the case of a male infant with PHPV and ipsilateral orbital lymphangioma.
Williams
Christopher P R
CP
Southampton Eye Unit, Southampton General Hospital, Tremona Road, Southampton, United Kingdom. cprwilliams@doctors.org.uk
Marsh
Catherine S
CS
Hodgkins
Peter R
PR
D003937:Diagnosis, Differential; D005124:Eye Abnormalities / Q000150:complications* / Q000175:diagnosis; D005500:Follow-Up Studies; D006801:Humans; D007223:Infant; D008202:Lymphangioma / Q000150:complications* / Q000175:diagnosis; D008279:Magnetic Resonance Imaging; D008297:Male; D009918:Orbital Neoplasms / Q000150:complications* / Q000175:diagnosis; D012163:Retinal Detachment / Q000175:diagnosis / Q000209:etiology; D014822:Vitreous Body / Q000002:abnormalities*