[Intermediary form of Foix-Chavany-Marie / Worster-Drought syndromes associated to involuntary movements: neuropsychological and phonoaudiological features].
The Foix-Chavany-Marie syndrome (FCMS) is characterized by apraxia of speech associated to bilateral central facio-linguo-velo-pharyngeal paralysis, with automatic-voluntary dissociation. In Worster-Drought Syndrome (WDS), dysarthria is remarkable. We report an 18-year-old female, with clinical and radiological findings of intermediary form of FCMS/WDS, and showing involuntary movements, an unusual fact.
Vasconcelos
Marcio Gadelha
MG
Disciplina de Neurologia Clínica da Universidade Federal de São Paulo, São Paulo, SP, Brazil. mgadvas@yahoo.com.br
Fiorot
José Antonio
JA
Sarkovas
Caroline
C
Pinto
Aline Pereira Martins
AP
Barsottini
Orlando G P
OG
Gabbai
Alberto Alain
AA
D000293:Adolescent; D001072:Apraxias / Q000150:complications / Q000175:diagnosis / Q000188:drug therapy; D003680:Deglutition Disorders / Q000150:complications* / Q000175:diagnosis / Q000188:drug therapy; D004401:Dysarthria / Q000150:complications / Q000175:diagnosis / Q000188:drug therapy; D004569:Electroencephalography; D005158:Facial Paralysis / Q000150:complications* / Q000175:diagnosis / Q000188:drug therapy; D005260:Female; D006801:Humans; D008279:Magnetic Resonance Imaging; D009483:Neuropsychological Tests; D013064:Speech Disorders / Q000150:complications* / Q000175:diagnosis / Q000188:drug therapy; D013577:Syndrome