title: Biventricular repair of Ebstein's anomaly with pulmonary atresia in a low birth weight neonate.
abstract: Cyanotic neonates with Ebstein's anomaly associated with pulmonary atresia are a subgroup with the high mortality rate in pediatric cardiac surgery. We report a case of a severely symptomatic low birth weight neonate with Ebstein's anomaly and pulmonary atresia. A biventricular repair with Danielson-type tricuspid valve repair was performed. The baby tolerated the procedure with adequate hemodynamics, but died of peritoneal hemorrhage on the second postoperative day. This report could be an addition to the recent literature regarding the feasibility of biventricular repair for symptomatic neonates with Ebstein's anomaly even in low birth weight neonates.
authors.affiliation: Department of Cardiac Surgery, University of Tsukuba, Tsukuba, Japan. yuji3@md.tsukuba.ac.jp
authors.forename: Yuji
authors.initials: Y
authors.lastname: Hiramatsu
authors.forename: Mio
authors.initials: M
authors.lastname: Noma
authors.forename: Hitoshi
authors.initials: H
authors.lastname: Horigome
authors.forename: Miho
authors.initials: M
authors.lastname: Takahashi-Igari
authors.forename: Yuzuru
authors.initials: Y
authors.lastname: Sakakibara
mesh_terms: D000015:Abnormalities, Multiple; D006348:Cardiac Surgical Procedures / Q000009:adverse effects; D004374:Ductus Arteriosus, Patent / Q000601:surgery; D004437:Ebstein Anomaly / Q000150:complications / Q000601:surgery*; D017809:Fatal Outcome; D005260:Female; D006471:Gastrointestinal Hemorrhage / Q000209:etiology; D006344:Heart Septal Defects, Atrial / Q000601:surgery; D006352:Heart Ventricles / Q000002:abnormalities / Q000601:surgery; D006801:Humans; D007230:Infant, Low Birth Weight; D007231:Infant, Newborn; D010537:Peritoneum / Q000098:blood supply / Q000293:injuries; D019106:Postoperative Hemorrhage / Q000209:etiology; D018633:Pulmonary Atresia / Q000150:complications / Q000601:surgery*; D014262:Tricuspid Valve Insufficiency / Q000151:congenital / Q000601:surgery