title: Isolated left atrial amyloidosis: acute premitral stenosis secondary to spontaneous intramural left atrial hemorrhagic dissection.
abstract: This case presentation describes the very rare condition of isolated atrial amyloidosis and it's associated complications. A 53-year-old male presented to hospital in severe pulmonary edema secondary to spontaneous intramural left atrial hemorrhage and subsequent wall dissection causing acute "pre-mitral valve" obstruction. The patient was subsequently found to have AL subtype amyloid, which has never before been reported in isolated atrial amyloidosis. The prognosis is poor in AL type amyloidosis with cardiac involvement.
authors.affiliation: Department of Intensive Care, Royal Perth Hospital, Perth, Western Australia. Cyrus.Edibam@health.wa.gov.au
authors.forename: Cyrus
authors.initials: C
authors.lastname: Edibam
authors.forename: David
authors.initials: D
authors.lastname: Playford
authors.forename: Michael
authors.initials: M
authors.lastname: Texler
authors.forename: Mark
authors.initials: M
authors.lastname: Edwards
mesh_terms: D000208:Acute Disease; D000686:Amyloidosis / Q000150:complications / Q000000981:diagnostic imaging*; D000784:Aortic Dissection / Q000150:complications* / Q000000981:diagnostic imaging*; D006325:Heart Atria / Q000000981:diagnostic imaging; D006341:Heart Rupture / Q000150:complications / Q000000981:diagnostic imaging; D006470:Hemorrhage / Q000150:complications* / Q000000981:diagnostic imaging*; D006801:Humans; D008297:Male; D008875:Middle Aged; D008946:Mitral Valve Stenosis / Q000000981:diagnostic imaging* / Q000209:etiology*; D014463:Ultrasonography