Isolated left atrial amyloidosis: acute premitral stenosis secondary to spontaneous intramural left atrial hemorrhagic dissection.
This case presentation describes the very rare condition of isolated atrial amyloidosis and it's associated complications. A 53-year-old male presented to hospital in severe pulmonary edema secondary to spontaneous intramural left atrial hemorrhage and subsequent wall dissection causing acute "pre-mitral valve" obstruction. The patient was subsequently found to have AL subtype amyloid, which has never before been reported in isolated atrial amyloidosis. The prognosis is poor in AL type amyloidosis with cardiac involvement.
Edibam
Cyrus
C
Department of Intensive Care, Royal Perth Hospital, Perth, Western Australia. Cyrus.Edibam@health.wa.gov.au
Playford
David
D
Texler
Michael
M
Edwards
Mark
M
D000208:Acute Disease; D000686:Amyloidosis / Q000150:complications / Q000000981:diagnostic imaging*; D000784:Aortic Dissection / Q000150:complications* / Q000000981:diagnostic imaging*; D006325:Heart Atria / Q000000981:diagnostic imaging; D006341:Heart Rupture / Q000150:complications / Q000000981:diagnostic imaging; D006470:Hemorrhage / Q000150:complications* / Q000000981:diagnostic imaging*; D006801:Humans; D008297:Male; D008875:Middle Aged; D008946:Mitral Valve Stenosis / Q000000981:diagnostic imaging* / Q000209:etiology*; D014463:Ultrasonography