Cardiac pacing in a patient with diaphragm pacing for congenital central hypoventilation syndrome (Ondine's curse).
Mechanical ventilation support and diaphragm pacing has improved the prognosis of patients with idiopathic congenital central hypoventilation syndrome (CCHS; Ondine's curse). However, severe bradyarrhythmias may occur. This report is about a patient who was supplied with a bilateral diaphragm pacing system at early childhood. At the age of 17 years, he experienced multiple syncopes due to sinus nodal arrest, which was successfully treated by the implantation of a dual chamber pacemaker.
Kolb
Christof
C
Deutsches Herzzentrum München and 1. Med. Klinik, Klinikum rechts der Isar der Technischen Universität München, Munich, Germany. kolb@dhm.mhn.de
Eicken
Andreas
A
Zrenner
Bernhard
B
Schmitt
Claus
C
D000293:Adolescent; D002304:Cardiac Pacing, Artificial; D003964:Diaphragm; D006801:Humans; D008297:Male; D020182:Sleep Apnea, Central / Q000151:congenital* / Q000628:therapy*