[Surgical management of a preaortic paraganglioma: Report of one case].
Paragangliomas (PG) are rare and often diagnosed in the young adult. One case of retroperitoneal preaortic paraganglioma localised between the celiac trunk and the superior mesenteric artery is reported. The management of paraganglioma involves endocrinologists, geneticists and surgeons but the only potentially curative treatment remains surgical resection. Pathology reports can not always discriminate between benign or malignant tumors. Hereditary in paraganglioma occurs in approximately 25% of cases. Genetic investigation is therefore mandatory in all patients with PG. Since the type of genetic mutation is correlated with tumoral aggressiveness, genetic investigation results should be taken into account when a surgical procedure is planned.
Puche
P
P
Service médicochirurgical des maladies de l'appareil digestif et transplantation hépatique, hôpital Saint-Eloi, 80, avenue Augustin-Fliche, 34295 Montpellier, France. p-puche@chu-montpellier.fr
Jacquet
E
E
Colombo
P-E
PE
Jaber
S
S
Alric
P
P
Carabalona
J-P
JP
Bouyabrine
H
H
Domergue
J
J
Navarro
F
F
D000328:Adult; D006801:Humans; D008297:Male; D010235:Paraganglioma / Q000601:surgery*; D012186:Retroperitoneal Neoplasms / Q000601:surgery*