title: Neonatal epithelioid sarcoma: a distinct clinical entity?
abstract: Epithelioid sarcoma is a rare soft tissue sarcoma with a propensity for local aggressiveness, regional nodal spread, and pulmonary metastases. We report a case of epithelioid sarcoma in a neonate with bilateral optic nerve hypoplasia who developed liver, kidney, and bone metastases. The unusual presenting features and pattern of disease progression in this patient suggest that a different disease evaluation strategy should be considered for infants with epithelioid sarcoma.
authors.affiliation: Department of Surgery, St Jude Children's Research Hospital, Memphis, TN 38105-2794, USA.
authors.forename: Himesh
authors.initials: H
authors.lastname: Gupta
authors.forename: Andrew M
authors.initials: AM
authors.lastname: Davidoff
authors.forename: Bhaskar N
authors.initials: BN
authors.lastname: Rao
authors.forename: Jesse J
authors.initials: JJ
authors.lastname: Jenkins
authors.forename: Sheri L
authors.initials: SL
authors.lastname: Spunt
mesh_terms: D005542:Forearm; D006801:Humans; D007231:Infant, Newborn; D007680:Kidney Neoplasms / Q000175:diagnosis / Q000556:secondary* / Q000601:surgery; D008113:Liver Neoplasms / Q000175:diagnosis / Q000556:secondary* / Q000601:surgery; D009362:Neoplasm Metastasis; D009364:Neoplasm Recurrence, Local; D012509:Sarcoma / Q000175:diagnosis / Q000556:secondary* / Q000601:surgery; D012983:Soft Tissue Neoplasms / Q000175:diagnosis / Q000473:pathology* / Q000601:surgery; D013848:Thigh