Concordant ventriculoarterial connections with parallel arterial trunks in the setting of isomerism of the right atrial appendages.
We describe an autopsied specimen, from an infant who died in 1967, in which concordant ventriculoarterial connections coexisted with parallel arterial trunks, usually described as "anatomically corrected malposition." Based on their shape, the extent of the pectinate muscles, and the absence of a coronary sinus, we diagnosed isomeric right atrial appendages. Despite this, the arrangement of the remaining thoracic and abdominal organs, as well as the patterns of venous drainage, was almost completely mirror imaged.
Crossland
David S
DS
Department of Cardiology, Royal Childern's Hospital, Flemington Road, Parkville, Victoria 3052, Australia.
Anderson
Robert H
RH
Wilkinson
James L
JL
D000015:Abnormalities, Multiple; D020517:Atrial Appendage / Q000002:abnormalities*; D001344:Autopsy; D003330:Coronary Vessel Anomalies / Q000473:pathology; D003914:Dextrocardia / Q000473:pathology; D017809:Fatal Outcome; D006330:Heart Defects, Congenital / Q000473:pathology*; D006345:Heart Septal Defects, Ventricular / Q000473:pathology; D006352:Heart Ventricles / Q000002:abnormalities; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D011667:Pulmonary Veins / Q000002:abnormalities; D014188:Transposition of Great Vessels / Q000473:pathology; D014683:Vena Cava, Superior / Q000002:abnormalities