Mast cell disease: surgical and anesthetic implications.
Mast cell disease (MCD) is a clonal disorder of the mast cell and its precursor cells. Cardiac surgery in MCD is rarely described. We report an unusual case of a 14-year-old girl who was admitted for atrial septal defect closure and incidentally found to have hepatosplenomegaly with lymphadenopathy who underwent a successful open-heart surgery, after a diagnosis of MCD.
Damodar
Sharat
S
Department of Haematology, Christian Medical College, Bangalore, Karnataka, India. drsharat_damodar@yahoo.co.in
John
Colin Noel
CN
Gopalakrishnan
Gayathri
G
Nair
Sheila
S
Samuel
Rekha
R
Thomas
Mathew
M
Shetty
Devi Prasad
DP
D000293:Adolescent; D000758:Anesthesia / Q000379:methods*; D001853:Bone Marrow / Q000473:pathology; D005260:Female; D006344:Heart Septal Defects, Atrial / Q000150:complications / Q000601:surgery; D006529:Hepatomegaly / Q000209:etiology; D006801:Humans; D008206:Lymphatic Diseases / Q000209:etiology; D034721:Mastocytosis, Systemic / Q000150:complications / Q000175:diagnosis* / Q000473:pathology; D013163:Splenomegaly / Q000209:etiology / Q000473:pathology