title: Cutaneous metastasis of pheochromocytoma in multiple endocrine neoplasia IIB.
abstract: Pheochromocytoma is a rare tumor originating from neuroectodermic cells. Only 10% of these tumors are malignant. There are many familial forms of this tumor, including multiple endocrine neoplasia type II, Von Hippel-Lindau syndrome, and neurofibromatosis type I. Skin manifestations of pheochromocytoma are rare, and cutaneous metastasis in patients with multiple endocrine neoplasia IIB has never been described. The case of a patient with multiple endocrine neoplasia IIB who presented malignant pheochromocytoma with multiple cutaneous metastasis is described.
authors.affiliation: Catholic University of Pôrto Alegre, Brazil. rodrigoduquia@terra.com.br
authors.forename: Rodrigo Pereira
authors.initials: RP
authors.lastname: Duquia
authors.forename: Hiram Larangeira
authors.initials: HL
authors.lastname: de Almeida
authors.forename: Moacir
authors.initials: M
authors.lastname: Traesel
authors.forename: Heitor Alberto
authors.initials: HA
authors.lastname: Jannke
mesh_terms: D000310:Adrenal Gland Neoplasms / Q000737:chemistry / Q000473:pathology*; D000328:Adult; D006801:Humans; D007150:Immunohistochemistry; D008297:Male; D018814:Multiple Endocrine Neoplasia Type 2b / Q000737:chemistry / Q000473:pathology*; D010673:Pheochromocytoma / Q000737:chemistry / Q000556:secondary*; D012878:Skin Neoplasms / Q000737:chemistry / Q000556:secondary*