title: Mast cell disease: surgical and anesthetic implications.
abstract: Mast cell disease (MCD) is a clonal disorder of the mast cell and its precursor cells. Cardiac surgery in MCD is rarely described. We report an unusual case of a 14-year-old girl who was admitted for atrial septal defect closure and incidentally found to have hepatosplenomegaly with lymphadenopathy who underwent a successful open-heart surgery, after a diagnosis of MCD.
authors.affiliation: Department of Haematology, Christian Medical College, Bangalore, Karnataka, India. drsharat_damodar@yahoo.co.in
authors.forename: Sharat
authors.initials: S
authors.lastname: Damodar
authors.forename: Colin Noel
authors.initials: CN
authors.lastname: John
authors.forename: Gayathri
authors.initials: G
authors.lastname: Gopalakrishnan
authors.forename: Sheila
authors.initials: S
authors.lastname: Nair
authors.forename: Rekha
authors.initials: R
authors.lastname: Samuel
authors.forename: Mathew
authors.initials: M
authors.lastname: Thomas
authors.forename: Devi Prasad
authors.initials: DP
authors.lastname: Shetty
mesh_terms: D000293:Adolescent; D000758:Anesthesia / Q000379:methods*; D001853:Bone Marrow / Q000473:pathology; D005260:Female; D006344:Heart Septal Defects, Atrial / Q000150:complications / Q000601:surgery; D006529:Hepatomegaly / Q000209:etiology; D006801:Humans; D008206:Lymphatic Diseases / Q000209:etiology; D034721:Mastocytosis, Systemic / Q000150:complications / Q000175:diagnosis* / Q000473:pathology; D013163:Splenomegaly / Q000209:etiology / Q000473:pathology