[Pathomorphology of the mixed form of mycoviscidosis in an adult patient].
The paper describes one case of the mixed form of mucoviscidosis, with involvement of the lung (chronic obstructive bronchitis, bronchiectasis, emphysema, pneumosclerosis), liver (cirrhosis), pancreas (lipomatosis with islet atrophy), ileum (enteritis). There were the following complications: cor pulmonale, esophageal varicose veins, ascitis, splenomegaly, secondary diffuse renal amyloidosis of the kidney, adrenals, and spleen, and brain edema. Due to modern therapy the patient reached the age of 25 years, which is a rarity.
Iunosova
Iu R
IuR
Plokhova
V A
VA
Sukhachev
P A
PA
Smetanikov
V M
VM
D000328:Adult; D003550:Cystic Fibrosis / Q000150:complications / Q000473:pathology*; D017809:Fatal Outcome; D006801:Humans; D007410:Intestinal Diseases / Q000150:complications / Q000473:pathology; D008107:Liver Diseases / Q000150:complications / Q000473:pathology; D008171:Lung Diseases / Q000150:complications / Q000473:pathology*; D008297:Male; D010182:Pancreatic Diseases / Q000150:complications / Q000473:pathology