Neonatal epithelioid sarcoma: a distinct clinical entity?
Epithelioid sarcoma is a rare soft tissue sarcoma with a propensity for local aggressiveness, regional nodal spread, and pulmonary metastases. We report a case of epithelioid sarcoma in a neonate with bilateral optic nerve hypoplasia who developed liver, kidney, and bone metastases. The unusual presenting features and pattern of disease progression in this patient suggest that a different disease evaluation strategy should be considered for infants with epithelioid sarcoma.
Gupta
Himesh
H
Department of Surgery, St Jude Children's Research Hospital, Memphis, TN 38105-2794, USA.
Davidoff
Andrew M
AM
Rao
Bhaskar N
BN
Jenkins
Jesse J
JJ
Spunt
Sheri L
SL
D005542:Forearm; D006801:Humans; D007231:Infant, Newborn; D007680:Kidney Neoplasms / Q000175:diagnosis / Q000556:secondary* / Q000601:surgery; D008113:Liver Neoplasms / Q000175:diagnosis / Q000556:secondary* / Q000601:surgery; D009362:Neoplasm Metastasis; D009364:Neoplasm Recurrence, Local; D012509:Sarcoma / Q000175:diagnosis / Q000556:secondary* / Q000601:surgery; D012983:Soft Tissue Neoplasms / Q000175:diagnosis / Q000473:pathology* / Q000601:surgery; D013848:Thigh