Diffuse supravalvular aortic stenosis: comprehensive imaging with ECG-gated CT angiography.
Congenital supravalvular aortic stenosis (SVAS) is a rare cause of congenital left ventricular outflow obstruction and pressure overload, with a diffuse form that often extends into the aortic arch, and can be associated with stenoses in other vascular territories. Knowledge of the extent of disease involvement can be complementary to medical management or critically important prior to surgical intervention. We report a case of diffuse SVAS and demonstrate the utility of ECG-gated multidetector computed tomography (CT) as a comprehensive diagnostic tool in evaluating such patients.
Liu
Peter S
PS
Department of Radiology, University of Pennsylvania School of Medicine, 3400 Spruce Street, Philadelphia, PA 19104, USA.
St John Sutton
Martin G
MG
Litt
Harold I
HI
D000328:Adult; D021921:Aortic Stenosis, Supravalvular / Q000175:diagnosis / Q000000981:diagnostic imaging*; D001027:Aortography / Q000379:methods; D017023:Coronary Angiography / Q000379:methods*; D004562:Electrocardiography; D006801:Humans; D008297:Male; D012720:Severity of Illness Index; D014057:Tomography, X-Ray Computed / Q000379:methods*