Successful revision of portoenterostomy in an infant with biliary atresia.
We present a case report of a boy with biliary atresia who, after hepatoportoenterostomy performed on day 21 of life, had immediate resolution of cholestasis and remained anicteric until 3.5 months of age. He then abruptly developed acholic stools. Nuclear medicine imaging study showed no excretion. Broad-spectrum antibiotics and corticosteroids were administered but did not lead to clinical improvement; a surgical revision of the original anastomosis was undertaken at 4 months of age. At 14 months of age, the child is anicteric and growing well. In this case, successful revision of hepatoportoenterostomy averted the need for liver transplantation.
Haber
Barbara A
BA
Division of Gastroenterology and Nutrition, The Children's Hospital of Philadelphia, Philadelphia, PA 19104, USA. haber@email.chop.edu
Erlichman
Jessi
J
Thayu
Meena
M
Flake
Alan W
AW
Rand
Elizabeth B
EB
D001656:Biliary Atresia / Q000150:complications / Q000601:surgery*; D006801:Humans; D007231:Infant, Newborn; D041781:Jaundice, Obstructive / Q000209:etiology / Q000601:surgery*; D008297:Male; D011171:Portoenterostomy, Hepatic; D012008:Recurrence; D012086:Reoperation