Bimaxillary osteotomy in a female patient with hemophilia A.
We report here a case of a 22-year-old female patient with hemophilia A who had a bimaxillary osteotomy operation. Adequate replacement of Factor VIII and DDAVP(1 deamino-8-D-arginine vasopressin) led to the achievement of hemostasis during and after the surgery. Le Fort I maxillary osteotomy and mandibular sagittal split osteotomies were done to correct the facial profile of this hemophiliac patient with a class III malocclusion and posterior open-bite deformity. Careful preoperative evaluation and close cooperation with the hematologist are required if surgery is to be successful. The operation was uneventful and no postoperative complication was observed.
Güzel
Mehmet Zeki
MZ
Plastic, Reconstructive and Aesthetic Surgery Department, Istanbul University Cerrahpasa Medical Faculty, Istanbul, Turkey. zg@e-kolay.net
Arslan
Hakan
H
Kiliç
Ali
A
D000328:Adult; D003029:Coagulants / Q000627:therapeutic use; D003894:Deamino Arginine Vasopressin / Q000627:therapeutic use; D005169:Factor VIII / Q000627:therapeutic use; D005260:Female; D006467:Hemophilia A / Q000503:physiopathology* / Q000517:prevention & control; D006488:Hemostasis, Surgical; D006490:Hemostatics / Q000627:therapeutic use; D006801:Humans; D008313:Malocclusion, Angle Class III / Q000601:surgery; D008334:Mandible / Q000601:surgery*; D008437:Maxilla / Q000601:surgery*; D024343:Open Bite / Q000601:surgery; D010027:Osteotomy / Q000379:methods*; D019340:Osteotomy, Le Fort; D010347:Patient Care Planning
D003029:Coagulants; D006490:Hemostatics; D005169:Factor VIII; D003894:Deamino Arginine Vasopressin