Pulmonary hypertension in a patient with adult-onset Stills disease.
Pulmonary manifestations of adult-onset Still's disease (AOSD) include aseptic pneumonitis, pleural effusions, rarely acute respiratory distress syndrome, and restrictive lung disease. Pulmonary arterial hypertension (PAH) occurs with several rheumatologic diseases, however, has only been reported once in AOSD. We describe a 29-year-old woman with a 9-year history of AOSD, who developed PAH without any other obvious cause. Therefore, we conclude that this is likely a result of pulmonary vascular changes related to AOSD.
Mubashir
Eisha
E
Department of Medicine, Center of Exellence for Arthritis and Rheumatology, Louisiana State University Health Science Center, 1501 Kings Highway, Shreveport, LA 71130, USA. emubas@lsuhsc.edu
Ahmed
M Mubashir
MM
Hayat
Samina
S
Heldmann
Maureen
M
Berney
Seth Mark
SM
D000328:Adult; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D006976:Hypertension, Pulmonary / Q000209:etiology*; D016706:Still's Disease, Adult-Onset / Q000150:complications*