Annular pancreas in identical twin newborns.
Annular pancreas is a rare congenital anomaly occurring in 1 of every 12,000 to 15,000 live births [Nerwich N, Shi E. Neonatal duodenal obstruction: a review of 30 consecutive cases. Pediatr Surg Int 1994;9:47-50]. It may remain asymptomatic throughout life, present in adulthood, or present in infancy as a high intestinal obstruction. Review of the literature demonstrates only 8 cases of familial annular pancreas and no case of twins exhibiting the disease. We will describe a case of identical (monochorionic diamniotic) female twins with neonatal presentation of duodenal obstruction and annular pancreas, and discuss data supportive of a genetic etiology.
Hulvat
Melissa C
MC
Stritch School of Medicine, Loyola University Medical Center, Maywood, IL, USA.
Kumar
Rajiv B
RB
Newman
Barry M
BM
Muraskas
Jonathan K
JK
D004200:Diseases in Twins; D004380:Duodenal Obstruction / Q000175:diagnosis / Q000209:etiology* / Q000601:surgery; D005260:Female; D006801:Humans; D007231:Infant, Newborn; D010179:Pancreas / Q000002:abnormalities*; D010182:Pancreatic Diseases / Q000150:complications / Q000151:congenital*