[Pentalogy of Cantrell. A case report].
Ectopia cordis is an extremely rare cardiac anomaly. The heart is localized partially or totally outside the thorax cavity. This anomaly occurs as an isolated defect or combined with others midline defects. Cantrell and colleagues described, in 1958, a syndrome including defects of the abdominal wall, sternum, diaphragm, pericardium and heart. There are few successful surgical cases with this pentalogy. We describe a case with this Cantrell's pentalogy. The cardiac malformation was a univentricular heart with pulmonary stenosis. The patient underwent successful surgical palliation with a systemic-to-pulmonary anastomosis and uneventful recovering.
Hernández-González
Martha
M
Servicio de Cardiopatías Congénitas, Hospital de Cardiología Centro Médico Nacional Siglo XXI, IMSS, Cuauhtémoc, 06725, México. martha_hdz@hotmail.com
Jiménez-Arteaga
Santiago
S
Ortega
Francisco
F
Solorio
Sergio
S
Martínez-Flores
Enrique
E
David-Gómez
Felipe
F
Sánchez-Soberanis
Agustín
A
Ortegón-Cerdeña
José
J
López-Gallegos
Diana
D
Argüero-Sánchez
Rubén
R
Alva
Carlos
C
D034861:Abdominal Wall / Q000002:abnormalities*; D000015:Abnormalities, Multiple / Q000175:diagnosis / Q000601:surgery; D002648:Child; D003964:Diaphragm / Q000002:abnormalities*; D006330:Heart Defects, Congenital / Q000175:diagnosis / Q000601:surgery; D006801:Humans; D008297:Male; D010496:Pericardium / Q000002:abnormalities*; D013249:Sternum / Q000002:abnormalities*; D013577:Syndrome