Childhood oral mucous membrane pemphigoid presenting as desquamative gingivitis in a 4-year-old girl.
Mucous membrane pemphigoid is a chronic inflammatory, bullous subepithelial auto-immune disease, with predominant involvement of the mucosal surfaces. Oral mucous membrane pemphigoid occurring in childhood is extremely rare. We describe a new case of this entity occurring in a 4-year-old girl who presented with desquamative gingivitis. Diagnosis was based on clinical presentation, histopathology, immunofluorescence and immunoblotting examinations. Treatment and 2-year follow-up are described.
Lourenço
Silvia V
SV
Department of Dermatology, Hospital das Clinicas, University of São Paulo School of Medicine, Brazil.
Boggio
Paula
P
Agner Machado Martins
Luis E
LE
Santi
Cláudia G
CG
Aoki
Valeria
V
Menta Simonsen Nico
Marcello
M
D002675:Child, Preschool; D005260:Female; D005882:Gingival Diseases / Q000175:diagnosis / Q000473:pathology*; D005891:Gingivitis / Q000473:pathology; D006801:Humans; D009061:Mouth Mucosa / Q000473:pathology; D010390:Pemphigoid, Benign Mucous Membrane / Q000175:diagnosis / Q000473:pathology*