title: Pulmonary hypertension in a patient with adult-onset Stills disease.
abstract: Pulmonary manifestations of adult-onset Still's disease (AOSD) include aseptic pneumonitis, pleural effusions, rarely acute respiratory distress syndrome, and restrictive lung disease. Pulmonary arterial hypertension (PAH) occurs with several rheumatologic diseases, however, has only been reported once in AOSD. We describe a 29-year-old woman with a 9-year history of AOSD, who developed PAH without any other obvious cause. Therefore, we conclude that this is likely a result of pulmonary vascular changes related to AOSD.
authors.affiliation: Department of Medicine, Center of Exellence for Arthritis and Rheumatology, Louisiana State University Health Science Center, 1501 Kings Highway, Shreveport, LA 71130, USA. emubas@lsuhsc.edu
authors.forename: Eisha
authors.initials: E
authors.lastname: Mubashir
authors.forename: M Mubashir
authors.initials: MM
authors.lastname: Ahmed
authors.forename: Samina
authors.initials: S
authors.lastname: Hayat
authors.forename: Maureen
authors.initials: M
authors.lastname: Heldmann
authors.forename: Seth Mark
authors.initials: SM
authors.lastname: Berney
mesh_terms: D000328:Adult; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D006976:Hypertension, Pulmonary / Q000209:etiology*; D016706:Still's Disease, Adult-Onset / Q000150:complications*