title: [Pentalogy of Cantrell. A case report].
abstract: Ectopia cordis is an extremely rare cardiac anomaly. The heart is localized partially or totally outside the thorax cavity. This anomaly occurs as an isolated defect or combined with others midline defects. Cantrell and colleagues described, in 1958, a syndrome including defects of the abdominal wall, sternum, diaphragm, pericardium and heart. There are few successful surgical cases with this pentalogy. We describe a case with this Cantrell's pentalogy. The cardiac malformation was a univentricular heart with pulmonary stenosis. The patient underwent successful surgical palliation with a systemic-to-pulmonary anastomosis and uneventful recovering.
authors.affiliation: Servicio de Cardiopatías Congénitas, Hospital de Cardiología Centro Médico Nacional Siglo XXI, IMSS, Cuauhtémoc, 06725, México. martha_hdz@hotmail.com
authors.forename: Martha
authors.initials: M
authors.lastname: Hernández-González
authors.forename: Santiago
authors.initials: S
authors.lastname: Jiménez-Arteaga
authors.forename: Francisco
authors.initials: F
authors.lastname: Ortega
authors.forename: Sergio
authors.initials: S
authors.lastname: Solorio
authors.forename: Enrique
authors.initials: E
authors.lastname: Martínez-Flores
authors.forename: Felipe
authors.initials: F
authors.lastname: David-Gómez
authors.forename: Agustín
authors.initials: A
authors.lastname: Sánchez-Soberanis
authors.forename: José
authors.initials: J
authors.lastname: Ortegón-Cerdeña
authors.forename: Diana
authors.initials: D
authors.lastname: López-Gallegos
authors.forename: Rubén
authors.initials: R
authors.lastname: Argüero-Sánchez
authors.forename: Carlos
authors.initials: C
authors.lastname: Alva
mesh_terms: D034861:Abdominal Wall / Q000002:abnormalities*; D000015:Abnormalities, Multiple / Q000175:diagnosis / Q000601:surgery; D002648:Child; D003964:Diaphragm / Q000002:abnormalities*; D006330:Heart Defects, Congenital / Q000175:diagnosis / Q000601:surgery; D006801:Humans; D008297:Male; D010496:Pericardium / Q000002:abnormalities*; D013249:Sternum / Q000002:abnormalities*; D013577:Syndrome