Complex pulmonary atresia in a neonate: successful surgical palliation for right pulmonary artery arising from the right main coronary artery.
We describe the case of a 3-week-old infant who was diagnosed with pulmonary atresia, a ventricular septal defect, and discontinuous pulmonary arteries. The pulmonary artery anatomy was delineated by angiography: the right pulmonary artery arose from the proximal right coronary artery, and the left pulmonary artery arose from a left ductus arteriosus. This case illustrates the importance of careful delineation of the anatomy in complex pulmonary atresia before surgical intervention.
Eble
Brian K
BK
Division of Pediatric Cardiology, Baylor College of Medicine, Texas Children's Hospital, MC 19345C, 6621 Fannin Street, Houston, Texas 77030, USA. eblebriank@uams.edu
Fraser
Charles D
CD
Nihill
Michael R
MR
Grifka
Ronald G
RG
Chang
Anthony C
AC
D000015:Abnormalities, Multiple / Q000601:surgery; D006348:Cardiac Surgical Procedures; D017023:Coronary Angiography; D003330:Coronary Vessel Anomalies / Q000601:surgery; D005260:Female; D006345:Heart Septal Defects, Ventricular / Q000453:epidemiology; D006801:Humans; D007231:Infant, Newborn; D011651:Pulmonary Artery / Q000002:abnormalities* / Q000601:surgery; D018633:Pulmonary Atresia / Q000209:etiology* / Q000601:surgery*