title: Childhood oral mucous membrane pemphigoid presenting as desquamative gingivitis in a 4-year-old girl.
abstract: Mucous membrane pemphigoid is a chronic inflammatory, bullous subepithelial auto-immune disease, with predominant involvement of the mucosal surfaces. Oral mucous membrane pemphigoid occurring in childhood is extremely rare. We describe a new case of this entity occurring in a 4-year-old girl who presented with desquamative gingivitis. Diagnosis was based on clinical presentation, histopathology, immunofluorescence and immunoblotting examinations. Treatment and 2-year follow-up are described.
authors.affiliation: Department of Dermatology, Hospital das Clinicas, University of São Paulo School of Medicine, Brazil.
authors.forename: Silvia V
authors.initials: SV
authors.lastname: Lourenço
authors.forename: Paula
authors.initials: P
authors.lastname: Boggio
authors.forename: Luis E
authors.initials: LE
authors.lastname: Agner Machado Martins
authors.forename: Cláudia G
authors.initials: CG
authors.lastname: Santi
authors.forename: Valeria
authors.initials: V
authors.lastname: Aoki
authors.forename: Marcello
authors.initials: M
authors.lastname: Menta Simonsen Nico
mesh_terms: D002675:Child, Preschool; D005260:Female; D005882:Gingival Diseases / Q000175:diagnosis / Q000473:pathology*; D005891:Gingivitis / Q000473:pathology; D006801:Humans; D009061:Mouth Mucosa / Q000473:pathology; D010390:Pemphigoid, Benign Mucous Membrane / Q000175:diagnosis / Q000473:pathology*