Anesthesia for sickle cell disease and congenital myopathy in combination.
We report on the perioperative management of anesthesia and analgesia in a child with sickle cell disease and a congenital myopathy, presenting for corrective orthopedic surgery. The case illustrates two valuable points of interest: the many benefits of regional anesthesia in complex medical cases and the successful use of tourniquets in children with sickle cell disease.
Fanning
Rebecca
R
Children's University Hospital, Temple Street, Dublin, Ireland. rfanning@gofree.indigo.ie
O'Donnell
Brian
B
Lynch
Brian
B
Stephens
Michael
M
O'Donovan
Frances
F
D000755:Anemia, Sickle Cell / Q000150:complications*; D000765:Anesthesia, Conduction / Q000379:methods*; D000768:Anesthesia, General / Q000009:adverse effects; D001176:Arthrogryposis / Q000150:complications / Q000601:surgery*; D002675:Child, Preschool; D002944:Circumcision, Male; D003025:Clubfoot / Q000150:complications / Q000601:surgery*; D005078:Exchange Transfusion, Whole Blood; D006801:Humans; D008297:Male; D020511:Neuromuscular Junction Diseases / Q000150:complications* / Q000151:congenital; D019637:Orthopedic Procedures; D019990:Perioperative Care; D014111:Tourniquets