title: Anesthesia for sickle cell disease and congenital myopathy in combination.
abstract: We report on the perioperative management of anesthesia and analgesia in a child with sickle cell disease and a congenital myopathy, presenting for corrective orthopedic surgery. The case illustrates two valuable points of interest: the many benefits of regional anesthesia in complex medical cases and the successful use of tourniquets in children with sickle cell disease.
authors.affiliation: Children's University Hospital, Temple Street, Dublin, Ireland. rfanning@gofree.indigo.ie
authors.forename: Rebecca
authors.initials: R
authors.lastname: Fanning
authors.forename: Brian
authors.initials: B
authors.lastname: O'Donnell
authors.forename: Brian
authors.initials: B
authors.lastname: Lynch
authors.forename: Michael
authors.initials: M
authors.lastname: Stephens
authors.forename: Frances
authors.initials: F
authors.lastname: O'Donovan
mesh_terms: D000755:Anemia, Sickle Cell / Q000150:complications*; D000765:Anesthesia, Conduction / Q000379:methods*; D000768:Anesthesia, General / Q000009:adverse effects; D001176:Arthrogryposis / Q000150:complications / Q000601:surgery*; D002675:Child, Preschool; D002944:Circumcision, Male; D003025:Clubfoot / Q000150:complications / Q000601:surgery*; D005078:Exchange Transfusion, Whole Blood; D006801:Humans; D008297:Male; D020511:Neuromuscular Junction Diseases / Q000150:complications* / Q000151:congenital; D019637:Orthopedic Procedures; D019990:Perioperative Care; D014111:Tourniquets