Bannayan-riley-ruvalcaba syndrome from the point of view of the pediatric surgeon.
Bannayan-Riley-Ruvalcaba syndrome (BRRS) is an overgrowth syndrome and polyposis condition, which carries an increased risk for development of benign and malignant tumors of various tissues and organs. A 9-year-old boy with BRRS who had multiple subcutaneous mesenchymal tumors and follicular adenoma of the thyroid and a 14-year-old boy with multiple subcutaneous mesenchymal tumors and gastrointestinal polyposis are presented, with special emphasis on the surgical management of these patients.
Ekinci
S
S
Department of Pediatric Surgery, Hacettepe University Faculty of Medicine, Ankara, Turkey.
Karnak
I
I
Balci
S
S
Tanyel
F C
FC
Büyükpamukçu
N
N
D000293:Adolescent; D002648:Child; D005145:Face / Q000002:abnormalities*; D006801:Humans; D008607:Intellectual Disability; D008297:Male; D009378:Neoplasms, Multiple Primary / Q000601:surgery*; D012983:Soft Tissue Neoplasms / Q000601:surgery*; D013577:Syndrome