Extra-axial chordoma.
A chordoma which occurs as a primary tumour outside the axial skeleton is known as an extra-axial chordoma, parachordoma or chordoma periphericum. It is extremely rare and therefore survival, recurrence and the rates of metastasis are not known. Whilst few recurrences have been described, the extra-axial chordoma has the potential for late recurrence at up to 12 years. Metastases are even less frequent. We report the case of a 56-year-old woman who developed an extra-axial chordoma of the right thoracic wall in close relationship with the tenth rib. The tumour was completely removed and the prognosis is excellent.
van Akkooi
A C J
AC
Department of Surgical Oncology, Erasmus University Medical Center, Postbus 2040, 3000 CA, Rotterdam, The Netherlands.
van Geel
A N
AN
Bessems
J H J M
JH
den Bakker
M A
MA
D002817:Chordoma / Q000473:pathology* / Q000601:surgery; D005260:Female; D006801:Humans; D008875:Middle Aged; D013899:Thoracic Neoplasms / Q000473:pathology* / Q000601:surgery; D035441:Thoracic Wall / Q000473:pathology / Q000601:surgery; D016896:Treatment Outcome