title: Extra-axial chordoma.
abstract: A chordoma which occurs as a primary tumour outside the axial skeleton is known as an extra-axial chordoma, parachordoma or chordoma periphericum. It is extremely rare and therefore survival, recurrence and the rates of metastasis are not known. Whilst few recurrences have been described, the extra-axial chordoma has the potential for late recurrence at up to 12 years. Metastases are even less frequent. We report the case of a 56-year-old woman who developed an extra-axial chordoma of the right thoracic wall in close relationship with the tenth rib. The tumour was completely removed and the prognosis is excellent.
authors.affiliation: Department of Surgical Oncology, Erasmus University Medical Center, Postbus 2040, 3000 CA, Rotterdam, The Netherlands.
authors.forename: A C J
authors.initials: AC
authors.lastname: van Akkooi
authors.forename: A N
authors.initials: AN
authors.lastname: van Geel
authors.forename: J H J M
authors.initials: JH
authors.lastname: Bessems
authors.forename: M A
authors.initials: MA
authors.lastname: den Bakker
mesh_terms: D002817:Chordoma / Q000473:pathology* / Q000601:surgery; D005260:Female; D006801:Humans; D008875:Middle Aged; D013899:Thoracic Neoplasms / Q000473:pathology* / Q000601:surgery; D035441:Thoracic Wall / Q000473:pathology / Q000601:surgery; D016896:Treatment Outcome