Optic pathway glioma associated with orbital rhabdomyosarcoma and bilateral optic nerve sheath dural ectasia in a child with neurofibromatosis-1.
Neurofibromatosis-1 (NF-1) is a multisystem disorder presenting with a variety of clinical and imaging manifestations. Neural and non-neural tumours, and unusual benign miscellaneous conditions, separately or combined, are encountered in variable locations. We present a 2(1/2)-year-old boy with NF-1 who demonstrated coexisting optic pathway glioma with involvement of the chiasm and optic nerve, orbital alveolar rhabdomyosarcoma and bilateral optic nerve sheath dural ectasia.
Nikas
Ioannis
I
Imaging Department, Aghia Sophia Children's Hospital, Athens, Greece.
Theofanopoulou
Maria
M
Lampropoulou
Penelope
P
Pourtsidis
Apostolos
A
Hadjigeorgi
Christiana
C
Kosmidis
Helen
H
D002675:Child, Preschool; D004108:Dilatation, Pathologic / Q000000981:diagnostic imaging*; D005910:Glioma / Q000000981:diagnostic imaging*; D006801:Humans; D008297:Male; D009186:Myelin Sheath / Q000473:pathology; D017253:Neurofibromatoses / Q000000981:diagnostic imaging*; D009900:Optic Nerve / Q000473:pathology; D019574:Optic Nerve Neoplasms / Q000000981:diagnostic imaging*; D009918:Orbital Neoplasms / Q000000981:diagnostic imaging*; D012208:Rhabdomyosarcoma / Q000000981:diagnostic imaging*; D014057:Tomography, X-Ray Computed