Osteoglophonic dysplasia: dental and orthodontic implications.
OBJECTIVE
Documentation of dental and orthodontic implications of osteoglophonic dysplasia (OGD).


METHODS
Case report describing oral and dental manifestations of a female with OGD, aged 39 years, who was first documented three decades ago.


RESULTS
This rare genetic disorder manifests with gross stunting of stature, associated with severe craniofacial malformation and multiple unerupted teeth. Radiographically, multiple lucent lesions were present in the tubular bones and mandible as well as several impacted teeth.


CONCLUSIONS
We concluded that prosthetic dental replacement in this patient would be difficult because of the distorted jaw relationship and large alveolar ridges. Equally, craniofacial reconstruction might be compromised by obstruction of the nasal airways, difficulty in intubation and postoperative respiratory problems.
Roberts
T S
TS
Faculty of Dentistry, University of the Western Cape, Cape Town, South Africa. troberts@uwc.ac.za
Stephen
L
L
Beighton
P
P
D000328:Adult; D001848:Bone Diseases, Developmental / Q000235:genetics*; D019465:Craniofacial Abnormalities / Q000235:genetics*; D004392:Dwarfism / Q000235:genetics*; D005260:Female; D006801:Humans; D009065:Mouth Rehabilitation; D009971:Orthodontics, Corrective; D014095:Tooth, Impacted / Q000235:genetics; D014097:Tooth, Unerupted / Q000235:genetics