title: Hallerborden Spatz disease.
abstract: Hallervorden Spatz disease is a rare disorder characterized by progressive extrapyramidal dysfunction. We report a case of a 18 year old boy who presented with cervical dystonia, pigmentary retinal degeneration and MRI brain showing the "eye-of-the-tiger" appearance. Renamed recently as "Neurodegeneration with brain iron accumulation", we present this case for its rarity and interesting features.
authors.affiliation: Govt General Hospital, Chennai.
authors.forename: V
authors.initials: V
authors.lastname: Raji
authors.forename: S E
authors.initials: SE
authors.lastname: Dhanasegaran
authors.lastname: Usha
authors.forename: K
authors.initials: K
authors.lastname: Subramanian
authors.lastname: Suresh
authors.forename: S
authors.initials: S
authors.lastname: Kumar
mesh_terms: D000293:Adolescent; D006801:Humans; D018810:Magnetic Resonance Angiography; D008279:Magnetic Resonance Imaging; D008297:Male; D006211:Pantothenate Kinase-Associated Neurodegeneration / Q000175:diagnosis* / Q000503:physiopathology