title: Mycosis fungoides/Sézary syndrome: report of an unusual case.
abstract: BACKGROUND
  Sézary syndrome (SS) is an uncommon form of cutaneous T cell lymphoma (CTCL) with a classical triad of lymphadenopathy, characteristic circulating lymphoma cells (Sézary cells) and erythrodermatous skin involvement with classical mycosis fungoides (MF)-like histological picture.
  
  
  METHODS
  A 32-year-old woman presented with this classical triad; however, her skin involvement, histologically, was in the form of folliculotropic MF, rather than the usual classical form of MF.
  
  
  CONCLUSIONS
  In the vast majority of cases, the cutaneous involvement in SS resembles conventional MF, histologically. One case of CD30-positive CTCL with pilotropic MF has been reported. However, English literature does not describe any case of SS with folliculotropic MF with typical immunophenotype of SS thus far. We presume that this case represents the first report of SS with folliculotropic MF histologically, displaying the typical CD30-negative immunophenotype.
authors.affiliation: Department of Pathology, Armed Forces Medical College, Pune, Maharastra, India.
authors.forename: Anurag
authors.initials: A
authors.lastname: Mehta
authors.forename: Bal Makunda
authors.initials: BM
authors.lastname: Dhungel
authors.forename: Mohd Fawad Farooq
authors.initials: MF
authors.lastname: Khan
mesh_terms: D000328:Adult; D005260:Female; D006801:Humans; D016130:Immunophenotyping; D017730:Ki-1 Antigen / Q000276:immunology; D009182:Mycosis Fungoides / Q000276:immunology / Q000473:pathology*; D012751:Sezary Syndrome / Q000276:immunology / Q000473:pathology*; D012878:Skin Neoplasms / Q000276:immunology / Q000473:pathology*
chemical_list: D017730:Ki-1 Antigen