[Gastric adenocarcinoma in Zinsser-Cole-Engman syndrome].
Zinsser-Cole-Engman syndrome is a congenital dyskeratosis that produces cutaneus and hematologic alterations and, in 5% of patients, gastrointestinal neoplasms. We report the case of a 37-year-old man with this syndrome who was diagnosed with gastric adenocarcinoma. This case provides an example of the management that should be followed with these patients in order to identify neoplasms at stages in which treatment is curative.
Bruna Esteban
Marcos
M
Servicio de Cirugía General y Aparato Digestivo, Consorcio Hospital General Universitario de Valencia, Valencia, España. drbruna@comv.es
Montalvá Orón
Eva
E
López Delgado
Alberto
A
Galindo Jara
Pablo
P
Vázquez Prado
Antonio
A
Fabra Ramis
Ricardo
R
D000230:Adenocarcinoma / Q000209:etiology*; D000328:Adult; D019871:Dyskeratosis Congenita / Q000150:complications*; D006801:Humans; D008297:Male; D013274:Stomach Neoplasms / Q000209:etiology*