Ciliary body medulloepithelioma: clinical, ultrasound biomicroscopic and histopathologic correlation.
A 3-year-old girl presented with a distorted pupil and decrease of visual acuity. A ciliary body mass at the superior-temporal quadrant could be seen at slit-lamp examination. Ultrasound biomicroscopy revealed a lesion with lobulated surface, arising at the ciliary body, composed of compact and cystic areas. An iridocyclectomy was performed but the tumour recurred after a few months. The eye was then enucleated. Histopathologic evaluation showed sheets and cords of proliferated medullary epithelium. Cystic spaces and Flexner-Wintersteiner rosettes were also seen. Those findings correlated well with ultrasound biomicroscopic images. The knowledge of echographic characteristics can significantly assist in the diagnosis of medulloepithelioma of the ciliary body.
Ayres
Bernadete
B
Instituto Brasileiro de Oftalmologia, Rio de Janeiro, Brazil.
Brasil
Oswaldo M
OM
Klejnberg
Celso
C
Moura
Letícia R
LR
Fernandes
Bruno F
BF
Burnier
Miguel N
MN
D002675:Child, Preschool; D002924:Ciliary Body / Q000000981:diagnostic imaging* / Q000473:pathology* / Q000601:surgery; D005260:Female; D006801:Humans; D007498:Iris / Q000601:surgery; D033401:Microscopy, Acoustic; D018242:Neuroectodermal Tumors, Primitive / Q000000981:diagnostic imaging* / Q000473:pathology*; D013508:Ophthalmologic Surgical Procedures; D014604:Uveal Neoplasms / Q000000981:diagnostic imaging* / Q000473:pathology*; D014792:Visual Acuity