Ascending aortic aneurysm in a fetus due to a benign nodular myofibroblastic lesion.
A fetal echocardiogram at 20 weeks of gestation revealed a large ascending aortic aneurysm in the presence of a normal aortic root and normal intracardiac anatomy. No other abnormalities were noted in the fetus. Upon termination of pregnancy, histopathological examination revealed an isolated benign nodular myofibroblastic lesion of likely hamartomatous origin, a first description of such pathology contributing to the formation of an aneurysm in the ascending aorta.
Ramaswamy
Prema
P
Division of Pediatric Cardiology, Maimonides Medical Center, Brooklyn, NY, USA. Electronic address: pramaswamy@maimonidesmed.org.
Haberman
Shoshana
S
Division of Perinatology, Maimonides Medical Center, Brooklyn, NY, USA.
Kleinman
Charles
C
Division of Pediatric Cardiology, Columbia Presbyterian Medical Center, NY, NY, USA.
Lytrivi
Irene D
ID
Division of Pediatric Cardiology, Maimonides Medical Center, Brooklyn, NY, USA.
Thaker
Harshwardhan M
HM
Department of Pathology, Columbia Presbyterian Medical Center, NY, NY, USA.
D000328:Adult; D001011:Aorta / Q000473:pathology*; D001014:Aortic Aneurysm / Q000151:congenital* / Q000473:pathology; D001018:Aortic Diseases / Q000151:congenital* / Q000473:pathology; D005260:Female; D005333:Fetus; D005355:Fibrosis / Q000150:complications; D006222:Hamartoma / Q000151:congenital* / Q000473:pathology; D006801:Humans; D032389:Myocytes, Smooth Muscle / Q000473:pathology*; D011247:Pregnancy