Fibromuscular dysplasia as the substrate for systemic and pulmonary hypertension in the setting of Moya-Moya disease.
We report the first case, to the best of our knowledge, of a child with the unusual association of Moya-Moya disease and both systemic and pulmonary hypertension. Histological examination revealed fibromuscular dysplasia as the common denominator for a diffuse arteriopathy.
Ou
Phalla
P
Cardiologie Pédiatrique, Hôpital Necker-Enfants Malades, AP-HP, Paris, France. phalla.ou@nck.ap-hop-paris.fr
Dupont
Peggy
P
Bonnet
Damien
D
D000293:Adolescent; D000800:Angioplasty, Balloon / Q000379:methods; D019917:Blood Vessel Prosthesis Implantation / Q000379:methods; D002533:Cerebral Angiography; D005260:Female; D005352:Fibromuscular Dysplasia / Q000150:complications* / Q000175:diagnosis / Q000628:therapy; D006801:Humans; D006976:Hypertension, Pulmonary / Q000000981:diagnostic imaging / Q000209:etiology* / Q000503:physiopathology; D009072:Moyamoya Disease / Q000150:complications* / Q000000981:diagnostic imaging; D011669:Pulmonary Wedge Pressure; D012077:Renal Artery / Q000000981:diagnostic imaging / Q000473:pathology*; D018608:Ultrasonography, Doppler