title: [Lymphocytic interstitial pneumonia in primary Sjögren syndrome].
abstract: Ljmphocytic interstitial pneumonia (LIP) is a rare form of interstitial pneumonia. It can occur as a idiopathic disease however most frequently associated with other diseases, particularly Sjogren syndrome. We present a 58 years old woman, with primary Sjögren syndrome who developed after 7 years interstitial lung disease. LIP was diagnosed on the basis of histological examinations of specimens obtained by open lung biopsy. Diffuse infiltrations composed of small polyclonal lymphocytes, plasma cells with reactive follicules were found. Infiltrates observed in bronchial and bronchiolar walls expanded into interlobular and alveolar septae. Prednisone in a dose of 40 mg per day was introduced and clinical, radiological, spirometric and gasometric improvement was observed. The dose of prednisone was gradually reduced but is still continued.
authors.affiliation: Instytutu Gruźlicy i Chorób Płuc w Warszawie.
authors.forename: Radzikowska
authors.initials: R
authors.lastname: Elzbieta
authors.forename: Wiatr
authors.initials: W
authors.lastname: Elzbieta
authors.forename: Gawryluk
authors.initials: G
authors.lastname: Dariusz
authors.forename: Renata
authors.initials: R
authors.lastname: Langfort
authors.forename: Jakub
authors.initials: J
authors.lastname: Ptak
mesh_terms: D003095:Collagen Diseases / Q000150:complications / Q000175:diagnosis* / Q000628:therapy; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D017563:Lung Diseases, Interstitial / Q000150:complications / Q000175:diagnosis* / Q000628:therapy; D008232:Lymphoproliferative Disorders / Q000150:complications / Q000175:diagnosis* / Q000473:pathology; D008875:Middle Aged; D012859:Sjogren's Syndrome / Q000150:complications / Q000175:diagnosis* / Q000628:therapy; D016896:Treatment Outcome; D014397:Tuberculosis, Pulmonary / Q000150:complications / Q000175:diagnosis* / Q000628:therapy