Posterior correction and fusion for severe cervical kyphosis in a patient with myotonic dystrophy: a case report.
METHODS
A case report.


OBJECTIVE
To report the first myotonic dystrophy case in which cervical kyphosis had been surgically corrected.


BACKGROUND
Myotonic dystrophy is an autosomal dominant disease that shows myotonia, progressive muscle atrophy, and other various symptoms. Instability of the neck is expected to cause disorders of the cervical spine; however, there are no detailed reports on deformity of cervical spine associated with this disease.


METHODS
A 43-year-old man with cervical kyphosis due to myotonic dystrophy had undergone an occiput-T2 fusion with autogenous iliac bone using spinal instrumentation.


RESULTS
The activity of daily life of the patient had improved markedly, and the good results continued to be preserved for 5 years. There were not any major perioperative complications.


CONCLUSIONS
Surgical correction of cervical spine is not necessarily a contraindication for myotonic dystrophy.
Yuzawa
Yohei
Y
Department of Orthopaedic Surgery Aizawa Hospital, Matsumoto, Japan. yuzawa@ai-hosp.or.jp
Hashimoto
Takao
T
Takahashi
Jun
J
Nakamura
Isao
I
Hirabayashi
Hiroki
H
Ebara
Sohei
S
D000328:Adult; D001269:Atlanto-Occipital Joint / Q000473:pathology / Q000601:surgery*; D002574:Cervical Vertebrae / Q000473:pathology / Q000601:surgery*; D006801:Humans; D007738:Kyphosis / Q000209:etiology / Q000473:pathology / Q000601:surgery*; D008297:Male; D009223:Myotonic Dystrophy / Q000150:complications / Q000473:pathology / Q000601:surgery*; D009777:Occipital Bone / Q000473:pathology / Q000601:surgery*; D013123:Spinal Fusion / Q000295:instrumentation / Q000379:methods*; D016896:Treatment Outcome