Anesthesia management for the child with Sanjad-Sakati syndrome.
Sanjad-Sakati syndrome (SSS) is a rare genetic disorder characterized by congenital hypoparathyroidism, hypocalcemia and hyperphosphatemia, seizures, severe intrauterine and postnatal growth failure, dwarfism, mental retardation, dysmorphic features including retromicrognathia and abnormal dentition and increased susceptibility to infection. It is mainly confined to children in the Middle-East countries. We report the anesthesia management of a 12-year-old boy with SSS for dental treatment, and discuss the anesthesia implications of this disorder.
Platis
Cari M
CM
Department of Anesthesia, Schneider Children's Medical Center of Israel, Tel Aviv, Israel. carip@clalit.org.il
Wasersprung
David
D
Kachko
Ludmyla
L
Tsunzer
Igor
I
Katz
Jacob
J
D000015:Abnormalities, Multiple; D000766:Anesthesia, Dental / Q000379:methods*; D018685:Anesthetics, Inhalation; D018686:Anesthetics, Intravenous; D000779:Anesthetics, Local; D002648:Child; D004392:Dwarfism; D006801:Humans; D007011:Hypoparathyroidism / Q000151:congenital*; D008607:Intellectual Disability; D008012:Lidocaine; D008297:Male; D008738:Methyl Ethers; D009609:Nitrous Oxide; D015742:Propofol; D000077149:Sevoflurane; D013577:Syndrome
D018685:Anesthetics, Inhalation; D018686:Anesthetics, Intravenous; D000779:Anesthetics, Local; D008738:Methyl Ethers; D000077149:Sevoflurane; D008012:Lidocaine; D009609:Nitrous Oxide; D015742:Propofol