title: Pregnancy with uterine vascular malformations associated with hemorrhagic hereditary telangiectasia: a case report.
abstract: BACKGROUND
  Hereditary hemorrhagic telangiectasia (HHT) is a rare autosomal dominant condition. It is rarely seen in pregnancy and even more rarely has uterine manifestations.
  
  
  METHODS
  A 29-year-old primigravid woman with HHT was noted to have vascular manifestations of her disease in the lower uterus, distal rectum, pelvis, and bladder before pregnancy. Prior to delivery, a case conference was held, involving representatives of the departments of vascular surgery, hematology, radiology, anaesthesiology, maternal-fetal medicine, neonatology, and laboratory medicine, and other appropriate health professionals. A successful elective Caesarean section was performed at term, with a good outcome for both mother and child.
  
  
  CONCLUSIONS
  regnancies in women with HHT and associated uterine vascular manifestations have been rarely reported, and published information is minimal. We present a case of a successful operative delivery following careful multidisciplinary antepartum care.
authors.affiliation: Department of Obstetrics and Gynaecology, University of British Columbia, Children's and Women's Hospital of British Columbia, Vancouver BC.
authors.forename: Leanne S
authors.initials: LS
authors.lastname: Dahlgren
authors.affiliation: Department of Obstetrics and Gynaecology, University of British Columbia, Children's and Women's Hospital of British Columbia, Vancouver BC.
authors.forename: Sidney B
authors.initials: SB
authors.lastname: Effer
authors.affiliation: Department of Medical Genetics, University of British Columbia, Children's and Women's Hospital of British Columbia, Vancouver BC.
authors.forename: Barbara C
authors.initials: BC
authors.lastname: McGillivray
authors.affiliation: Department of Radiology and Ultrasound, University of British Columbia, Children's and Women's Hospital of British Columbia, Vancouver BC.
authors.forename: Denise J
authors.initials: DJ
authors.lastname: Pugash
mesh_terms: D000328:Adult; D002585:Cesarean Section; D005260:Female; D006801:Humans; D011247:Pregnancy; D011249:Pregnancy Complications, Cardiovascular / Q000235:genetics*; D011256:Pregnancy Outcome; D013683:Telangiectasia, Hereditary Hemorrhagic / Q000150:complications*; D014599:Uterus / Q000098:blood supply*