title: Non-compaction of the right atrium and left ventricle in Ebstein's malformation.
abstract: Ebstein's malformation (EM) is characterized by dysplasia and displacement of the tricuspid inferior and septal leaflets from the true atrioventricular (AV) junction. Left ventricular hypertrabeculation/non-compaction (LVHT) including the 'atrialized' portion in EM has not been described. A 42-year-old man with a history of radiofrequency ablation of a Mahaim-like bundle suffered from chest pain. Coronary angiography was normal, but echocardiography showed a septal tricuspid leaflet inserting 3.5-cm apically beyond the AV junction, deep recesses of the atrialized interventricular septum, and a heavily trabeculated left ventricle; these were confirmed by cardiac magnetic resonance imaging. Neurologically, hypoacusis, positive pyramidal signs, postural tremor and brisk tendon reflexes were identified.
authors.affiliation: Second Medical Department, Krankenanstalt Rudolfstiftung, Vienna, Austria. claudia.stoellberger@chello.at
authors.forename: Claudia
authors.initials: C
authors.lastname: Stöllberger
authors.forename: Wolfgang
authors.initials: W
authors.lastname: Kopsa
authors.forename: Josef
authors.initials: J
authors.lastname: Finsterer
mesh_terms: D000328:Adult; D001283:Atrioventricular Node / Q000473:pathology; D017115:Catheter Ablation; D017023:Coronary Angiography; D004437:Ebstein Anomaly / Q000000981:diagnostic imaging / Q000473:pathology* / Q000601:surgery; D004452:Echocardiography; D006325:Heart Atria / Q000473:pathology*; D006346:Heart Septum / Q000473:pathology; D006352:Heart Ventricles / Q000473:pathology*; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D009206:Myocardium / Q000473:pathology; D011227:Pre-Excitation, Mahaim-Type / Q000151:congenital / Q000601:surgery; D014261:Tricuspid Valve / Q000473:pathology