[Radiologic findings in Gorham-Stout syndrome].
Gorham-Stout syndrome, also called "disappearing bone disease" or idiopathic massive osteolysis, is a rare disease of unknown etiology and pathogenesis. It is characterized by rapidly progressive localized massive osteolysis associated to a proliferation of vascular structures of benign origin in which the absence of new bone formation is representative. We present two cases (a six-year-old boy with affected right ulna, and a 15-year-old girl with right rib affection associated to chylothorax) of this disease with the characteristic clinical, histological, and imaging findings.
Cano
Bernardo
B
Servicio de Radiodiagnóstico de adultos, Hospital La Fe, Valencia, España. cano_bernar@gva.es
Insa
Sonia
S
Cifrián
Carlos
C
Cortina
Héctor
H
Hernández
Miguel
M
D000293:Adolescent; D002648:Child; D005260:Female; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D010015:Osteolysis, Essential / Q000175:diagnosis*; D014057:Tomography, X-Ray Computed