title: Linear scleroderma 'en coup de sabre' associated with cerebral and ocular vasculitis.
abstract: Linear scleroderma 'en coup de sabre' (LSCS) has been reported in association with intracranial abnormalities. We report the case of an 11-year-old boy with LSCS who presented with recurrent headaches. Cranial magnetic resonance imaging (MRI) and angiography were consistent with the diagnosis of a cerebral vasculitis. In addition, retinal examination showed an exudative inflammatory lesion consistent with vasculitis.
authors.affiliation: Children's Hospital, Section of Paediatric Rheumatology, University of Würzburg, Germany.
authors.forename: A
authors.initials: A
authors.lastname: Holl-Wieden
authors.forename: T
authors.initials: T
authors.lastname: Klink
authors.forename: J
authors.initials: J
authors.lastname: Klink
authors.forename: M
authors.initials: M
authors.lastname: Warmuth-Metz
authors.forename: H J
authors.initials: HJ
authors.lastname: Girschick
mesh_terms: D002533:Cerebral Angiography; D002648:Child; D006261:Headache / Q000209:etiology; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D031300:Retinal Vasculitis / Q000150:complications* / Q000175:diagnosis / Q000473:pathology; D012594:Scleroderma, Localized / Q000150:complications* / Q000175:diagnosis / Q000473:pathology; D020293:Vasculitis, Central Nervous System / Q000150:complications* / Q000175:diagnosis / Q000473:pathology