Primary synovial sarcoma.
OBJECTIVE
To describe the clinicopathologic and immunohistochemical features and treatment of a rare case of primary synovial sarcoma of the orbit.


METHODS
Retrospective interventional case report.


METHODS
A 14-year-old young man with histologically proven synovial sarcoma of the orbit. The diagnosis was confirmed by demonstration of a specific chromosomal translocation by polymerase chain reaction studies.


METHODS
The patient was treated with orbital exenteration and followed up for 18 months at regular intervals.


RESULTS
The tumor was excised completely, and the patient has done well during the initial 1-year follow-up with no sign of recurrence.


CONCLUSIONS
We report the fourth case of synovial sarcoma of the orbit and, at 14 years of age, the youngest patient reported.
Hartstein
Morris E
ME
Department of Ophthalmology, Saint Louis University Eye Institute, Saint Louis University School of Medicine, St. Louis, Missouri 63104, USA. mhartstein@earthlink.net
Silver
Frankie-Lynn
FL
Ludwig
Olivia J
OJ
O'Connor
Dennis M
DM
D000293:Adolescent; D006801:Humans; D007150:Immunohistochemistry / Q000379:methods; D008297:Male; D013508:Ophthalmologic Surgical Procedures; D009918:Orbital Neoplasms / Q000175:diagnosis / Q000235:genetics / Q000473:pathology / Q000601:surgery*; D016133:Polymerase Chain Reaction; D012189:Retrospective Studies; D013584:Sarcoma, Synovial / Q000175:diagnosis / Q000235:genetics / Q000473:pathology / Q000601:surgery*; D013194:Staining and Labeling; D014057:Tomography, X-Ray Computed; D014178:Translocation, Genetic