title: [A case of hemophagocytic syndrome with terminal ileal ulcerations].
abstract: Reactive hemophagocytic syndrome or hemophagocytic lymphohistiocytosis, is characterized by the proliferation of benign histiocytes showing phagocytosis of blood cells in hematopoietic organs including bone marrow, spleen, or lymph nodes, accompanied by fever, hepatosplenomegaly, hepatic dysfunction, pancytopenia, and hypertriglyceridemia. The pathogenesis of reactive hemophagocytic syndrome is unknown. It is often associated with infection, malignant neoplasm, autoimmune disease, drugs and various immunodeficiencies. The prognosis of this syndrome is poor and the causes of death are hemorrhage, infection, or multiorgan failure. We experienced a case of hemophagocytic syndrome with terminal ileal ulcers, not associated with other causes. Thus, we report this case with a review of literatures.
authors.affiliation: Department of Internal Medicine, Bundang CHA Hospital, Pochon CHA University, Yatap-dong, Bundang-gu, Seongnam, Korea.
authors.forename: Jae Hyun
authors.initials: JH
authors.lastname: Moon
authors.forename: Sung Pyo
authors.initials: SP
authors.lastname: Hong
authors.forename: Pil Won
authors.initials: PW
authors.lastname: Park
authors.forename: Kwang Hyun
authors.initials: KH
authors.lastname: Ko
authors.forename: Seong Gyu
authors.initials: SG
authors.lastname: Hwang
authors.forename: Kyu Sung
authors.initials: KS
authors.lastname: Rim
authors.forename: Hee Jung
authors.initials: HJ
authors.lastname: An
authors.forename: Myung Seo
authors.initials: MS
authors.lastname: Kang
mesh_terms: D000328:Adult; D017809:Fatal Outcome; D006801:Humans; D007077:Ileal Diseases / Q000150:complications / Q000175:diagnosis*; D051359:Lymphohistiocytosis, Hemophagocytic / Q000150:complications / Q000175:diagnosis* / Q000473:pathology; D008297:Male; D014057:Tomography, X-Ray Computed; D014456:Ulcer / Q000150:complications / Q000175:diagnosis*