[Surgical management of Mondini dysplasia with cerebrospinal fluid leakage].
OBJECTIVE
To investigate the etiology, clinical presentation, surgical treatment and prevention of Mondini dysplasia with cerebrospinal fluid otorrhea.


METHODS
Fifteen cases of Mondini dysplasia were collected from our department during 1998-2004. The clinical presentations, surgical treatment and image characters were analysed. Surgical therapy methods included: checking fenestra vestibuli, fenestra cochlear or other fistula and repairing the fistulas by plugging with fascial tissue via tympanoplastic approach with endaural incision.


RESULTS
Severe sensorineural hearing loss and spontaneous recrudescent meningitis were the characteristics of Mondini dysplasia. The leakage was from fenestra vestibuli, fenestra cochlear or other fragile region nearby. In these cases, ten cases underwent one plugging operation and cured, five cases underwent two or three operation and cured. All these cases had no leakage or meningitis recrudescence after ten months follow up.


CONCLUSIONS
Repairing fistula via tympanoplastic approach is an effective therapeutic method. Avoiding nosogenesis, fitting hearing aid or taking cochlear implantation are important means of prevention and cure.
Li
Weirnin
W
Department of Otolaryngology-Head and Neck Surgery, General Hospital of PLA, Beijing, 100853, China.
Han
Dongyi
D
Yang
Weiyan
W
D000293:Adolescent; D000328:Adult; D002558:Cerebrospinal Fluid Otorrhea / Q000150:complications* / Q000601:surgery*; D002648:Child; D002675:Child, Preschool; D007758:Ear, Inner / Q000002:abnormalities*; D005260:Female; D006319:Hearing Loss, Sensorineural / Q000150:complications / Q000601:surgery; D006801:Humans; D006965:Hyperplasia; D008297:Male; D019651:Plastic Surgery Procedures / Q000379:methods*; D055815:Young Adult