Linear scleroderma 'en coup de sabre' associated with cerebral and ocular vasculitis.
Linear scleroderma 'en coup de sabre' (LSCS) has been reported in association with intracranial abnormalities. We report the case of an 11-year-old boy with LSCS who presented with recurrent headaches. Cranial magnetic resonance imaging (MRI) and angiography were consistent with the diagnosis of a cerebral vasculitis. In addition, retinal examination showed an exudative inflammatory lesion consistent with vasculitis.
Holl-Wieden
A
A
Children's Hospital, Section of Paediatric Rheumatology, University of Würzburg, Germany.
Klink
T
T
Klink
J
J
Warmuth-Metz
M
M
Girschick
H J
HJ
D002533:Cerebral Angiography; D002648:Child; D006261:Headache / Q000209:etiology; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D031300:Retinal Vasculitis / Q000150:complications* / Q000175:diagnosis / Q000473:pathology; D012594:Scleroderma, Localized / Q000150:complications* / Q000175:diagnosis / Q000473:pathology; D020293:Vasculitis, Central Nervous System / Q000150:complications* / Q000175:diagnosis / Q000473:pathology