[Non-compact left ventricular myocardium: current state of the problem].
Non-compaction of the left ventricle or spongy myocardium is a rare congenital cardiomyopathy which is characterized by impaired endomyocardial morphogenesis, hypertrophy of left ventricular myocardium with prominent trabeculation, and deep inter-trabecular recesses. According to WHO classification (1995) this disease belongs to unclassified cardiomyopathies. Main clinical signs of ventricular non-compaction are heart failure, ventricular arrhythmias, systemic and pulmonary embolism. Echocardiography which is a basic method of diagnosis can reveal double layer structure of thickened left ventricular wall and multiple prominent trabeculation with wide inter-trabecular spaces. Predominant localizations of pathological process are region of cardiac apex, inferior and lateral left ventricular walls. Treatment of patients with ventricular non-compaction concentrates on elimination of its main clinical symptoms.
Domnitskaia
T M
TM
Sidorenko
B A
BA
Erokhina
M G
MG
Saidova
M A
MA
D009202:Cardiomyopathies / Q000150:complications / Q000151:congenital / Q000175:diagnosis; D003937:Diagnosis, Differential; D004452:Echocardiography; D006352:Heart Ventricles / Q000000981:diagnostic imaging / Q000473:pathology*; D006801:Humans; D017379:Hypertrophy, Left Ventricular / Q000150:complications / Q000151:congenital / Q000175:diagnosis; D009206:Myocardium / Q000473:pathology