[A case of hemophagocytic syndrome with terminal ileal ulcerations].
Reactive hemophagocytic syndrome or hemophagocytic lymphohistiocytosis, is characterized by the proliferation of benign histiocytes showing phagocytosis of blood cells in hematopoietic organs including bone marrow, spleen, or lymph nodes, accompanied by fever, hepatosplenomegaly, hepatic dysfunction, pancytopenia, and hypertriglyceridemia. The pathogenesis of reactive hemophagocytic syndrome is unknown. It is often associated with infection, malignant neoplasm, autoimmune disease, drugs and various immunodeficiencies. The prognosis of this syndrome is poor and the causes of death are hemorrhage, infection, or multiorgan failure. We experienced a case of hemophagocytic syndrome with terminal ileal ulcers, not associated with other causes. Thus, we report this case with a review of literatures.
Moon
Jae Hyun
JH
Department of Internal Medicine, Bundang CHA Hospital, Pochon CHA University, Yatap-dong, Bundang-gu, Seongnam, Korea.
Hong
Sung Pyo
SP
Park
Pil Won
PW
Ko
Kwang Hyun
KH
Hwang
Seong Gyu
SG
Rim
Kyu Sung
KS
An
Hee Jung
HJ
Kang
Myung Seo
MS
D000328:Adult; D017809:Fatal Outcome; D006801:Humans; D007077:Ileal Diseases / Q000150:complications / Q000175:diagnosis*; D051359:Lymphohistiocytosis, Hemophagocytic / Q000150:complications / Q000175:diagnosis* / Q000473:pathology; D008297:Male; D014057:Tomography, X-Ray Computed; D014456:Ulcer / Q000150:complications / Q000175:diagnosis*