Dubin-Johnson syndrome with systemic lupus erythematosus: a case report.
BACKGROUND
Dubin-Johnson syndrome (DJS) is a rare clinical entity. We describe a case of DJS complicated by systemic lupus erythematosus (SLE).


METHODS
A case of congenital hyperbilirubinemia with SLE was evaluated systematically including review of history, physical examination for the stigmata of chronic liver disease, and other investigations.


RESULTS
Liver biopsy revealed a black liver with preserved architecture suggestive of DJS.


CONCLUSIONS
SLE may develop in DJS. The relationship between DJS and SLE in this case is most likely a chance occurrence.
Mahtab
Mamun-Al
MA
Department of Hepatology, Bangabandhu Sheikh Mujib Medical University, Dhaka, Bangladesh. shwapnil@agni.com
Karim
Md Fazal
MF
Rahman
Salimur
S
Adnan
Abul Barkat Muhammad
AB
D000293:Adolescent; D005260:Female; D006801:Humans; D007566:Jaundice, Chronic Idiopathic / Q000150:complications* / Q000175:diagnosis / Q000473:pathology; D008099:Liver / Q000473:pathology; D008180:Lupus Erythematosus, Systemic / Q000150:complications*