title: Atresia of the ileocecal junction with agenesis of the ileocecal valve and vermiform appendix: report of a case.
abstract: Intestinal atresia involving the ileocecal region is a very rare intestinal malformation, and the presence or absence of the ileocecal valve influences its surgical management. We report the case of a male newborn with a provisional diagnosis of distal ileal atresia, in whom laparotomy revealed that the entire ileocecal region was atretic with an absent ileocecal valve and appendix vermiformis. We resected the dilated terminal ileum together with the atretic segment and performed an ileocolic anastomosis between the terminal ileum and the transverse microcolon without valve reconstruction. When last seen, 8 months after the operation, the baby was developing normally. Ileocolic anastomosis without valve replacement appears to be sufficient if an ileocecal valve is completely absent and only a short segment of the terminal ileum is lost.
authors.affiliation: Department of Pediatric Surgery, Medical and Health Science Center, University of Debrecen, Nagyerdei krt. 98, 4012 Debrecen, Hungary.
authors.forename: Tamás
authors.initials: T
authors.lastname: Cserni
authors.forename: Agnes
authors.initials: A
authors.lastname: Magyar
authors.forename: Tamás
authors.initials: T
authors.lastname: Németh
authors.forename: Thambipillai Sri
authors.initials: TS
authors.lastname: Paran
authors.forename: István
authors.initials: I
authors.lastname: Csízy
authors.forename: Tamas
authors.initials: T
authors.lastname: Józsa
mesh_terms: D000015:Abnormalities, Multiple / Q000175:diagnosis* / Q000601:surgery; D001065:Appendix / Q000002:abnormalities*; D002429:Cecal Diseases / Q000151:congenital / Q000175:diagnosis* / Q000601:surgery; D003937:Diagnosis, Differential; D005500:Follow-Up Studies; D006801:Humans; D007080:Ileocecal Valve / Q000002:abnormalities*; D007231:Infant, Newborn; D007409:Intestinal Atresia / Q000175:diagnosis* / Q000601:surgery; D007813:Laparotomy / Q000379:methods; D008297:Male; D011860:Radiography, Abdominal