Bilateral renal angiomyolipoma coexistent with pulmonary lymphangioleiomyomatosis and tuberous sclerosis.
A case of bilateral renal angiomyolipoma coexistent with pulmonary lymphangioleiomyomatosis and tuberous sclerosis was described, being in shock with massive hematuria. The left giant angiomyolipoma, filling the almost entire abdomen, was complicated with two large hump and moniliform aneurysms. This life-threatening hemorrhage was successfully treated by transcatheter arterial embolization; packing mechanically detachable coils into the aneurysms and embolization of trunk of the left renal artery. Lymphangioleiomyomatosis has been suggested to be an incomplete expression of tuberous sclerosis. Although coexisting renal and pulmonary involvement in tuberous sclerosis is rare, it is important to recognize lymphangioleiomyomatosis as a pulmonary involvement of angiomyolipoma with tuberous sclerosis.
Yoshida
Soichiro
S
Department of Urology, Saitama Medical Center, Saitama Medical School, 1981 Tsujido, Kamoda, Kawagoe, Saitama, 350-8550, Japan. soichiroyoshida2000@yahoo.co.jp
Hayashi
Tetsuo
T
Ishii
Nobuyuki
N
Yoshinaga
Atsushi
A
Ohno
Rena
R
Terao
Toshiya
T
Watanabe
Toru
T
Yamada
Takumi
T
Osada
Hisato
H
D018207:Angiomyolipoma / Q000150:complications*; D005260:Female; D006801:Humans; D007680:Kidney Neoplasms / Q000150:complications*; D008175:Lung Neoplasms / Q000150:complications*; D018192:Lymphangioleiomyomatosis / Q000150:complications*; D008297:Male; D009378:Neoplasms, Multiple Primary / Q000150:complications*; D014402:Tuberous Sclerosis / Q000150:complications*