title: [Domiciliary respiratory muscle training in myotonic dystrophy].
abstract: A 42-year-old man diagnosed with myotonic dystrophy experienced loss of respiratory muscle strength over a period of 6 months. We report the application of a domiciliary training program targeting both inspiratory and expiratory muscles. Maximal inspiratory and expiratory pressures, forced vital capacity, and forced midexpiratory flow rate were measured 6 months before start of training, just before commencement of the program, and immediately after 12 weeks of training. Adherence to the program was satisfactory. Inspiratory muscle training was efficacious in increasing respiratory muscle strength. Expiratory muscle training, which made use of the Threshold PEP bronchial hygiene device incorporating an adapted flutter valve, was not efficacious in increasing maximal expiratory pressure or halting its loss. However, decreased obstruction of medium-caliber airways was observed with use of the device.
authors.affiliation: Departamento de Neumología, Hospital de la Santa Creu i de Sant Pau, Facultad de Medicina, Universitat Autònoma de Barcelona, Barcelona, España. fregonezi@ufrnet.br
authors.forename: Guilherme Augusto
authors.initials: GA
authors.lastname: de Freitas Fregonezi
authors.forename: Vanessa Regiane
authors.initials: VR
authors.lastname: Resqueti
authors.forename: Pere
authors.initials: P
authors.lastname: Casan
mesh_terms: D000328:Adult; D015444:Exercise; D006699:Home Care Services; D006801:Humans; D008297:Male; D009223:Myotonic Dystrophy / Q000628:therapy*; D012132:Respiratory Muscles / Q000502:physiology*; D016896:Treatment Outcome