title: Bilateral renal angiomyolipoma coexistent with pulmonary lymphangioleiomyomatosis and tuberous sclerosis.
abstract: A case of bilateral renal angiomyolipoma coexistent with pulmonary lymphangioleiomyomatosis and tuberous sclerosis was described, being in shock with massive hematuria. The left giant angiomyolipoma, filling the almost entire abdomen, was complicated with two large hump and moniliform aneurysms. This life-threatening hemorrhage was successfully treated by transcatheter arterial embolization; packing mechanically detachable coils into the aneurysms and embolization of trunk of the left renal artery. Lymphangioleiomyomatosis has been suggested to be an incomplete expression of tuberous sclerosis. Although coexisting renal and pulmonary involvement in tuberous sclerosis is rare, it is important to recognize lymphangioleiomyomatosis as a pulmonary involvement of angiomyolipoma with tuberous sclerosis.
authors.affiliation: Department of Urology, Saitama Medical Center, Saitama Medical School, 1981 Tsujido, Kamoda, Kawagoe, Saitama, 350-8550, Japan. soichiroyoshida2000@yahoo.co.jp
authors.forename: Soichiro
authors.initials: S
authors.lastname: Yoshida
authors.forename: Tetsuo
authors.initials: T
authors.lastname: Hayashi
authors.forename: Nobuyuki
authors.initials: N
authors.lastname: Ishii
authors.forename: Atsushi
authors.initials: A
authors.lastname: Yoshinaga
authors.forename: Rena
authors.initials: R
authors.lastname: Ohno
authors.forename: Toshiya
authors.initials: T
authors.lastname: Terao
authors.forename: Toru
authors.initials: T
authors.lastname: Watanabe
authors.forename: Takumi
authors.initials: T
authors.lastname: Yamada
authors.forename: Hisato
authors.initials: H
authors.lastname: Osada
mesh_terms: D018207:Angiomyolipoma / Q000150:complications*; D005260:Female; D006801:Humans; D007680:Kidney Neoplasms / Q000150:complications*; D008175:Lung Neoplasms / Q000150:complications*; D018192:Lymphangioleiomyomatosis / Q000150:complications*; D008297:Male; D009378:Neoplasms, Multiple Primary / Q000150:complications*; D014402:Tuberous Sclerosis / Q000150:complications*