title: [The use of Nd-Yag laser in the treatment of tracheal tumor in 14 years old child with mukopolisacharydosis type II].
abstract: Hunter's Syndrome (MPS II) is a class of hereditary disorder characterized by a deficiency of specific enzyme--iduronate sulphatase required to break down mucopolisacharides and occurs in Poland in one of 100-150 thousand male live births. MPS II may be lethal in the second decade of life as a result of infiltrativ cardiomiopathy leading to irreversible heart failure or upper airway obstruction caused by infiltration, granulation and deformation in trachea or larynx. We report a case of 14-year-old male with Hunter Syndrome who developed tracheal obstruction and was treated with Nd-Yag laser. We discuss the possibility of treatment and our results--improvement in patient's symptomatic and functional status.
authors.affiliation: Katedra i Klinika Otolaryngologii Collegium Medicum im. Rydygiera w Bydgoszczy, Uniwersytetu Mikołaja Kopernika w Toruniu.
authors.forename: Józef
authors.initials: J
authors.lastname: Mierzwiński
authors.forename: Aleksander
authors.initials: A
authors.lastname: Zwierz
authors.forename: Artur
authors.initials: A
authors.lastname: Jaworski
authors.forename: Ryszard
authors.initials: R
authors.lastname: Redziński
authors.forename: Władysław
authors.initials: W
authors.lastname: Bandrowicz
authors.forename: Krzysztof
authors.initials: K
authors.lastname: Dalke
authors.forename: Paweł
authors.initials: P
authors.lastname: Burduk
mesh_terms: D000293:Adolescent; D000402:Airway Obstruction / Q000175:diagnosis / Q000209:etiology / Q000601:surgery*; D001999:Bronchoscopy; D006801:Humans; D053685:Laser Therapy; D008297:Male; D016532:Mucopolysaccharidosis II / Q000150:complications*; D009354:Neodymium; D014134:Tracheal Neoplasms / Q000175:diagnosis / Q000209:etiology / Q000601:surgery*; D016896:Treatment Outcome
chemical_list: D009354:Neodymium