title: Cardiac involvement in Kugelberg-Welander disease: a case report and review.
abstract: There are few reports of cardiac involvement in patients with Kugelberg-Welander disease. We report a case of a 51-year-old man with Kugelberg-Welander disease who presented with syncope. His electrocardiogram showed complete right bundle branch block and transient complete atrioventricular block without escape rhythm. He was successfully treated with emergency temporary pacing followed by permanent pacemaker implantation. In this report, we review the relevant literature and argue that patients with Kugelberg-Welander disease should be evaluated regularly for cardiac disease.
authors.affiliation: Division of Cardiovascular Medicine, Department of Internal Medicine, Shimane University School of Medicine, Izumo City, Shimane, Japan.
authors.forename: Nobuyuki
authors.initials: N
authors.lastname: Takahashi
authors.forename: Toshio
authors.initials: T
authors.lastname: Shimada
authors.forename: Yutaka
authors.initials: Y
authors.lastname: Ishibashi
authors.forename: Takashi
authors.initials: T
authors.lastname: Sugamori
authors.forename: Yoshifumi
authors.initials: Y
authors.lastname: Hirano
authors.forename: Nobuyuki
authors.initials: N
authors.lastname: Oyake
authors.forename: Yo
authors.initials: Y
authors.lastname: Murakami
mesh_terms: D006327:Heart Block / Q000150:complications* / Q000175:diagnosis / Q000628:therapy; D006801:Humans; D008297:Male; D008875:Middle Aged; D014897:Spinal Muscular Atrophies of Childhood / Q000150:complications*; D013575:Syncope / Q000150:complications