A case of split notochord syndrome: a child with a neuroenteric fistula presenting with meningitis.
The authors describe a case of split notochord syndrome with a neuroenteric fistula in a newborn presenting with meningitis. Associated anomalies included agenesis of the corpus callosum, short colon, malrotation, epispadias, and an abnormally high bifurcation of the abdominal aorta and inferior vena cava. The embryological mechanisms and etiologic theories are discussed in short.
van Ramshorst
Gabrielle H
GH
Department of Pediatric Surgery, Erasmus Medical Center/Sophia Children's Hospital, 3000 CB Rotterdam, the Netherlands.
Lequin
Maarten H
MH
Mancini
Grazia M S
GM
van de Ven
Cornelis P
CP
D000015:Abnormalities, Multiple; D002493:Central Nervous System Diseases / Q000150:complications / Q000175:diagnosis* / Q000601:surgery; D003108:Colonic Diseases / Q000150:complications / Q000175:diagnosis* / Q000601:surgery; D006801:Humans; D007231:Infant, Newborn; D007412:Intestinal Fistula / Q000150:complications / Q000175:diagnosis* / Q000601:surgery; D008297:Male; D008581:Meningitis / Q000209:etiology*; D009672:Notochord / Q000002:abnormalities*; D013577:Syndrome