Dilatation of the intrahepatic bile duct associated with congenital anomalous junction of the cystic duct--a new disease entity.
We describe 3 children with dilatation of the intrahepatic bile duct, who had anomalous junctions of the cystic duct, 2 high and 1 low, without pancreaticobiliary maljunction. They were all male, and underwent excision of the gallbladder and the extrahepatic bile duct followed by a Roux-en-Y hepaticojejunostomy as a definitive surgery. Postoperatively, the dilated intrahepatic bile duct became normal in size. From these 3 cases, we propose a new disease entity-dilatation of the intrahepatic bile duct because of congenital anomalous junction of the cystic duct.
Ohama
Kazunori
K
Department of Pediatric Surgery, Ishikawa Prefectural Central Hospital, Kanazawa, Ishikawa, 920-8530 Japan. kazu-ohama@ipch.jp
Ishikawa
Nobuki
N
D001649:Bile Duct Diseases / Q000151:congenital* / Q000175:diagnosis / Q000601:surgery*; D002648:Child; D003549:Cystic Duct / Q000002:abnormalities* / Q000601:surgery*; D004106:Dilatation; D006801:Humans; D008297:Male; D011171:Portoenterostomy, Hepatic