[The use of Nd-Yag laser in the treatment of tracheal tumor in 14 years old child with mukopolisacharydosis type II].
Hunter's Syndrome (MPS II) is a class of hereditary disorder characterized by a deficiency of specific enzyme--iduronate sulphatase required to break down mucopolisacharides and occurs in Poland in one of 100-150 thousand male live births. MPS II may be lethal in the second decade of life as a result of infiltrativ cardiomiopathy leading to irreversible heart failure or upper airway obstruction caused by infiltration, granulation and deformation in trachea or larynx. We report a case of 14-year-old male with Hunter Syndrome who developed tracheal obstruction and was treated with Nd-Yag laser. We discuss the possibility of treatment and our results--improvement in patient's symptomatic and functional status.
Mierzwiński
Józef
J
Katedra i Klinika Otolaryngologii Collegium Medicum im. Rydygiera w Bydgoszczy, Uniwersytetu Mikołaja Kopernika w Toruniu.
Zwierz
Aleksander
A
Jaworski
Artur
A
Redziński
Ryszard
R
Bandrowicz
Władysław
W
Dalke
Krzysztof
K
Burduk
Paweł
P
D000293:Adolescent; D000402:Airway Obstruction / Q000175:diagnosis / Q000209:etiology / Q000601:surgery*; D001999:Bronchoscopy; D006801:Humans; D053685:Laser Therapy; D008297:Male; D016532:Mucopolysaccharidosis II / Q000150:complications*; D009354:Neodymium; D014134:Tracheal Neoplasms / Q000175:diagnosis / Q000209:etiology / Q000601:surgery*; D016896:Treatment Outcome
D009354:Neodymium