title: Purely cystic form of choroid plexus papilloma with acute hydrocephalus in an infant. Case report.
abstract: Infants with acute hydrocephalus often present with nonspecific neurological signs, and cystic choroid plexus papilloma (CPP) is a very rare cause of acute obstructive hydrocephalus. The authors present the case of a 1-year-old girl who became irritable, started vomiting, and became comatose within a day. Magnetic resonance (MR) imaging revealed a cystic lesion in the third ventricle as well as hydrocephalus. Although the aqueduct appeared to be patent, phase-contrast MR imaging showed no pulsatile flow of cerebrospinal fluid in the ventricles. An emergent endoscopic third ventriculostomy was performed. Endoscopic examination revealed a highly mobile cyst attached by a pedicle to the choroid plexus adjacent to the Monro foramen in the lateral ventricle. The cyst was totally excised during the endoscopic procedure and was subsequently diagnosed as a CPP on the basis of histopathological findings. Purely cystic CPP is a very rare pathological entity; however, when it does occur, it can cause obstructive hydrocephalus which, without rapid diagnosis and surgical intervention, could lead to sudden death.
authors.affiliation: Department of Neurosurgery, Graduate School of Medical Sciences, Kyushu University, Fukuoka, Japan. yamiyagi@ns.med.kyushu-u.ac.jp
authors.forename: Yasushi
authors.initials: Y
authors.lastname: Miyagi
authors.forename: Yoshihiro
authors.initials: Y
authors.lastname: Natori
authors.forename: Satoshi O
authors.initials: SO
authors.lastname: Suzuki
authors.forename: Toru
authors.initials: T
authors.lastname: Iwaki
authors.forename: Takato
authors.initials: T
authors.lastname: Morioka
authors.forename: Koichi
authors.initials: K
authors.lastname: Arimura
authors.forename: Yoshihisa
authors.initials: Y
authors.lastname: Maeda
authors.forename: Tadahisa
authors.initials: T
authors.lastname: Shono
authors.forename: Koichiro
authors.initials: K
authors.lastname: Matsukado
authors.forename: Tomio
authors.initials: T
authors.lastname: Sasaki
mesh_terms: D000208:Acute Disease; D002555:Cerebrospinal Fluid / Q000378:metabolism; D003560:Cysts / Q000209:etiology / Q000473:pathology / Q000601:surgery; D005260:Female; D006801:Humans; D006849:Hydrocephalus / Q000209:etiology* / Q000473:pathology* / Q000601:surgery; D007223:Infant; D008279:Magnetic Resonance Imaging; D020288:Papilloma, Choroid Plexus / Q000150:complications* / Q000473:pathology* / Q000601:surgery; D020542:Third Ventricle / Q000473:pathology / Q000601:surgery