title: Botryoid rhabdomyosarcoma of the biliary tract in children: a unique case report.
abstract: Rhabdomyosarcoma (RMS) is the most common tumour of the biliary tree in childhood. In children, it is a rare lesion, accounting for about 1% of all RMS. Hepatobiliary botryoid RMS is a disease affecting young children at a median age of about 3 years. In literature, the radiological findings of hepatobiliary RMS have been described in small series and some case reports. In this case report, we present a rare case of RMS of the extrahepatic biliary tree initially diagnosed as a choledochal cyst.
authors.affiliation: Department of Surgical Sciences, Pediatric Surgical Unit, University of Verona, Verona, Italy, and Department of Woman and Children, King's College Hospital NHS Trust, London, UK. zampius@libero.it
authors.forename: N
authors.initials: N
authors.lastname: Zampieri
authors.forename: F
authors.initials: F
authors.lastname: Camoglio
authors.forename: M
authors.initials: M
authors.lastname: Corroppolo
authors.forename: M
authors.initials: M
authors.lastname: Cecchetto
authors.forename: S
authors.initials: S
authors.lastname: Ornis
authors.forename: A
authors.initials: A
authors.lastname: Ottolenghi
mesh_terms: D000971:Antineoplastic Combined Chemotherapy Protocols / Q000627:therapeutic use; D001650:Bile Duct Neoplasms / Q000175:diagnosis* / Q000188:drug therapy / Q000601:surgery; D017734:Bile Ducts, Extrahepatic; D002648:Child; D015529:Choledochal Cyst / Q000175:diagnosis*; D003131:Combined Modality Therapy / Q000379:methods; D003138:Common Bile Duct Neoplasms / Q000175:diagnosis / Q000188:drug therapy / Q000601:surgery; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D012208:Rhabdomyosarcoma / Q000175:diagnosis* / Q000188:drug therapy / Q000601:surgery