Acute para-esophageal hernia in Ehlers-Danlos Syndrome.
Para-esophageal herniation is a recognized complication of the Ehlers-Danlos syndrome. While chronic herniation is well described, acute symptomatic herniation is far less common. We describe a case of acute, life-threatening para-esophageal herniation of the abdominal viscera in a young woman with Ehlers-Danlos syndrome. Careful anaesthetic assessment and surgical management resulted in a successful clinical outcome.
Ignoto
Augusto
A
Thoracic Surgery Unit, Ospedale Civile Maria Paternò Arezzo, Ragusa, Italy.
Ambrogio
Marco
M
Distefano
Nunzio
N
Presti
Corrado
C
Puglisi
Francesco
F
Vaccarella
Antonio
A
Nucifora
Rosario
R
D000208:Acute Disease; D000328:Adult; D004535:Ehlers-Danlos Syndrome / Q000150:complications* / Q000175:diagnosis / Q000601:surgery; D005260:Female; D006551:Hernia, Hiatal / Q000175:diagnosis / Q000209:etiology* / Q000601:surgery; D006801:Humans; D016896:Treatment Outcome