title: [Oral rehabilitation of a patient with Wilson-syndrome using MK1 bolt attachment. A case report].
abstract: The oral condition of neurologically compromised patients seemed to be worse as compared to the healthy population, which is confirmed by concrete data in case of epilepsy patients. The dental status of our 33 years old patient with Wilson-syndrome showed the same situation. The Wilson-syndrome is a hepatolenticular degeneration, with the disfunction of copper excretion in liver. Toxic dose of copper is accumulated in liver, in the nuclei of central nerve system, in kidneys, and in cornea. Deficiency of coeruloplasmin characterizes the disease which might occur in a form of acute hepatitis, chronic active hepatitis, cirrhosis or hepatosplenomegaly without any symptom. Initial symptoms might usually be extrahepatic, with the presence of the green and golden brown Kayser-Fleischer copper deposition. Treatment is necessary until the end of life, 1 g Penicillamine/ day. Our patient with Wilson-syndrome has been treated for 17 years at the Department of Neurology Semmelweis University. Dystonia, speech disorder, and intention tremor are rampant among his symptoms. At the time of admittance to dental clinic, both the upper and lower dental arches belonged to class 2B according to the Fábián and Fejérdy classification of partial edentulousness. After root canal fillings and cementation of dowel cores, an upper and lower fix and removable partial denture combination was made. Oral hygiene was controlled every three months. Dentures are worn for half a year without complaint.
authors.affiliation: Semmelweis Egyetem, Fogpótlástani Klinika, Budapest.
authors.forename: Katalin
authors.initials: K
authors.lastname: Károlyházy
authors.forename: Péter
authors.initials: P
authors.lastname: Kivovics
authors.forename: Péter
authors.initials: P
authors.lastname: Faluhelyi
authors.forename: Pál
authors.initials: P
authors.lastname: Fejérdy
mesh_terms: D000328:Adult; D003779:Denture Design; D003832:Denture, Partial, Removable; D006527:Hepatolenticular Degeneration / Q000150:complications* / Q000534:rehabilitation; D006801:Humans; D007576:Jaw, Edentulous, Partially / Q000209:etiology* / Q000534:rehabilitation*; D008297:Male; D016876:Metal Ceramic Alloys; D009910:Oral Hygiene; D017060:Patient Satisfaction; D012390:Root Canal Therapy; D013577:Syndrome
chemical_list: D016876:Metal Ceramic Alloys