title: [Anesthesic management of a patient with Stickler's syndrome].
abstract: Stickler's syndrome is a connective-tissue disease of autosome dominant inheritance. This report concerns a 3-year-old girl with Stickler's syndrome who underwent arthroplasty under general anesthesia. After slow induction of anesthesia with an inhalation anesthetic, neither a oropharyngeal airway nor a laryngeal mask airway fitted her, and mask ventilation and endotracheal intubation became difficult. Endotracheal intubation was performed not with a muscle relaxant but under deep anesthesia. Care should be taken when planning anesthesia for a case of this syndrome because airway management is often difficult and emergency surgery for detached retinas might be required.
authors.affiliation: Department of Anesthesiology and Critical Care Medicine, Asahikawa Medical College, Asahikawa.
authors.forename: Hiroshi
authors.initials: H
authors.lastname: Yokota
authors.forename: Osamu
authors.initials: O
authors.lastname: Takahata
authors.forename: Kazufumi
authors.initials: K
authors.lastname: Sengoku
authors.forename: Hanako
authors.initials: H
authors.lastname: Okada
authors.forename: Hiroshi
authors.initials: H
authors.lastname: Iwasaki
mesh_terms: D000768:Anesthesia, General / Q000379:methods*; D019645:Arthroplasty, Replacement, Knee; D002675:Child, Preschool; D003240:Connective Tissue Diseases / Q000150:complications*; D005260:Female; D006801:Humans; D007442:Intubation, Intratracheal / Q000379:methods*; D010855:Pierre Robin Syndrome / Q000150:complications*