title: Atypical lung involvement in a patient with systemic juvenile xanthogranuloma.
abstract: Juvenile xanthogranuloma (JXG) is a non-Langerhans cell histiocytosis characterized by xanthoma-like cutaneous lesions. It is a benign condition that is generally asymptomatic. Visceral involvement is uncommon, but when present may occur in various locations and in different combinations. Pulmonary involvement has been reported as bilateral, multiple micro- or macronodular lesions. We present a 10-year-old boy with systemic (skin, lung, liver and kidney) JXG who showed lung involvement with mainly an interstitial pattern. Bilateral multiple micronodules in both lungs and mediastinal adenopathy were also present.
authors.affiliation: Department of Radiology, Istanbul Medical School, Istanbul University, 34390 Capa, Turkey. drbarisbakir@yahoo.com
authors.forename: Baris
authors.initials: B
authors.lastname: Bakir
authors.forename: Emin
authors.initials: E
authors.lastname: Unuvar
authors.forename: Ege
authors.initials: E
authors.lastname: Terzibasioglu
authors.forename: Koray
authors.initials: K
authors.lastname: Guven
mesh_terms: D001706:Biopsy; D002648:Child; D005500:Follow-Up Studies; D006801:Humans; D007674:Kidney Diseases / Q000175:diagnosis; D008107:Liver Diseases / Q000175:diagnosis; D008171:Lung Diseases / Q000175:diagnosis*; D008297:Male; D013902:Radiography, Thoracic; D014057:Tomography, X-Ray Computed; D018084:Ultrasonography, Interventional; D014972:Xanthogranuloma, Juvenile / Q000175:diagnosis*