Schwannomatosis involving peripheral nerves: a case report.
Schwannomatosis or neurilemmomatosis has been used to describe patients with multiple nonvestibular schwannomas with no other stigmata of neurofibromatosis type-2 (NF-2). In our case, schwannomatosis, multiple schwannomas were present in a 21-yr-old woman with no stigmata or family history of NF-1 or NF-2. She had no evidence of vestibular schwannoma or other intracranial tumors. Multiple peripheral tumors were found in the carotid space of the neck, and soft tissue of posterior shoulder, lower back, ankle and middle mediastinum. All of those tumors were completely limited to the right side of the body. All surgically removed tumor specimens in this patient proved to be schwannomas.
Kim
Dong Hun
DH
Department of Radiology, Chosun University Hospital, Gwangju, Korea.
Hwang
Jung Hwa
JH
Park
Sung-Tae
ST
Shin
Ji Hoon
JH
D000328:Adult; D005260:Female; D006801:Humans; D009442:Neurilemmoma / Q000175:diagnosis* / Q000601:surgery*; D010524:Peripheral Nervous System Neoplasms / Q000175:diagnosis* / Q000601:surgery*; D016896:Treatment Outcome