title: Acute para-esophageal hernia in Ehlers-Danlos Syndrome.
abstract: Para-esophageal herniation is a recognized complication of the Ehlers-Danlos syndrome. While chronic herniation is well described, acute symptomatic herniation is far less common. We describe a case of acute, life-threatening para-esophageal herniation of the abdominal viscera in a young woman with Ehlers-Danlos syndrome. Careful anaesthetic assessment and surgical management resulted in a successful clinical outcome.
authors.affiliation: Thoracic Surgery Unit, Ospedale Civile Maria Paternò Arezzo, Ragusa, Italy.
authors.forename: Augusto
authors.initials: A
authors.lastname: Ignoto
authors.forename: Marco
authors.initials: M
authors.lastname: Ambrogio
authors.forename: Nunzio
authors.initials: N
authors.lastname: Distefano
authors.forename: Corrado
authors.initials: C
authors.lastname: Presti
authors.forename: Francesco
authors.initials: F
authors.lastname: Puglisi
authors.forename: Antonio
authors.initials: A
authors.lastname: Vaccarella
authors.forename: Rosario
authors.initials: R
authors.lastname: Nucifora
mesh_terms: D000208:Acute Disease; D000328:Adult; D004535:Ehlers-Danlos Syndrome / Q000150:complications* / Q000175:diagnosis / Q000601:surgery; D005260:Female; D006551:Hernia, Hiatal / Q000175:diagnosis / Q000209:etiology* / Q000601:surgery; D006801:Humans; D016896:Treatment Outcome