title: Moyamoya disease associated with midaortic syndrome.
abstract: We report a 1-year-old girl who presented moyamoya disease associated with midaortic syndrome. She had been treated for cardiac failure and severe hypertension due to midaortic syndrome until she suffered seizure and repeated cerebral ischemic attack. Cerebral angiography revealed stenosis of the bilateral internal carotid artery at its terminal portion. She was successfully treated with encephaloduroarteriosynangiosis, and ischemic attack ceased postoperatively. This is the first report of moyamoya disease with midaortic syndrome. Although cerebral ischemic attack has been effectively managed by encephaloduroarteriosynangiosis, renovascular hypertension is still difficult to control.
authors.affiliation: Department of Neurosurgery, Oita Prefectural Hospital, Oita, Japan. korematsu-nsu@umin.ac.jp
authors.forename: Kojiro
authors.initials: K
authors.lastname: Korematsu
authors.forename: Susumu
authors.initials: S
authors.lastname: Yoshioka
authors.forename: Takashi
authors.initials: T
authors.lastname: Maruyama
authors.forename: Yasuyuki
authors.initials: Y
authors.lastname: Nagai
authors.forename: Kazuhiko
authors.initials: K
authors.lastname: Inoue
authors.forename: Naoko
authors.initials: N
authors.lastname: Yukaya
authors.forename: Haruhisa
authors.initials: H
authors.lastname: Baba
authors.forename: Jun-ichi
authors.initials: J
authors.lastname: Kuratsu
mesh_terms: D001017:Aortic Coarctation / Q000150:complications* / Q000175:diagnosis / Q000628:therapy; D005260:Female; D006801:Humans; D006978:Hypertension, Renovascular / Q000150:complications* / Q000175:diagnosis / Q000628:therapy; D007223:Infant; D009072:Moyamoya Disease / Q000150:complications* / Q000175:diagnosis / Q000628:therapy; D013577:Syndrome