Ebstein's anomaly of the tricuspid valve in combination of tetralogy of Fallot: total correction in infancy.
Ebstein's anomaly of the tricuspid valve in combination with Tetralogy of Fallot is extremely rare. We report a patient with these combined entities in a baby presented with cyanosis and right heart failure soon after birth. Total correction toward biventricular repair was successfully conducted when he was 7 months old. For management of a patient with such rare complex anomalies, we recommend Carpentier's technique for Ebstein's anomaly to restore the morphology of the right ventricle, and "one and half ventricle repair" can be a salvage procedure if the right ventricle is not functionally tolerant.
Lai
Chao-Han
CH
Division of Cardiovascular Surgery, Department of Surgery, National Cheng Kung University Hospital, Tainan, Taiwan.
Wu
Jing-Ming
JM
Yang
Yu-Jen
YJ
D004437:Ebstein Anomaly / Q000000981:diagnostic imaging / Q000601:surgery*; D004452:Echocardiography; D006801:Humans; D007223:Infant; D008297:Male; D013771:Tetralogy of Fallot / Q000000981:diagnostic imaging / Q000601:surgery*; D014262:Tricuspid Valve Insufficiency / Q000209:etiology