Giant arteriovenous malformation associated with unilateral moyamoya disease in a child: case report.
BACKGROUND
Cerebral AVMs associated with definite or probable moyamoya disease is a very rare situation, and the association between them is unclear.


METHODS
An 8-year-old boy presented with repeated transient motor weakness in the left arm and leg for 1 year. On his admission, physical examination and neuropsychological testing showed no exact neurological deficits. Magnetic resonance imaging showed a giant AVM in the right basal ganglia and thalamus. Angiography revealed occlusion of left ICA and bilateral PCA with well-developed basal collateral vessels. A giant AVM was also noticed in angiography, which was filled by basal collateral vessels from both left anterior circulation and posterior circulation. The diagnosis of unilateral moyamoya disease combined with a Spetzler-Martin grade V AVM was made. The patient was managed nonoperatively and discharged with close follow-up.


CONCLUSIONS
We present a rare case of giant AVM-associated with unilateral moyamoya disease, and giant AVM makes planning any aggressive treatments difficult.
Chen
Zhi
Z
Department of Neurosurgery, Southwest Hospital, Third Military Medical University, Chongqing 400038, The People's Republic of China. chenzhi@xinhuanet.com
Zhu
Gang
G
Feng
Hua
H
Lin
Jiangkai
J
Wu
Nan
N
D002648:Child; D006801:Humans; D002538:Intracranial Arteriovenous Malformations / Q000175:diagnosis* / Q000209:etiology* / Q000628:therapy; D008297:Male; D009072:Moyamoya Disease / Q000150:complications* / Q000175:diagnosis* / Q000628:therapy