Spinal epidural Rosai-Dorfman disease preceding by relapsing uveitis: a case report with literature review.
METHODS
Case report.


METHODS
Tertiary referral center hospital in Taiwan.


OBJECTIVE
To report a case of spinal Rosai-Dorfman disease (RDD) presenting with paraparesis and also preceding by relapsing uveitis for 6 months. A thoracic laminectomy was performed to remove the solid mass. The pathological diagnosis reveals infiltrating histiocytes, emperipolesis and positivity for S-100. There is no recurrence 1 year later with MR imaging.


CONCLUSIONS
The relapsing idiopathic uveitis may be a prodrome for this unusual disease, because RDD is associated closely to defective immunogical response. Early and accurate diagnosis of CNS RDD may reverse the neurologic deficits by early decompression.
Huang
Y-C
YC
Department of Neurosurgery, Chang Gung Memorial Hospital, Chang Gung University, College of Medicine, Taoyuan, Taiwan.
Tan
H-Y
HY
Jung
S-M
SM
Chuang
W-Y
WY
Chuang
C-C
CC
Hsu
P-W
PW
Chang
C-N
CN
D004824:Epidural Space / Q000276:immunology / Q000473:pathology*; D005260:Female; D015618:Histiocytosis, Sinus / Q000175:diagnosis* / Q000209:etiology* / Q000276:immunology; D006801:Humans; D012008:Recurrence; D013122:Spinal Diseases / Q000175:diagnosis* / Q000209:etiology* / Q000276:immunology; D014605:Uveitis / Q000150:complications* / Q000175:diagnosis* / Q000276:immunology