Surgery for cystic lymphangioma in Gorlin-Goltz syndrome.
BACKGROUND
We present a case of three major lymphomesenteric cysts in a female patient with known basal cell nevus syndrome (BCNS or Gorlin-Goltz syndrome).


CONCLUSIONS
Although those cysts have been reported to appear in this syndrome, the exact prevalence is not known. In this case, the patient suffered from severe and recurrent abdominal pain due to bowel obstruction.


CONCLUSIONS
By causing severe symptoms, cystic lymphangiomas are an important complication of the BCNS despite of their seldom occurrence. Surgeons confronted with intraabdominal masses in a patient with BCNS should always be aware of this manifestation of the disorder and plan interdisciplinary operations.
Kayser
C
C
Department of General Surgery, Freiburg University Hospital, Hugstetter Strasse 55, 79106, Freiburg, Germany. carolin.kayser@uniklinik-freiburg.de
Kayser
G
G
Baier
P
P
Hopt
U T
UT
Eggstein
S
S
D015746:Abdominal Pain / Q000209:etiology; D000328:Adult; D001478:Basal Cell Nevus Syndrome / Q000150:complications*; D004727:Endothelium / Q000473:pathology; D005260:Female; D006801:Humans; D018191:Lymphangioma, Cystic / Q000000981:diagnostic imaging / Q000209:etiology* / Q000473:pathology / Q000601:surgery*; D012008:Recurrence; D014057:Tomography, X-Ray Computed