Orofacial dystonia related to Sjogren's syndrome.
Sjogren's syndrome (SS), either primary or secondary, is rarely accompanied by CNS complications. We report the exceptional case of a patient with secondary SS, who presented orofacial dystonia as a consequence of her disease. Initial treatment with clonazepam and levetiracetam was unsuccessful. However, dystonia was dramatically improved by a treatment with corticosteroids. This case demonstrates that corticosteroids can be efficacious in the treatment of dystonia related to SS.
Papageorgiou
Sokratis G
SG
Department of Neurology, Eginition Hospital, Medical School, University of Athens, 74, Vassilissis Sofias Avenue, 11528 Athens, Greece. sokpapa@med.uoa.gr
Kontaxis
Theodoros
T
Bonakis
Anastasios
A
Kalfakis
Nikolaos
N
D000305:Adrenal Cortex Hormones / Q000627:therapeutic use; D001921:Brain / Q000473:pathology; D002998:Clonazepam / Q000627:therapeutic use; D004421:Dystonia; D020821:Dystonic Disorders / Q000150:complications* / Q000175:diagnosis; D005145:Face / Q000473:pathology*; D005260:Female; D006801:Humans; D000077287:Levetiracetam; D008279:Magnetic Resonance Imaging / Q000379:methods; D008875:Middle Aged; D010889:Piracetam / Q000031:analogs & derivatives / Q000627:therapeutic use; D012074:Remission Induction; D012859:Sjogren's Syndrome / Q000150:complications* / Q000175:diagnosis; D016896:Treatment Outcome
D000305:Adrenal Cortex Hormones; D000077287:Levetiracetam; D002998:Clonazepam; D010889:Piracetam