Dramatic effect of sirolimus on renal angiomyolipomas in a patient with tuberous sclerosis complex.
Angiomyolipomas are very common in patients with tuberous sclerosis complex (TSC) and cause substantial morbidity. Until now, arterial embolization has been the recommended treatment for symptomatic patients. We report the case of a woman with TSC and giant angiolipomas in whom sirolimus induced a dramatic reduction in bilateral renal tumors.
Herry
Isabelle
I
Service de pneumologie, AP-HP, Hôpital Bichat-Claude Bernard, Paris, France, Université Paris 7, France.
Neukirch
Catherine
C
Debray
Marie-Pierre
MP
Mignon
Françoise
F
Crestani
Bruno
B