Auditory manifestations of superficial hemosiderosis of the central nervous system.
Superficial hemosiderosis of the central nervous system (SH-CNS) is a relatively rare condition caused by chronic or repeated subarachnoid bleeding. The aim of this article was to present hearing disorders related to SH-CNS, and to describe results of magnetic resonance imaging (MRI) to confirm the diagnosis. We performed a retrospective case review at a tertiary referral center. Clinical presentation, auditory manifestations and MRI findings of two patients with SH-CNS are reported. The two patients experienced bilateral sensorineural hearing loss (SNHL) that progressively worsened. MRI revealed typical aspects of SH-CNS on T2-weighted images. Progressive bilateral SNHL is the most common manifestation of SH-CNS. The otolaryngologist should be aware of this disease that can be easily diagnosed with MRI.
Ayache
Denis
D
Otology-Neurotology Unit, Department of Otolaryngology Head and Neck Surgery, Fondation Adolphe de Rothschild, 25-29 rue Manin, 75019, Paris, France. dayache@fo-rothschild.fr
Blaivie
Catherine
C
El Kohen
Asma
A
Tosello
Lucrecia
L
Williams
Marc T
MT
D000328:Adult; D002493:Central Nervous System Diseases / Q000150:complications* / Q000175:diagnosis; D003937:Diagnosis, Differential; D005260:Female; D006310:Hearing Aids; D006319:Hearing Loss, Sensorineural / Q000175:diagnosis / Q000209:etiology*; D006486:Hemosiderosis / Q000150:complications* / Q000175:diagnosis; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male