Anaesthesiological and ventilatory precautions during cardiac surgery in Steinert's disease.
Myotonic dystrophia type I or Steinert's disease is a progressive multisystemic-inherited neuromuscular disease. Higher sensitivity to sedatives, anaesthetic, and neuromuscular blocking agents may result in cardiovascular and respiratory complications. We describe the anaesthesiological and ventilatory measures in a 43-year-old patient with Steinert's disease successfully undergoing cardiac surgery.
Klompe
Lennart
L
Department of Cardiothoracic Surgery, Erasmus MC, Rotterdam, The Netherlands. l.klompe@erasmusmc.nl
Lancé
Marcus
M
van der Woerd
Dries
D
Scohy
Thierry
T
Bogers
Ad J J C
AJ
D000328:Adult; D000768:Anesthesia, General; D013504:Cardiovascular Surgical Procedures; D006801:Humans; D008297:Male; D009223:Myotonic Dystrophy; D012086:Reoperation; D012121:Respiration, Artificial; D013771:Tetralogy of Fallot / Q000473:pathology / Q000601:surgery*