[A rare tracheal tumour: solitary fibroma].
BACKGROUND
Solitary fibromas are rare anatomo-pathological entities, described initially in the pleural cavity. The mesenchymal origin of these tumours explains their widespread distribution.


METHODS
The authors report a case of solitary fibroma of the trachea in a woman of 30 years of age, presenting as acute respiratory distress and preceded by a 2 year history of episodes of dyspnoea diagnosed as unstable asthma. CT and MRI imaging showed evidence of a localised tracheal tumour without mediastinal infiltration. The images and macroscopic appearances were non-specific. Bronchoscopic resection of the tumour gave immediate relief of the symptoms. Histology, which was positive for anti-CD34 antibodies and negative for epithelial, muscular and neurological markers, led to a diagnosis of solitary fibroma with no evidence of malignancy.


CONCLUSIONS
To our knowledge, this observation is the first description of a primary solitary fibroma localised to the trachea. The clinical and radiological features are no different from those of other tracheal tumours. After excision, the prognosis is good but long-term follow-up is necessary on account of the risk of local recurrence or metastasis.
Gomez
E
E
Service des Maladies Respiratoires et Réanimation Respiratoire, Hôpitaux de Brabois, CHU Nancy, France.
Marie
B
B
Tissier
S
S
Thivilier
C
C
Vignaud
J M
JM
Regent
D
D
Chabot
F
F
D000328:Adult; D005260:Female; D005350:Fibroma / Q000175:diagnosis*; D006801:Humans; D014134:Tracheal Neoplasms / Q000175:diagnosis*