title: Anaesthesiological and ventilatory precautions during cardiac surgery in Steinert's disease.
abstract: Myotonic dystrophia type I or Steinert's disease is a progressive multisystemic-inherited neuromuscular disease. Higher sensitivity to sedatives, anaesthetic, and neuromuscular blocking agents may result in cardiovascular and respiratory complications. We describe the anaesthesiological and ventilatory measures in a 43-year-old patient with Steinert's disease successfully undergoing cardiac surgery.
authors.affiliation: Department of Cardiothoracic Surgery, Erasmus MC, Rotterdam, The Netherlands. l.klompe@erasmusmc.nl
authors.forename: Lennart
authors.initials: L
authors.lastname: Klompe
authors.forename: Marcus
authors.initials: M
authors.lastname: Lancé
authors.forename: Dries
authors.initials: D
authors.lastname: van der Woerd
authors.forename: Thierry
authors.initials: T
authors.lastname: Scohy
authors.forename: Ad J J C
authors.initials: AJ
authors.lastname: Bogers
mesh_terms: D000328:Adult; D000768:Anesthesia, General; D013504:Cardiovascular Surgical Procedures; D006801:Humans; D008297:Male; D009223:Myotonic Dystrophy; D012086:Reoperation; D012121:Respiration, Artificial; D013771:Tetralogy of Fallot / Q000473:pathology / Q000601:surgery*