Pediatric intradural extramedullary synovial sarcoma: case report.
OBJECTIVE
The diagnosis of intradural synovial sarcoma has not been previously published. This report provides a summary of the literature on this tumor and on tumors arising in this location, as well as a description of this patient's clinical course.


METHODS
An 11-year-old girl presented with back pain and radiculopathy. A magnetic resonance imaging scan of the spine revealed a spinal intradural, extramedullary mass at L2-L4 and four additional nodules of enhancement.


METHODS
The mass was nearly totally resected. Radiation and chemotherapy were administered. Intracranial metastases became evident during treatment. The patient died of the disease 14 months after diagnosis.


CONCLUSIONS
The rapid progression of leptomeningeal metastasis despite maximal treatment demonstrates the aggressive nature of the tumor and the need for further study.
Greene
Stephanie
S
Department of Neurological Surgery, University of Washington School of Medicine, Children's Hospital and Regional Medical Center, Seattle, Washington, USA. Greene1hinz@pol.net
Hawkins
Douglas S
DS
Rutledge
Joe C
JC
Tsuchiya
Karen D
KD
Douglas
James
J
Ellenbogen
Richard G
RG
Avellino
Anthony M
AM
D002648:Child; D005260:Female; D006801:Humans; D008159:Lumbar Vertebrae / Q000473:pathology*; D008279:Magnetic Resonance Imaging; D013584:Sarcoma, Synovial / Q000473:pathology* / Q000628:therapy*