[Melkersson-Rosenthal syndrome. Report of five cases and review of the literature].
The goal of this work is to report five cases of Melkersson-Rosenthal syndrom with a literature review. It is a rare entity and is characterized in its complete presentation, by the association of reccurent orofacial swelling, peripheral facial palsy and plicated tongue. Incomplete forms are more frequent and more difficult to establish its diagnosis. This latter is based on major and minor clinical and histological critieria sorted in three levels. There is four forms of MRS. The pathogenesis of this syndrome is still unknown; treatment remains random. It is based on topical or systemic steroids with or without cheiloplastic procedure. We must think of MRS in presence of any recurrent peripheral facial palsy and/or chronic facial swelling.
Ghorbel
Imed Ben
IB
Service de Médecine Interne, Hôpital La Rabta, Tunis, Tunisie.
SioudDhrif
Asma
A
Lamloum
Mounir
M
Trabelsi
Salem
S
Habib Houman
Mohammed
M
D000293:Adolescent; D000328:Adult; D002675:Child, Preschool; D005260:Female; D006801:Humans; D008297:Male; D008556:Melkersson-Rosenthal Syndrome / Q000175:diagnosis*; D008875:Middle Aged