An unusual case of a highly progressive supratentorial capillary haemangioblastoma - histopathological considerations.
We describe a case of a rapidly progressive, sporadic, non-von Hippel-Lindau (VHL) disease associated supratentorial capillary haemangioblastoma. Despite the classical histopathological presentation consisting of stromal cells and abundant capillaries, the tumour showed an unfavourable clinical course.
Orakcioglu
B
B
Department of Neurosurgery, University Hospital Zurich, Zurich, Switzerland. berk.orakcioglu@med.uni-heidelberg.de
Sakowitz
O W
OW
Perren
A
A
Heppner
F L
FL
Yonekawa
Y
Y
D000328:Adult; D001253:Astrocytes / Q000378:metabolism / Q000473:pathology; D001254:Astrocytoma / Q000378:metabolism / Q000473:pathology; D014408:Biomarkers, Tumor / Q000032:analysis / Q000378:metabolism; D001921:Brain / Q000098:blood supply / Q000473:pathology / Q000503:physiopathology; D001932:Brain Neoplasms / Q000473:pathology* / Q000503:physiopathology / Q000628:therapy; D002196:Capillaries / Q000473:pathology* / Q000503:physiopathology; D003937:Diagnosis, Differential; D018450:Disease Progression; D004621:Embolization, Therapeutic; D005904:Glial Fibrillary Acidic Protein / Q000032:analysis / Q000378:metabolism; D005910:Glioma / Q000175:diagnosis; D018325:Hemangioblastoma / Q000473:pathology* / Q000503:physiopathology / Q000628:therapy; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D009361:Neoplasm Invasiveness / Q000473:pathology / Q000503:physiopathology; D011878:Radiotherapy; D017211:Treatment Failure
D014408:Biomarkers, Tumor; D005904:Glial Fibrillary Acidic Protein