Perivascular epithelioid cell tumor of the uterus: a case report.
A case of a perivascular epithelioid cell tumor (PEComa) arising in the uterus of a 35-year-old woman is presented. Imaging studies revealed a 5 cm well circumscribed mass in the uterine fundus. The tumor was composed of clear to faintly eosinophilic, epithelioid and spindled cells. Immunohistochemically, most tumour cells were strongly positive for HMB-45, smooth muscle actin and desmine, but negative for epithelial markers, S-100 Protein and neuroendocrine markers. Reevaluation of the patient for signs of tuberous sclerosis complex after the diagnosis gave negative results. At the most recent follow-up 4 months later there was no evidence of recurrence.
Rammeh Rommani
S
S
Department of Pathology, Charles Nicolle Hospital, Tunis, Tunisia. rammehs@yahoo.fr
Trabelsi
A
A
Attia
L
L
Msakni
I
I
Koubaa
A
A
Ben Jilani
S
S
Zermani
R
R
D000328:Adult; D005260:Female; D006801:Humans; D014594:Uterine Neoplasms / Q000473:pathology*