A spontaneously ruptured primitive neuroectodermal tumor/extraosseous Ewing's sarcoma of the kidney with renal vein tumor thrombus.
Primitive neuroectodermal tumor/extraosseous Ewing's sarcoma (PNET/EES) is a childhood disease rarely seen in adults. It is a soft tissue tumor, which is often observed in the paraspinal region and lower extremity. We report the case of a 32-year-old man who presented with sudden abdominal pain on the right upper quadrant that was radiated to the right flank. During the operation, a spontaneously ruptured right kidney mass was found. The histopathologic and immunohistochemical characteristics of the excised mass were consistent with PNET/EES. This is the first known reported case of spontaneously ruptured PNET/EES of the kidney with renal vein tumor thrombus. The clinical details and the management of this case are described.
Moustafellos
Panagiotis
P
Surgical Department, Athens Medical Centre, Athens, Greece.
Gourgiotis
Stavros
S
Athanasopoulos
George
G
Karagianni
Evangelia
E
Hadjiyannakis
Evangelos
E
D000328:Adult; D006801:Humans; D007680:Kidney Neoplasms / Q000150:complications*; D008297:Male; D009360:Neoplastic Cells, Circulating; D018242:Neuroectodermal Tumors, Primitive / Q000150:complications*; D012082:Renal Veins; D012422:Rupture, Spontaneous; D012512:Sarcoma, Ewing / Q000150:complications*