title: The placement of osseointegrated dental implants in a patient with type IV B osteogenesis imperfecta: a 9-year follow-up.
abstract: Osteogenesis imperfecta (OI) is a rare autosomal dominant connective tissue and metabolic disorder. Typically, patients with OI exhibit bone fragility, with the sclera, joints, skin, and tooth dentin being affected to varying degrees. Despite existing classifications, there is an extreme phenotypic variation within this population, and at times the mild forms of OI may be difficult to diagnose. Comprehensive management of the severe types of OI involves aggressive physical and surgical orthopaedic treatment to improve muscle structure and joint mobility. For those patients with associated dentinogenesis imperfecta (DI), early and definitive management can help prevent excessive tooth wear and sensitivity. A case of a late diagnosis of type IV OI with DI successfully treated with implant-supported dentures is reported. To date, 9 years after implant surgery and prosthetic loading, the patient continues to be clinically and radiographically normal.
authors.affiliation: Pediatric Dentistry, Westmead Hospital, Sydney, Australia. neetaprabhu@hotmail.com <neetaprabhu@hotmail.com>
authors.forename: Neeta
authors.initials: N
authors.lastname: Prabhu
authors.forename: Norton
authors.initials: N
authors.lastname: Duckmanton
authors.forename: Alastair R
authors.initials: AR
authors.lastname: Stevenson
authors.forename: Angus
authors.initials: A
authors.lastname: Cameron
mesh_terms: D000328:Adult; D003388:Cranial Fossa, Posterior / Q000601:surgery; D017742:Dental Care for Chronically Ill; D003758:Dental Implantation, Endosseous; D019094:Dental Prosthesis, Implant-Supported; D003811:Dentinogenesis Imperfecta / Q000209:etiology / Q000534:rehabilitation*; D005500:Follow-Up Studies; D020233:Gait Disorders, Neurologic / Q000209:etiology / Q000601:surgery; D006801:Humans; D008297:Male; D016348:Osseointegration; D010013:Osteogenesis Imperfecta / Q000150:complications*