[Spheno-orbital mesenchymal chondrosarcoma. A case report].
Mesenchymal chondrosarcoma is a highly malignant and extremely rare tumor of the orbit: only 18 cases have been reported to date. We report a case of spheno-orbital mesenchymal chondrosarcoma in a 36-year-old woman presented with a 4-month history of progressive left exophthalmia and temporal mass. A CT-scan of the orbit and MRI showed a spheno-orbital mass, with temporal fossa extension, fed by the internal maxillary artery visible on cerebral angiography. Surgery via a transcranial, left frontotemporozygomatic approach after selective embolization enabled subtotal removal. Definitive histologic examination revealed mesenchymal chondrosarcoma. Postoperatively, exophthalmia spectacularly regressed. We report our clinical findings and present a review of the literature.
Naama
O
O
Service de Neurochirurgie, Hôpital Militaire d'Instruction Mohammed V, Rabat, Morocco. oukacha_naama@caramail.com
Ajja
A
A
El Moustarchid
B
B
Albouzidi
A
A
Asri
A
A
Belhachmi
A
A
Akhaddar
A
A
Gazzaz
M
M
Kadiri
B
B
Labraimi
A
A
Boucetta
M
M
D000328:Adult; D001859:Bone Neoplasms / Q000000981:diagnostic imaging / Q000601:surgery*; D002813:Chondrosarcoma / Q000000981:diagnostic imaging / Q000532:radiotherapy / Q000601:surgery*; D003131:Combined Modality Therapy; D005094:Exophthalmos / Q000209:etiology; D005260:Female; D006801:Humans; D008279:Magnetic Resonance Imaging; D011878:Radiotherapy / Q000379:methods; D012886:Skull / Q000000981:diagnostic imaging / Q000601:surgery*; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome