Intra-abdominal desmoplastic small round cell tumor.
Intra-abdominal desmoplastic small round cell tumor (IDSRCT) is a unique, highly aggressive neoplasm that chiefly affects male adolescents and young adults and most frequently presents as a large abdominal mass with widespread peritoneal involvement at the time of diagnosis. We present two cases of IDSRCT in a young male and a female. Both typically presented with diffuse peritoneal involvement.
Zeeshan-ud-din
Department of Pathology and Microbiology, The Aga Khan University, Karachi.
Yaqoob
Nausheen
N
Pishoroi
Turab
T
Rafique
Muhammad Zafar
MZ
Kamran
Ali
A
D000328:Adult; D018288:Carcinoma, Small Cell / Q000175:diagnosis* / Q000473:pathology; D005260:Female; D006801:Humans; D007150:Immunohistochemistry; D008297:Male; D009852:Omentum / Q000473:pathology; D010534:Peritoneal Neoplasms / Q000175:diagnosis* / Q000473:pathology