title: [Spheno-orbital mesenchymal chondrosarcoma. A case report].
abstract: Mesenchymal chondrosarcoma is a highly malignant and extremely rare tumor of the orbit: only 18 cases have been reported to date. We report a case of spheno-orbital mesenchymal chondrosarcoma in a 36-year-old woman presented with a 4-month history of progressive left exophthalmia and temporal mass. A CT-scan of the orbit and MRI showed a spheno-orbital mass, with temporal fossa extension, fed by the internal maxillary artery visible on cerebral angiography. Surgery via a transcranial, left frontotemporozygomatic approach after selective embolization enabled subtotal removal. Definitive histologic examination revealed mesenchymal chondrosarcoma. Postoperatively, exophthalmia spectacularly regressed. We report our clinical findings and present a review of the literature.
authors.affiliation: Service de Neurochirurgie, Hôpital Militaire d'Instruction Mohammed V, Rabat, Morocco. oukacha_naama@caramail.com
authors.forename: O
authors.initials: O
authors.lastname: Naama
authors.forename: A
authors.initials: A
authors.lastname: Ajja
authors.forename: B
authors.initials: B
authors.lastname: El Moustarchid
authors.forename: A
authors.initials: A
authors.lastname: Albouzidi
authors.forename: A
authors.initials: A
authors.lastname: Asri
authors.forename: A
authors.initials: A
authors.lastname: Belhachmi
authors.forename: A
authors.initials: A
authors.lastname: Akhaddar
authors.forename: M
authors.initials: M
authors.lastname: Gazzaz
authors.forename: B
authors.initials: B
authors.lastname: Kadiri
authors.forename: A
authors.initials: A
authors.lastname: Labraimi
authors.forename: M
authors.initials: M
authors.lastname: Boucetta
mesh_terms: D000328:Adult; D001859:Bone Neoplasms / Q000000981:diagnostic imaging / Q000601:surgery*; D002813:Chondrosarcoma / Q000000981:diagnostic imaging / Q000532:radiotherapy / Q000601:surgery*; D003131:Combined Modality Therapy; D005094:Exophthalmos / Q000209:etiology; D005260:Female; D006801:Humans; D008279:Magnetic Resonance Imaging; D011878:Radiotherapy / Q000379:methods; D012886:Skull / Q000000981:diagnostic imaging / Q000601:surgery*; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome