Congenital pulmonary vein stenosis beyond childhood.
We report a case of anomalous connection of pulmonary veins with insertional stenoses causing undiagnosed severe pulmonary hypertension in a 37-year-old woman. We report the use of non-invasive diagnostic investigations in making the diagnosis, and the apparent cure of this rare condition with resolution of right heart failure following surgical treatment.
Kelly
Damian J
DJ
Brodison
Adrian
A
Millner
Russell W
RW
Goode
Grahame K
GK
D000328:Adult; D002315:Cardiopulmonary Bypass / Q000379:methods; D018450:Disease Progression; D004417:Dyspnea / Q000175:diagnosis / Q000209:etiology; D017548:Echocardiography, Transesophageal; D005260:Female; D005500:Follow-Up Studies; D006330:Heart Defects, Congenital / Q000175:diagnosis* / Q000601:surgery; D006801:Humans; D010690:Phlebography; D011666:Pulmonary Valve Stenosis / Q000151:congenital* / Q000175:diagnosis / Q000601:surgery; D012121:Respiration, Artificial / Q000379:methods; D012131:Respiratory Insufficiency / Q000175:diagnosis* / Q000628:therapy; D018570:Risk Assessment; D012720:Severity of Illness Index; D016896:Treatment Outcome; D014656:Vascular Surgical Procedures / Q000379:methods*