Video-assisted thoracic surgery for pneumothorax in LAM.
Spontaneous pneumothorax is one of the more common presentations of lymphangioleiomyomatosis; however, recurrences are common which can be challenging to manage particularly in bilateral pneumothorax. We present a case of recurrent bilateral spontaneous pneumothorax associated with lymphangioleiomyomatosis, diagnosed intra-operatively, and confirmed by the resected lung specimen. Video-assisted thoracic surgery bullectomy and mechanical as well as talc pleurodesis was required to prevent further recurrences. The case discusses the unusual clinical course, radiological, operative and pathologic findings of the disease, and management difficulties that are distinct from other causes of spontaneous pneumothorax.
Garzon
Juan C
JC
Division of Cardiothoracic Surgery, Prince of Wales Hospital, The Chinese University of Hong Kong, Hong Kong SAR, China.
Ng
Calvin S H
CS
Lee
Tak Wai
TW
Yim
Anthony P C
AP
D000328:Adult; D018207:Angiomyolipoma / Q000473:pathology; D005260:Female; D006801:Humans; D007680:Kidney Neoplasms / Q000556:secondary; D008175:Lung Neoplasms / Q000473:pathology* / Q000601:surgery; D018192:Lymphangioleiomyomatosis / Q000473:pathology* / Q000601:surgery; D018700:Pleurodesis; D011030:Pneumothorax / Q000209:etiology / Q000601:surgery*; D012008:Recurrence; D012086:Reoperation; D013627:Talc / Q000008:administration & dosage; D020775:Thoracic Surgery, Video-Assisted
D013627:Talc