Mauriac syndrome in a 3-year-old boy.
OBJECTIVE
To report a case of Mauriac syndrome in a young child with poorly controlled type 1 diabetes mellitus.


METHODS
We describe the typical features of Mauriac syndrome and review the clinical, laboratory, and ultrasound findings and follow-up results in our current patient.


RESULTS
Hepatomegaly, growth impairment, and cushingoid features characterize Mauriac syndrome. Most frequently, it is seen in adolescents and young adults with a history of poor glycemic control. In our current patient, a 3-year-old boy with type 1 diabetes mellitus of 2 years' duration, Mauriac syndrome developed in the context of a disrupted social environment. His liver enzyme derangement, hepatomegaly, and growth improved once euglycemia was achieved.


CONCLUSIONS
Although Mauriac syndrome is currently uncommon, close monitoring of children with type 1 diabetes is important to maintain optimal glycemic control and prevent such an occurrence.
Mahesh
Shefali
S
Department of Pediatric Nephrology, Montefiore Medical Center, Bronx, New York, USA.
Karp
Robert J
RJ
Castells
Salvador
S
Quintos
Jose Bernardo Q
JB
D002675:Child, Preschool; D003922:Diabetes Mellitus, Type 1 / Q000175:diagnosis* / Q000188:drug therapy* / Q000503:physiopathology; D006130:Growth Disorders / Q000175:diagnosis* / Q000503:physiopathology; D006529:Hepatomegaly / Q000175:diagnosis* / Q000503:physiopathology; D006801:Humans; D006943:Hyperglycemia / Q000175:diagnosis / Q000188:drug therapy / Q000503:physiopathology; D007004:Hypoglycemic Agents / Q000627:therapeutic use*; D007328:Insulin / Q000627:therapeutic use*; D008297:Male; D013577:Syndrome
D007004:Hypoglycemic Agents; D007328:Insulin