Alveolar capillary dysplasia presenting as pneumothorax: a case report and review of literature.
Alveolar capillary dysplasia, although rare, is a universally fatal form of persistent pulmonary hypertension of the newborn. We report a case of a newborn male baby who developed respiratory distress and pneumothorax 11 h after an uncomplicated delivery. He deteriorated despite full ventilatory support and extracorporeal membrane oxygenation (ECMO). Open lung biopsy provided a diagnosis of alveolar capillary dysplasia and decision was made to withdraw treatment.
Roy
Pankaj G
PG
Department of Paediatric Surgery, John Radcliffe hospital, Oxford OX3 9DU, UK. pankajgroy@yahoo.co.uk
Patel
Prerna
P
Vayalakkad
Anitha
A
Bowker
Colene
C
Lakhoo
Kokila
K
D001706:Biopsy; D002196:Capillaries / Q000002:abnormalities / Q000473:pathology*; D003937:Diagnosis, Differential; D015199:Extracorporeal Membrane Oxygenation; D017809:Fatal Outcome; D006801:Humans; D007231:Infant, Newborn; D008168:Lung / Q000098:blood supply / Q000473:pathology; D008297:Male; D010547:Persistent Fetal Circulation Syndrome / Q000150:complications / Q000175:diagnosis* / Q000628:therapy; D011030:Pneumothorax / Q000175:diagnosis* / Q000209:etiology; D011650:Pulmonary Alveoli / Q000098:blood supply* / Q000473:pathology*; D035583:Rare Diseases; D012121:Respiration, Artificial; D012127:Respiratory Distress Syndrome, Newborn / Q000209:etiology / Q000628:therapy