Malignant triton tumour of the anterior mediastinum as incidental finding.
A rare case of malignant peripheral nerve sheath tumour with rhabdomyoblastic differentiation (malignant triton tumour) of the anterior mediastinum in a 30-year-old male is reported. The tumour was an incidental finding during the diagnostic work-up following a motor vehicle accident. The patient underwent median sternotomy with a tumour resection performed. Local relapse was suspected one month later, as per the chest CT-scan, and post-operative chemoradiation was applied, which produced a response. Twelve months later the patient is doing well while radiological findings remain invariable. Localization of a triton tumour in the anterior mediastinum is extremely rare, adjuvant treatment is necessary, recurrence frequently occurs and the prognosis is dismal.
Zisis
C
C
Thoracic Surgery Department, Evangelismos Hospital, Athens, Greece. chzisis@hol.gr
Fragoulis
S
S
Rontogianni
D
D
Stratakos
G
G
Bellenis
I
I
D000328:Adult; D006801:Humans; D033162:Incidental Findings; D008297:Male; D008479:Mediastinal Neoplasms / Q000175:diagnosis* / Q000473:pathology / Q000601:surgery; D009364:Neoplasm Recurrence, Local; D018317:Nerve Sheath Neoplasms / Q000175:diagnosis* / Q000473:pathology / Q000601:surgery; D013249:Sternum / Q000000981:diagnostic imaging / Q000473:pathology / Q000601:surgery; D019616:Thoracic Surgical Procedures; D014057:Tomography, X-Ray Computed