Pulmonary hypertension alters natural history of anomalous left coronary artery.
A girl who was diagnosed at 8 months old with anomalous left coronary artery from the pulmonary artery and was subsequently lost to follow-up, presented at the age of 11 years with congestive heart failure and severe mitral regurgitation with supra-systemic pulmonary artery pressure. With progressive mitral regurgitation, coronary steal is reduced by the rising pulmonary artery pressure, and patients present late with severe valvular cardiomyopathy.
Akbari
Jayesh
J
Division of Cardiovascular & Thoracic Surgery, Sree Chitra Tirunal Institute for Medical Sciences and Technology, Trivandrum, Kerala, India.
Theodore
Sanjay
S
Krishnamanohar
Soman R
SR
Neelakandhan
Kurur S
KS
D002648:Child; D003330:Coronary Vessel Anomalies / Q000150:complications* / Q000601:surgery; D018450:Disease Progression; D005260:Female; D006333:Heart Failure / Q000209:etiology* / Q000601:surgery; D006801:Humans; D006976:Hypertension, Pulmonary / Q000209:etiology* / Q000601:surgery; D008944:Mitral Valve Insufficiency / Q000209:etiology / Q000601:surgery; D011654:Pulmonary Edema / Q000209:etiology