title: Role of implantable cardioverter defibrillator therapy in patients with long QT syndrome.
abstract: Long QT syndrome (LQTS) is one of several primary electrical disorders or hereditary arrhythmia syndromes along with the short QT syndrome, Brugada syndrome, and catecholaminergic polymorphic ventricular tachycardia. Since its initial recognition in 1957 by Jervell and Lange-Nielsen (Am Heart J. 1957;54:59-68), LQTS has been intimately associated with risk for sudden cardiac death. The implantable defibrillator was developed by Morowski et al (N Engl J Med. 1980;303:322-4) as a treatment to prevent sudden cardiac death. Consequently, implanted cardioverter-defibrillator therapy deserves serious consideration as an important therapy for LQTS.
authors: Cardiology Division, Department of Medicine, University of Rochester Medical Center, Rochester, NY 14642, USA. James_Daubert@urmc.rochester.edu <James_Daubert@urmc.rochester.edu>
authors: James P
authors: JP
authors: Daubert
authors: Wojciech
authors: W
authors: Zareba
authors: Spencer Z
authors: SZ
authors: Rosero
authors: Adam
authors: A
authors: Budzikowski
authors: Jennifer L
authors: JL
authors: Robinson
authors: Arthur J
authors: AJ
authors: Moss
mesh_terms: D017147:Defibrillators, Implantable / Q000009:adverse effects; D006801:Humans; D008133:Long QT Syndrome / Q000188:drug therapy / Q000628:therapy*