[Heart failure and cardiomyopathies: a case report].
Isolated noncompaction of left ventricular myocardium is a rare congenital heart disease, characterized by an excessive prominence of trabecular meshwork, spaced out by deep intertrabecular recesses, consequent to the arrest of the normal myocardial embryogenesis. Although there are numerous descriptions, the pathophysiological effects of the structural alterations, like the clinical spectrum and the evolution of the disease, are not fully clarified. In this paper we evaluated the natural history of the disease, the family incidence and the alterations of the systolic and diastolic function. An interesting case report is described concerning a patient affected by noncompaction and atrial fibrillation.
Fazio
Giovanni
G
Divisione di Cardiologia, Università degli Studi, Palermo. Giovanni.fazio-aaaa@poste.it
Sutera
Loredana
L
Vernuccio
Federica
F
Fazio
Marco
M
Vernuccio
Daniela
D
Pizzuto
Caterina
C
Di Gesaro
Gabriele
G
Cascio
Caterina
C
Novo
Salvatore
S
D000328:Adult; D001281:Atrial Fibrillation / Q000188:drug therapy / Q000209:etiology* / Q000601:surgery / Q000628:therapy; D017115:Catheter Ablation; D004452:Echocardiography; D004562:Electrocardiography; D005500:Follow-Up Studies; D006330:Heart Defects, Congenital / Q000150:complications / Q000175:diagnosis; D006333:Heart Failure / Q000188:drug therapy / Q000209:etiology*; D006352:Heart Ventricles / Q000002:abnormalities*; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D010138:Pacemaker, Artificial; D013997:Time Factors; D016896:Treatment Outcome