Surgical treatment of scoliosis associated with central core disease: minimizing the effects of malignant hyperthermia with provocation tests.
We report the case of a 7-year-old boy with thoracolumbar scoliosis and central core disease who had a history of malignant hyperthermia. He had scoliosis with Cobb's angle deteriorating to 67 degrees (thoracic) and 59 degrees (lumbar). A provocation test of general anesthesia was performed to confirm no hyperthermic reaction. Then, he underwent surgical correction by a posterior approach. The thoracic curve was reduced to 38 degrees and the lumbar curve to 42 degrees . He has been followed up for 2 years without any complications. This is the first report with a detailed description of perioperative management on surgical treatment of scoliosis associated with central core disease.
Miyamoto
Kei
K
Department of Orthopaedic Surgery, Gifu University Graduate School of Medicine, Gifu City, Gifu, Japan.
Shimizu
Katsuji
K
Matsumoto
Shigemi
S
Sumida
Hisashi
H
Iida
Hiroki
H
Hosoe
Hideo
H
D002648:Child; D019937:Diagnostic Techniques and Procedures; D006801:Humans; D008297:Male; D008305:Malignant Hyperthermia / Q000175:diagnosis* / Q000517:prevention & control*; D020512:Myopathy, Central Core / Q000150:complications*; D011300:Preoperative Care; D012600:Scoliosis / Q000209:etiology* / Q000601:surgery*