[Pulmonary blastoma in adults].
Pneumoblastoma (PB) is a rare, malignant, primary, pulmonary tumour, of young adults. Its discovery is fortuitous in asymptomatic patients. It is a well-delimited, homogeneous lesion in the lung periphery. Histologically, its structure looks like a normal fetal lung. The surgical resection is the treatment of choice. The radiotherapy is an empirical palliative treatment to relieve dyspnea when other treatments failed. The prognosis is bad: 16% survive 5 years and 8% beyond 10 years, all treatments included. Metastases could appear in the liver, the brain and the bone.
Terrettaz
Emmanuel
E
Centre valaisan de pneumologie, 3963 Crans-Montana.
Frey
Jean-Georges
JG
Chavaillaz
Olivier
O
D000328:Adult; D017024:Chemotherapy, Adjuvant; D006801:Humans; D008175:Lung Neoplasms / Q000175:diagnosis / Q000401:mortality / Q000628:therapy; D008297:Male; D011379:Prognosis; D018202:Pulmonary Blastoma / Q000175:diagnosis / Q000401:mortality / Q000628:therapy; D018714:Radiotherapy, Adjuvant; D016019:Survival Analysis; D013557:Switzerland / Q000453:epidemiology