Special airway concerns in patients with mucopolysaccharidoses.
The mucopolysaccharidoses are comprised of hereditary disorders joined by errant degradation of mucopolysaccharides. The relatively infrequent opportunity to care for these patients is evidenced by a fairly small number of case reports and anecdotal information. Though lifespan is increasing, onset of respiratory pathology or involvement remains portentous. We present two cases that punctuate the need for insightful decision making while managing the airway for these patients.
Steven Sims
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Chicago Institute for Voice Care, University of Illinois at Chicago, IL 60612, USA. voicecare@uic.edu
Kempiners
James J
JJ
D000293:Adolescent; D000328:Adult; D000402:Airway Obstruction / Q000209:etiology* / Q000628:therapy; D003937:Diagnosis, Differential; D017809:Fatal Outcome; D006801:Humans; D007442:Intubation, Intratracheal; D008297:Male; D016532:Mucopolysaccharidosis II / Q000150:complications*; D009085:Mucopolysaccharidosis IV / Q000150:complications*; D014139:Tracheostomy / Q000379:methods*; D016896:Treatment Outcome