Bacteria-associated haemophagocytic syndrome and septic pulmonary embolism caused by Burkholderia cepacia complex in a woman with chronic granulomatous disease.
Chronic granulomatous disease (CGD) is a primary immunodeficiency characterized by recurrent infections with certain types of bacteria and fungi. Presented herein is the case of a 29 year old woman with CGD who suffered from bacteria-associated haemophagocytic syndrome and a septic pulmonary embolism following a uterine infection and sepsis, caused by Burkholderia cepacia complex.
Hisano
Michi
M
Department of Perinatology, National Center for Child Health and Development, Tokyo, Japan.
Sugawara
Kana
K
Department of Perinatology, National Center for Child Health and Development, Tokyo, Japan.
Tatsuzawa
Osamu
O
Department of Medical Specialties, Division of Infectious Disease and Rheumatology, National Center for Child Health and Development, Tokyo, Japan.
Kitagawa
Michihiro
M
Department of Perinatology, National Center for Child Health and Development, Tokyo, Japan.
Murashima
Atsuko
A
Department of Perinatology, National Center for Child Health and Development, Tokyo, Japan.
Yamaguchi
Koushi
K
Department of Perinatology, National Center for Child Health and Development, Tokyo, Japan.
D000328:Adult; D000900:Anti-Bacterial Agents / Q000627:therapeutic use; D000935:Antifungal Agents / Q000627:therapeutic use; D019121:Burkholderia Infections / Q000150:complications* / Q000188:drug therapy / Q000382:microbiology; D042602:Burkholderia cepacia complex / Q000302:isolation & purification*; D054714:Echinocandins; D005260:Female; D006105:Granulomatous Disease, Chronic / Q000150:complications*; D006801:Humans; D055666:Lipopeptides; D008074:Lipoproteins / Q000627:therapeutic use; D051359:Lymphohistiocytosis, Hemophagocytic / Q000188:drug therapy / Q000382:microbiology*; D000077551:Micafungin; D008911:Minocycline / Q000627:therapeutic use; D010456:Peptides, Cyclic / Q000627:therapeutic use; D011655:Pulmonary Embolism / Q000382:microbiology*; D018805:Sepsis / Q000150:complications / Q000188:drug therapy / Q000382:microbiology*; D015662:Trimethoprim, Sulfamethoxazole Drug Combination / Q000627:therapeutic use
D000900:Anti-Bacterial Agents; D000935:Antifungal Agents; D054714:Echinocandins; D055666:Lipopeptides; D008074:Lipoproteins; D010456:Peptides, Cyclic; D015662:Trimethoprim, Sulfamethoxazole Drug Combination; D008911:Minocycline; D000077551:Micafungin