Hemolytic anemia secondary to modified blalock-taussig shunt.
The Norwood procedure with a modified Blalock-Taussig shunt (MBTS) is the first of the three-stage surgical palliation for infants with hypoplastic left heart syndrome. We report a patient with schistocytic hemolytic anemia that developed following a right MBTS with a Gore-Tex graft. Hemolysis associated with a MBTS has not been previously reported in the literature. Multiple packed red blood cell transfusions were required due to desaturation and hypoxemia. Hemi-Fontan procedure was performed early for chronic anemia. Hemolysis resolved post operatively even though the patient subsequently required a Gore-Tex central shunt for persistent cyanosis.
Ryerson
Lindsay M
LM
Department of Pediatrics, University of Michigan, Ann Arbor, ML 48109, USA. lrverson@med.umich.edu
Wechsler
Stephanie Burns
SB
Ohye
Richard G
RG
D000714:Anastomosis, Surgical / Q000009:adverse effects*; D000743:Anemia, Hemolytic / Q000209:etiology*; D001024:Aortic Valve Stenosis / Q000601:surgery; D001803:Blood Transfusion; D018729:Fontan Procedure / Q000379:methods*; D006330:Heart Defects, Congenital / Q000628:therapy*; D006801:Humans; D018636:Hypoplastic Left Heart Syndrome / Q000601:surgery*; D007231:Infant, Newborn; D008297:Male; D008946:Mitral Valve Stenosis / Q000601:surgery