Binasal visual field defects from simultaneous bilateral retinal infarctions in sickle cell disease.
OBJECTIVE
To report a case of retinal occlusive disease producing binasal visual field defects in a patient with sickle cell (SC) disease.


METHODS
Retrospective case report.


METHODS
A 21-year-old man with SC disease presented with binasal field defects and 20/20 acuity in each eye.


RESULTS
Initial ophthalmoscopy and fluorescein angiography revealed no abnormalities. Optical coherence tomography (OCT) demonstrated bilateral temporal inner retinal hyperreflectivity, and multifocal electroretinography (mfERG) confirmed retinal dysfunction. Several weeks later, ophthalmoscopy and angiography demonstrated macular arteriolar occlusive disease.


CONCLUSIONS
Simultaneous bilateral macular occlusive events are uncommon in patients particularly with SC disease. Although the binasal field defects raised the suspicion of a process affecting the optic nerves, the OCT and mfERG proved essential in diagnosing retinal rather than optic nerve disease.
Cusick
Michael
M
The Wilmer Eye Institute, Johns Hopkins University School of Medicine, Baltimore, Maryland 21287, USA.
Toma
Hassanain S
HS
Hwang
Thomas S
TS
Brown
Justin C
JC
Miller
Neil R
NR
Adams
N A
NA
D000328:Adult; D001160:Arterioles / Q000473:pathology; D004596:Electroretinography; D005451:Fluorescein Angiography; D007839:Functional Laterality; D006450:Hemoglobin SC Disease / Q000150:complications*; D006801:Humans; D007238:Infarction / Q000175:diagnosis / Q000209:etiology*; D008297:Male; D009887:Ophthalmoscopy; D015356:Retinal Artery Occlusion / Q000175:diagnosis / Q000209:etiology*; D012171:Retinal Vessels / Q000473:pathology*; D012189:Retrospective Studies; D041623:Tomography, Optical Coherence; D014786:Vision Disorders / Q000175:diagnosis / Q000209:etiology*; D014792:Visual Acuity; D058609:Visual Field Tests; D014794:Visual Fields