title: Parry Romberg syndrome and linear scleroderma in coup de sabre mimicking Rasmussen encephalitis.
abstract: We present one patient with Parry Romberg syndrome and another with linear scleroderma in coup de sabre, with focal neurologic deficits and intractable seizures arising from the hemisphere ipsilateral to the cutaneous lesion. Brain MRI showed progressive hemispheric atrophy. Pathology after functional hemispherectomy showed chronic inflammatory features suggestive of Rasmussen encephalitis.
authors: Department of Neurology, Hospital Clínic, Barcelona, Spain. mcarreno@clinic.ub.es
authors: M
authors: M
authors: Carreño
authors: A
authors: A
authors: Donaire
authors: M I
authors: MI
authors: Barceló
authors: J
authors: J
authors: Rumià
authors: M
authors: M
authors: Falip
authors: R
authors: R
authors: Agudo
authors: N
authors: N
authors: Bargalló
authors: X
authors: X
authors: Setoain
authors: T
authors: T
authors: Boget
authors: A
authors: A
authors: Raspall
authors: L
authors: L
authors: Pintor
authors: T
authors: T
authors: Ribalta
mesh_terms: D000328:Adult; D017668:Age of Onset; D001284:Atrophy / Q000276:immunology / Q000473:pathology / Q000503:physiopathology; D001327:Autoimmune Diseases / Q000503:physiopathology; D002648:Child; D004660:Encephalitis / Q000150:complications* / Q000276:immunology / Q000503:physiopathology; D004828:Epilepsies, Partial / Q000150:complications / Q000276:immunology / Q000503:physiopathology; D004827:Epilepsy / Q000150:complications* / Q000276:immunology / Q000503:physiopathology; D005150:Facial Hemiatrophy / Q000150:complications* / Q000276:immunology / Q000503:physiopathology; D005260:Female; D038421:Hemispherectomy; D006801:Humans; D007166:Immunosuppressive Agents / Q000627:therapeutic use; D008279:Magnetic Resonance Imaging; D008297:Male; D045745:Scleroderma, Limited / Q000150:complications* / Q000276:immunology / Q000503:physiopathology; D013687:Telencephalon / Q000276:immunology / Q000473:pathology / Q000503:physiopathology*; D016896:Treatment Outcome
chemical_list: D007166:Immunosuppressive Agents