Pulmonary hypertension in neurofibromatosis.
Two cases of severe pulmonary arterial hypertension in patients with neurofibromatosis are reported. The published research is reviewed. In conclusion, it is suggested that the association between these conditions be recognized in the classification of pulmonary hypertension.
Engel
Peter J
PJ
The Ohio Heart and Vascular Center, Cincinnati, Ohio, USA.
Baughman
Robert P
RP
Menon
Santosh G
SG
Kereiakes
Dean J
DJ
Taylor
Lisa
L
Scott
Mark
M
D000368:Aged; D019080:Cafe-au-Lait Spots / Q000473:pathology; D005260:Female; D006801:Humans; D006976:Hypertension, Pulmonary / Q000209:etiology*; D008875:Middle Aged; D009456:Neurofibromatosis 1 / Q000150:complications* / Q000473:pathology