Sotos syndrome: a case report.
Sotos Syndrome is a genetic condition characterized by accelerated bone development, abnormal craniofacial morphology and psychomotor developmental retardation. The behavioral problems usually associated with the syndrome include poor social skills, anxiety and/or irritability. Oral findings include prognathism and a high-arched palate with premature eruption of the teeth. Delayed psychomotor development increases the risk for caries. A personalized preventive treatment plan with close supervision of the patient's oral health care is required. This paper documents a child diagnosed with Sotos Syndrome and describes the primary clinical features, the disease-specific craniofacial, oral and dental findings, and dental care management of this patient.
Gomes-Silva
Jaciara Miranda
JM
Department of Pediatric Clinics, Preventive and Social Dentistry School of Dentistry of Ribeirão Preto, University of São Paulo, Ribeirão Preto, SP, Brazil.
Ruviére
Denise Belucio
DB
Segatto
Regina Aparecida Saiani
RA
de Queiroz
Alexandra Mussolino
AM
de Freitas
Aldevina Campos
AC
D002675:Child, Preschool; D019465:Craniofacial Abnormalities; D017742:Dental Care for Chronically Ill; D003731:Dental Caries / Q000628:therapy; D003773:Dental Plaque / Q000628:therapy; D002658:Developmental Disabilities; D019066:Facies; D005260:Female; D005877:Gigantism; D005891:Gingivitis / Q000628:therapy; D006801:Humans; D013577:Syndrome