Late-onset monomelic amyotrophy in a Caucasian woman.
We describe a 53-year-old Caucasian woman with a 19-year history of an evolving amyotrophy confined to her dominant right arm and hand. Although this atypical case of a late-onset monomelic amyotrophy in some respects mimics Hirayama disease or O'Sullivan-McLeod syndrome, it does not conform precisely with either of those disorders. We compare this individual's difficulties and clinical temporal profile to other disorders considered in the differential diagnoses with regard to her evolving clinical setting.
Patel
Dharmesh R
DR
Department of Neurology, Lahey Clinic, 41 Mall Road, Burlington, Massachusetts 01805, USA.
Knepper
Laurie
L
Jones
H Royden
HR
D017668:Age of Onset; D001132:Arm / Q000473:pathology / Q000503:physiopathology*; D003937:Diagnosis, Differential; D018450:Disease Progression; D004568:Electrodiagnosis; D005260:Female; D007839:Functional Laterality; D006801:Humans; D016756:Immunoglobulins, Intravenous / Q000627:therapeutic use; D008875:Middle Aged; D016472:Motor Neuron Disease / Q000175:diagnosis* / Q000208:ethnology / Q000503:physiopathology; D009046:Motor Neurons; D018482:Muscle, Skeletal / Q000473:pathology / Q000503:physiopathology*; D009133:Muscular Atrophy / Q000175:diagnosis* / Q000208:ethnology / Q000503:physiopathology; D009431:Neural Conduction; D010525:Peripheral Nerves / Q000503:physiopathology; D010523:Peripheral Nervous System Diseases / Q000175:diagnosis* / Q000208:ethnology / Q000503:physiopathology; D016896:Treatment Outcome; D044465:White People
D016756:Immunoglobulins, Intravenous