Brooke-Spiegler syndrome.
A 46-year-old woman with Brooke-Spiegler syndrome has multiple cutaneous adnexal neoplasms on her face and scalp. One of the lesions has concurrent features of cylindroma, trichoepithelioma, and spiradenoma in the same specimen. Etiology, clinical features, malignant transformation, and treatment modalities for Brooke-Spiegler syndrome are reviewed.
Kim
Carolyn
C
New York University Department of Dermatology, USA.
Kovich
Olympia I
OI
Dosik
Jonathan
J
D003528:Carcinoma, Adenoid Cystic / Q000473:pathology*; D003937:Diagnosis, Differential; D005145:Face; D005260:Female; D006801:Humans; D008875:Middle Aged; D012535:Scalp; D012878:Skin Neoplasms / Q000473:pathology*; D013577:Syndrome