Embryonal rhabdomyosarcoma of the temporal bone.
The most common soft-tissue sarcoma in infants and children is rhabdomyosarcoma. The head and neck is the most common site of involvement; temporal bone involvement has been seen in about 7% of reported cases. Multimodality therapy--surgery, multiagent chemotherapy, and radiotherapy-yields sufficiently good results. The author reports a case of embryonal rhabdomyosarcoma of the temporal bone with cranial nerve palsies and extension into the parapharyngeal space in a 4-year-old boy. Despite surgery and chemotherapy, the patient died of his disease within 3 months of presentation.
Viswanatha
Borlingegowda
B
ENT Department, Victoria Hospital, Bangalore Medical College, Bangalore, Karnataka, India. drbviswanatha@yahoo.co.in
D002675:Child, Preschool; D003131:Combined Modality Therapy; D003937:Diagnosis, Differential; D004424:Ear Canal / Q000473:pathology; D004428:Ear Neoplasms / Q000175:diagnosis* / Q000473:pathology / Q000628:therapy; D004432:Ear, Middle / Q000473:pathology; D005158:Facial Paralysis / Q000209:etiology*; D017809:Fatal Outcome; D006801:Humans; D008297:Male; D008416:Mastoid / Q000473:pathology; D009364:Neoplasm Recurrence, Local / Q000175:diagnosis / Q000473:pathology / Q000628:therapy; D009886:Ophthalmoplegia / Q000209:etiology*; D010166:Palliative Care; D010610:Pharyngeal Neoplasms / Q000175:diagnosis / Q000473:pathology / Q000628:therapy; D018233:Rhabdomyosarcoma, Embryonal / Q000175:diagnosis* / Q000473:pathology / Q000628:therapy; D012888:Skull Neoplasms / Q000175:diagnosis* / Q000473:pathology / Q000628:therapy; D013701:Temporal Bone / Q000473:pathology