ACTH-independent macronodular adrenal hyperplasia: imaging findings of a rare condition : A case report.
Endogenous Cushing's syndrome is a relatively rare disease. Most cases being ACTH-dependent, ACTH-independent Cushing's syndrome (AICS) is an even rarer condition [15%-20%]. In more than 95% cases the cause of AICS is unilateral adrenal enlargement caused by adenoma or carcinoma. Bilateral adrenal disease is caused by primary pigmented nodular adrenal dysplasia (PPNAD) and ACTH-independent macro nodular hyperplasia (AIMAH). Only few case reports of the latter condition exist in the radiology literature, PPNAD being the commoner of two as the cause for AICS.
Verma
Ashish
A
Department of Radio Diagnosis, Sanjay Gandhi Post Graduate Institute of Medical Sciences, Rae Bareily Road, Lucknow, 226 014, Uttar Pradesh, India.
Mohan
Suyash
S
Gupta
Archna
A
D000311:Adrenal Glands / Q000000981:diagnostic imaging* / Q000473:pathology* / Q000601:surgery; D000324:Adrenocorticotropic Hormone; D003287:Contrast Media / Q000008:administration & dosage; D003480:Cushing Syndrome / Q000175:diagnosis* / Q000601:surgery; D003920:Diabetes Mellitus; D006801:Humans; D007008:Hypokalemia / Q000209:etiology; D008279:Magnetic Resonance Imaging; D008297:Male; D008875:Middle Aged; D011856:Radiographic Image Enhancement; D035583:Rare Diseases; D014057:Tomography, X-Ray Computed
D003287:Contrast Media; D000324:Adrenocorticotropic Hormone