Anetodermic mastocytosis: response to PUVA therapy.
Mastocytosis is a group of disorders characterized by the accumulation of mast cells in different tissues and organs. The skin is the most frequently involved organ (90% of cases) where mastocytosis may show a heterogenic clinical expression. Anetodermic lesions are an unusual clinical presentation of mastocytosis. We report a case of anetodermic mastocytosis in a 26-year-old man, with sparse lesions and a benign course. PUVA therapy obtained excellent results in this case. Darier's sign should be investigated in patients with anetodermic lesions of unclear origin in order to exclude cutaneous mastocytosis.
Del Pozo
Jesús
J
Department of Dermatology, Hospital Juan Canalejo, La Coruña, Spain. del_pozo@canalejo.org
Pimentel
María Teresa Yebra
MT
Paradela
Sabela
S
Almagro
Manuel
M
Martínez
Walter
W
Fonseca
Eduardo
E
D000328:Adult; D003937:Diagnosis, Differential; D006801:Humans; D008297:Male; D034701:Mastocytosis, Cutaneous / Q000175:diagnosis* / Q000188:drug therapy* / Q000473:pathology; D011701:PUVA Therapy