Surgical repair of coronary sinus orifice atresia with persistent left superior vena cava in heterotaxia.
A 6-month-old boy was diagnosed with coronary sinus orifice atresia, double-outlet right ventricle, complete atrioventricular septal defect, pulmonary stenosis, and moderate common atrioventricular valve regurgitation associated with heterotaxy syndrome. Cardiac venous flow drained through a persistent left superior vena cava. We decided to perform coronary sinus orifice unroofing through the right atrium under a guide using a bougie. The persistent left superior vena cava was divided. Bidirectional Glenn anastomosis and edge-to-edge common atrioventricular valve repair were concomitantly performed. After a 1-year follow-up period, the patient is alive and well without any ischemic event.
Takabayashi
Shin
S
Department of Thoracic and Cardiovascular Surgery, Mie University Graduate School of Medicine, 2-174 Edobashi, Tsu, Mie 514-8507, Japan. shin1111@clin.medic.mie-u.ac.jp
Shimpo
Hideto
H
Yokoyama
Kazuto
K
D000015:Abnormalities, Multiple; D006348:Cardiac Surgical Procedures; D003330:Coronary Vessel Anomalies / Q000601:surgery*; D004310:Double Outlet Right Ventricle / Q000601:surgery; D006344:Heart Septal Defects, Atrial / Q000601:surgery; D006345:Heart Septal Defects, Ventricular / Q000601:surgery; D006801:Humans; D007223:Infant; D008297:Male; D011666:Pulmonary Valve Stenosis / Q000601:surgery; D014683:Vena Cava, Superior / Q000002:abnormalities* / Q000601:surgery*