title: [A case of lymphangioleiomyomatosis found due to chylous ascites, pleural effusion and pelvic lymphadenopathy].
abstract: We report a case of lymphangioleiomyomatosis, complaining initially of abdominal distension due to massive chylous ascites. The patient was a 28-year-old woman in whom abdominal ultrasound had strongly suggested the existence of both pelvic lymphadenopathy and massive ascites, the latter subsequently turning out to be chylous. Pelvic lymph node biopsy yielded a diagnosis of lymphangioleiomyomatosis. High-resolution computed tomography (HRCT) of the chest showed no remarkable findings except for very few cystic changes in the lung parenchyma. Pulmonary function had remained normal except for a temporary constrictive pattern when chylous pleural effusion developed. No airflow obstruction was detected on pulmonary function tests. Although lymphangioleiomyomatosis is often associated with pulmonary symptoms, we should bear in mind the possibility of lymphangioleiomyomatosis even in the absence of such symptoms when facing any woman of child-bearing age with abdominal chylous ascites of unknown etiology.
authors.affiliation: Department of Respiratory Medicine, Hamamatsu Medical Center.
authors.forename: Toshiaki
authors.initials: T
authors.lastname: Yano
authors.forename: Ikko
authors.initials: I
authors.lastname: Hasizume
authors.forename: Norio
authors.initials: N
authors.lastname: Kasamatsu
authors.forename: Toshiya
authors.initials: T
authors.lastname: Kato
authors.forename: Masahiko
authors.initials: M
authors.lastname: Shibata
authors.forename: Norihiro
authors.initials: N
authors.lastname: Ashinuma
authors.forename: Ken
authors.initials: K
authors.lastname: Kobayashi
authors.forename: Tadashi
authors.initials: T
authors.lastname: Yasuda
authors.forename: Akira
authors.initials: A
authors.lastname: Nakamura
mesh_terms: D000328:Adult; D002915:Chylous Ascites / Q000150:complications*; D005260:Female; D006801:Humans; D018192:Lymphangioleiomyomatosis / Q000175:diagnosis*; D008206:Lymphatic Diseases / Q000150:complications*; D010388:Pelvis; D010996:Pleural Effusion / Q000150:complications*