title: Anetodermic mastocytosis: response to PUVA therapy.
abstract: Mastocytosis is a group of disorders characterized by the accumulation of mast cells in different tissues and organs. The skin is the most frequently involved organ (90% of cases) where mastocytosis may show a heterogenic clinical expression. Anetodermic lesions are an unusual clinical presentation of mastocytosis. We report a case of anetodermic mastocytosis in a 26-year-old man, with sparse lesions and a benign course. PUVA therapy obtained excellent results in this case. Darier's sign should be investigated in patients with anetodermic lesions of unclear origin in order to exclude cutaneous mastocytosis.
authors.affiliation: Department of Dermatology, Hospital Juan Canalejo, La Coruña, Spain. del_pozo@canalejo.org
authors.forename: Jesús
authors.initials: J
authors.lastname: Del Pozo
authors.forename: María Teresa Yebra
authors.initials: MT
authors.lastname: Pimentel
authors.forename: Sabela
authors.initials: S
authors.lastname: Paradela
authors.forename: Manuel
authors.initials: M
authors.lastname: Almagro
authors.forename: Walter
authors.initials: W
authors.lastname: Martínez
authors.forename: Eduardo
authors.initials: E
authors.lastname: Fonseca
mesh_terms: D000328:Adult; D003937:Diagnosis, Differential; D006801:Humans; D008297:Male; D034701:Mastocytosis, Cutaneous / Q000175:diagnosis* / Q000188:drug therapy* / Q000473:pathology; D011701:PUVA Therapy