Parry Romberg's disease with intractable partial epilepsy.
Parry Romberg's syndrome is an uncommon disorder characterized by atrophy of skin and subcutaneous tissue of one side of face. It has neurologic sequel. The commonest of which is epilepsy. Here, we present a 17-year old girl with features of Parry Romberg's disease with intractable epilepsy. Her seizures have stopped with systemic corticosteroids. This treatment response, together with previous reports is suggestive of an autoimmune basis to this disorder. Thus the epilepsy in some such cases may be steroid responsive.
Haldar
Amit
A
Department of Neurology, Vivekananda Institute of Medical Sciences and Ramkrishna Mission Seva Pratisthan, Sarat Bose Road, Kolkata, India. docamithaldar@rediffmail.com
Mukherjee
Arabinda
A
D000293:Adolescent; D000893:Anti-Inflammatory Agents / Q000627:therapeutic use; D000927:Anticonvulsants / Q000627:therapeutic use; D004351:Drug Resistance; D004828:Epilepsies, Partial / Q000150:complications* / Q000188:drug therapy*; D005150:Facial Hemiatrophy / Q000150:complications* / Q000188:drug therapy; D005260:Female; D006801:Humans; D011239:Prednisolone / Q000627:therapeutic use
D000893:Anti-Inflammatory Agents; D000927:Anticonvulsants; D011239:Prednisolone