Mirizzi syndrome type IV associated with cholecystocolic fistula: a very rare condition--report of a case.
BACKGROUND
Mirizzi syndrome is a rare complication of prolonged cholelithiasis with presence of large, impacted gallstone into the Hartman's pouch, causing chronic extrinsic compression of common bile duct (CBD). Fistula formation between the CBD and the gallbladder may represent an outcome of that condition. According to Mirizzi's classification and Csendes's subclassification, Mirizzi syndrome type IV represents the most uncommon type (4%). Spontaneous biliary-enteric fistulas have also been rarely reported (1.2-5%) in a large series of cholecystectomies. Cholecystocolic fistula is the most infrequent biliary enteric fistula, causing significant morbidity and representing a diagnostic challenge.


METHODS
We describe a very rare, to our knowledge, combination of Mirizzi syndrome type IV and cholecystocolic fistula. A 52 year old male, presented to our clinic complaining of episodic diarrhea (monthly episodes lasting 16 days), high temperature (38 degrees C-39 degrees C), right upper quadrant pain without jaundice. The definitive diagnosis was made intraoperatively. Magnetic Resonance Imaging (MRI) and Endoscopic Retrograde Cholangiopancreatography (ERCP) demonstrated the presence of Mirizzi syndrome with cholecystocolic fistula formation. The patient was operated upon, and cholecystectomy, cholecystocolic fistula excision and Roux-en-Y biliary-enteric anastomosis were undertaken with excellent post-operative course.


CONCLUSIONS
Appropriate biliary tree imaging with ERCP and MRI/MRCP is essential for the diagnosis of Mirizzi syndrome and its complications. Cholecystectomy, fistula excision and biliary-enteric anastomosis with Roux-en-Y loop appears to be the most appropriate surgical intervention in order to avoid damage to Calot's triangle anatomic elements. Particularly in our case, ERCP was a valuable diagnostic tool that Mirizzi syndrome type IV and cholecystocolic fistula.
Chatzoulis
George
G
Department of Surgery, 424 Military Hospital Thessaloniki, Greece. surgchatz@yahoo.gr
Kaltsas
Andreas
A
Danilidis
Lazaros
L
Dimitriou
John
J
Pachiadakis
Ioannis
I
D001658:Biliary Fistula / Q000150:complications* / Q000601:surgery; D002760:Cholangiopancreatography, Endoscopic Retrograde; D042883:Choledocholithiasis / Q000150:complications* / Q000601:surgery; D003108:Colonic Diseases / Q000150:complications* / Q000601:surgery; D003135:Common Bile Duct / Q000473:pathology; D003137:Common Bile Duct Diseases / Q000150:complications* / Q000601:surgery; D003251:Constriction, Pathologic; D006801:Humans; D007412:Intestinal Fistula / Q000150:complications* / Q000601:surgery; D008279:Magnetic Resonance Imaging; D008297:Male; D008875:Middle Aged; D013577:Syndrome