A case with heterotaxy reaching the Fontan procedure after unifocalizations.
One patient with major aorto-pulmonary collateral arteries and heterotaxy underwent staged unifocalizations, and eventually the staged Fontan completion. Subsequent to the bidirectional Glenn procedure, the left pulmonary artery was once thrombozed, but successfully treated. The progressively regurgitant common atrioventricular valve needed repair twice during the course. Pulmonary arterial pressure was 11 mm Hg 1 year after the Fontan procedure.
Tsunekawa
Tomohiro
T
Ishizaka
Toru
T
Uemura
Hideki
H
Kagisaki
Koji
K
Hagino
Ikuo
I
Yagihara
Toshikatsu
T
D000015:Abnormalities, Multiple / Q000000981:diagnostic imaging / Q000601:surgery*; D002648:Child; D002675:Child, Preschool; D003097:Collateral Circulation; D018729:Fontan Procedure; D006330:Heart Defects, Congenital / Q000000981:diagnostic imaging / Q000601:surgery*; D006801:Humans; D008297:Male; D018633:Pulmonary Atresia / Q000000981:diagnostic imaging / Q000601:surgery*; D011859:Radiography