title: Aortic arch aneurysm of Takayasu arteritis associated with entero-Behçet disease.
abstract: We report a case of a ruptured aortic arch aneurysm due to Takayasu arteritis concomitant with entero-Behçet disease. A 53-year-old woman with total left lung atelectasis underwent emergency total aortic arch replacement with a modified Bentall operation and elephant trunk procedure. The postoperative course was highly eventful. A pseudoaneurysm of the left coronary button occurred with mediastinitis due to fistula of the left bronchus into the remnant of the aneurysmal wall. The left main trunk was reconstructed with a saphenous vein graft. The left bronchial fistula into the esophagus was exposed and an esophageal stent was placed. Finally, the saphenous vein graft ruptured and the patient expired. The autopsy diagnosis was Takayasu arteritis. This is the first reported case of concomitant Takayasu arteritis and entero-Behçet disease.
authors.affiliation: Department of Cardiothoracic Surgery, Nagoya University Graduate School of Medicine, Nagoya, Japan.
authors.forename: Yoshimori
authors.initials: Y
authors.lastname: Araki
authors.forename: Toshiaki
authors.initials: T
authors.lastname: Akita
authors.forename: Akihiko
authors.initials: A
authors.lastname: Usui
authors.forename: Ryoichi
authors.initials: R
authors.lastname: Ichihashi
authors.forename: Masafumi
authors.initials: M
authors.lastname: Ito
authors.forename: Yuichi
authors.initials: Y
authors.lastname: Ueda
mesh_terms: D017542:Aneurysm, Ruptured / Q000000981:diagnostic imaging / Q000453:epidemiology*; D001011:Aorta / Q000473:pathology; D017545:Aortic Aneurysm, Thoracic / Q000000981:diagnostic imaging / Q000453:epidemiology*; D001528:Behcet Syndrome / Q000453:epidemiology*; D015897:Comorbidity; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D007410:Intestinal Diseases / Q000453:epidemiology*; D008875:Middle Aged; D001261:Pulmonary Atelectasis / Q000000981:diagnostic imaging; D011859:Radiography; D013625:Takayasu Arteritis / Q000453:epidemiology* / Q000473:pathology