title: A case of unilateral sensorineural hearing loss caused by a venous malformation of the internal auditory canal.
abstract: Intracranial vascular malformations can be classified as telangiectasis, varices, cavernous malformations, venous malformations (VMs), or arteriovenous malformations. VMs are congenital vascular malformations of the brain thought to be anomalies of the normal venous drainage. VMs are the most common intracranial vascular malformations documented by brain imaging and by autopsy series. However, vascular lesions of the internal auditory canal (IAC) are extremely rare. We report here a case of a VM arising within the IAC and expanding to the brainstem, causing a unilateral profound sensorineural hearing loss (SNHL). To the best of our knowledge, this is the first documented case of a VM as a rare cause of a unilateral SNHL in a child.
authors.affiliation: Department of Otolaryngology, Daegu Fatima Hospital, 576-31 Shinam 4 Dong, Dong Gu, Daegu 701-600, Republic of Korea.
authors.forename: Hyung Jun
authors.initials: HJ
authors.lastname: Shim
authors.forename: Dae Keun
authors.initials: DK
authors.lastname: Song
authors.forename: Soo Whan
authors.initials: SW
authors.lastname: Lee
authors.forename: Dong Yik
authors.initials: DY
authors.lastname: Lee
authors.forename: Jun Ho
authors.initials: JH
authors.lastname: Park
authors.forename: Jong Heon
authors.initials: JH
authors.lastname: Shin
authors.forename: SungHee
authors.initials: S
authors.lastname: Kim
mesh_terms: D001165:Arteriovenous Malformations / Q000150:complications* / Q000175:diagnosis; D001933:Brain Stem / Q000473:pathology; D002675:Child, Preschool; D007758:Ear, Inner / Q000473:pathology*; D006319:Hearing Loss, Sensorineural / Q000175:diagnosis / Q000209:etiology*; D046088:Hearing Loss, Unilateral / Q000175:diagnosis / Q000209:etiology* / Q000503:physiopathology*; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D012720:Severity of Illness Index