Intracranial medulloepithelioma. A case report and review of the literature.
Medulloepithelioma is a rare primitive neuroectodermal tumour of the central nervous system usually developing in childhood, displaying highly malignant behaviour, with early progression or recurrence. The Authors report a new case of intracranial medulloepithelioma removed from the right cerebellar hemisphere of a 13-year-old boy who showed unspecific signs of intracranial hypertension. Based on a review of the thirty seven cases reported in the literature, they analyse the clinical, histological, immunohistochemical, ultrastructural and therapeutic features of this rare nervous system tumour.
Mekni
A
A
Department of Pathology, Hospital La Rabta, 1007 Bab Saadoun Tunis, Tunisia. aminamekninouira@yahoo.fr
Ferchichi
L
L
Kallel
J
J
Braham
E
E
Bellil
K
K
Bellil
S
S
Haouet
S
S
Zitouna
M
M
Khaldi
M
M
Nidhameddine
K
K
D000293:Adolescent; D001932:Brain Neoplasms / Q000473:pathology / Q000628:therapy; D006801:Humans; D008297:Male; D018242:Neuroectodermal Tumors, Primitive / Q000473:pathology / Q000628:therapy; D010296:Parietal Lobe; D013702:Temporal Lobe