Geste antagonistes in idiopathic lower cranial dystonia.
Geste antagonistes, or sensory tricks, are well described in focal dystonia affecting the neck, hand, and face. Improvement in dystonic movements is typically maintained while the trick is performed, but disappears when the geste ends. We investigated the phenomenological features of geste antagoniste maneuvers in 19 patients with idiopathic lower cranial dystonia who were prospectively evaluated over a period of 6 years. Of the 19, 10 were men, mean age of onset was 49.8 years, and the most commonly involved lower cranial area was the jaw (10 patients). In most patients, dystonia was task-specific. Taking advantage of the improvement with a sensory geste, we manufactured oral appliances that mimicked the geste in 8 patients, and 3 continue to use it.
Lo
Steven E
SE
The Neurological Institute, Columbia University Medical Center, New York, New York, USA.
Gelb
Michael
M
Frucht
Steven J
SJ
D000328:Adult; D000368:Aged; D020821:Dystonic Disorders / Q000503:physiopathology* / Q000534:rehabilitation; D004576:Electromyography; D005260:Female; D005868:Gestures; D006801:Humans; D008297:Male; D008875:Middle Aged; D009068:Movement; D011187:Posture