Osler-Weber-Rendu disease with esophageal varices and hepatic nodular change.
A 72-year-old male visited our hospital for further evaluation of esophageal varices. Telangiectasias were present in the stomach. He had recurrent epistaxis, which was also confirmed in his family's medical history. We diagnosed this case as Osler-Weber-Rendu disease. He had concomitant with hepatic nodular change. Abdominal angiography showed arterio-portal (A-P) shunts, superior mesenteric artery (SMA)-superior mesenteric vein (SMV) shunt, extension of SMV, and dilated and meandering portal vein. Esophageal varices were treated by endoscopic variceral ligation (EVL) and argon plasma coagulation (APC) therapy for prophylaxis of bleeding.
Goto
Takashi
T
Department of Gastroenterology, Akita University School of Medicine. takashi@doc.med.akita-u.ac.jp
Dohmen
Takahiro
T
Yoneyama
Kazuo
K
Monma
Ayako
A
Ohshima
Shigetoshi
S
Shibuya
Tomomi
T
Kataoka
Ei
E
Segawa
Daisuke
D
Sato
Wataru
W
Takeuchi
Satoko
S
Anezaki
Yumiko
Y
Ishii
Hajime
H
Yamada
Ikuhiro
I
Komatsu
Masafumi
M
Watanabe
Sumio
S
D000368:Aged; D004844:Epistaxis / Q000209:etiology; D004932:Esophageal and Gastric Varices / Q000175:diagnosis / Q000209:etiology* / Q000628:therapy; D020022:Genetic Predisposition to Disease; D006801:Humans; D008107:Liver Diseases / Q000175:diagnosis / Q000209:etiology* / Q000628:therapy; D008297:Male; D013683:Telangiectasia, Hereditary Hemorrhagic / Q000150:complications* / Q000175:diagnosis / Q000235:genetics / Q000628:therapy