Severely obstructed totally anomalous pulmonary venous return with residual connection to the left atrium.
Totally anomalous pulmonary venous return may present diagnostic difficulty to clinicians, as it often appears similar to severe neonatal pulmonary disease. We describe a neonate who presented with severely obstructed pulmonary venous return, but with a residual venous connection to the left atrium. The unusual anatomy confounded the diagnosis. To our knowledge, this particular permutation has not previously been described. Our experience indicates that echocardiographic interrogation should be repeated in cases where there is no response to conventional therapy, and all individual pulmonary veins should be observed carefully.
Loh
Lik Eng
LE
Cardiothoracic Unit, Great Ormond Street Hospital for Sick Children, London, United Kingdom.
Brown
Katherine
K
Marek
Jan
J
D005260:Female; D006330:Heart Defects, Congenital / Q000000981:diagnostic imaging*; D006801:Humans; D007231:Infant, Newborn; D011667:Pulmonary Veins / Q000002:abnormalities*; D011668:Pulmonary Veno-Occlusive Disease / Q000000981:diagnostic imaging* / Q000473:pathology; D014463:Ultrasonography