title: Giant Eustachian valve and left ventricular systolic dysfunction in a patient with non-dilated amyloid cardiomyopathy.
abstract: Amyloid cardiomyopathy is characterized by non-dilated thick-walled left ventricular, thickening of interventricular septum and right ventricular free wall, biatrial enlargement associated with granular 'sparkling' appearance of the myocardium. Typically, decreased left ventricular compliance results in abnormal diastolic functions but left ventricular systolic functions are preserved until late in the course of the illness when left ventricle starts to dilate culminating into dilated cardiomyopathy. We present a 77-year-old patient who had typical echocardiographic features of amyloid heart disease, a giant Eustachian valve resembling cor triatriatum dexter and left ventricular systolic dysfunction without associated left ventricular dilatation.
authors.affiliation: Department of Cardiovascular Disease, Western Pennsylvania Hospital/Temple University Program, 4800 Friendship Avenue, Pittsburgh, PA 15224, USA. sandeeparora24@hotmail.com
authors.forename: Sandeep
authors.initials: S
authors.lastname: Arora
authors.forename: Madhavi
authors.initials: M
authors.lastname: Kadiyala
authors.forename: LeRoy
authors.initials: L
authors.lastname: Moore
mesh_terms: D000368:Aged; D000686:Amyloidosis / Q000150:complications*; D009202:Cardiomyopathies / Q000000981:diagnostic imaging* / Q000209:etiology; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D013599:Systole; D014463:Ultrasonography; D014682:Vena Cava, Inferior / Q000000981:diagnostic imaging*; D055422:Venous Valves / Q000000981:diagnostic imaging; D018487:Ventricular Dysfunction, Left / Q000000981:diagnostic imaging*