Primary Ewing's sarcoma/primitive neuroectodermal tumor of the kidney. An infrequent finding.
OBJECTIVE
Ewing's sarcoma/Primitive neuroectodermal tumor (ES/PNET) is an extraordinarily rare primary tumor in the kidney. We re-port herein the clinical, histological, and immunohisto-chemical features of a primary renal ES/PNET.


METHODS
A 19-year old male referred a two weeks history of constant, colic, left flank pain, and fever. A left radical nephrectomy was performed. Gross pathologic examination showed pink-tan, lobulated solid tumor, localized at the superior pole.


RESULTS
Histologically, the tumor was solid with necrosis. The neoplastic cells showed a small amount of clear cytoplasm, and had vesicular nuclei with small nucleoli. Immunohistochemical studies showed strongly and diffusely positive staining for CD99 in a membranous pattern.


CONCLUSIONS
This case represents a typical ES/ PNET affecting a young male patient. Adequate diagnosis is important because this neoplasm has an aggressive behaviour.
Parada
David
D
Department of Anatomic Pathology, Vargas Hospital, Caracas, Venezuela. parada@cantv.net
Godoy
All
A
Liuzzi
Francisco
F
Pelia
Karla B
KB
Romero
Aramis
A
Parada
Arelí M
AM
D000328:Adult; D006801:Humans; D007680:Kidney Neoplasms / Q000473:pathology*; D008297:Male; D009378:Neoplasms, Multiple Primary / Q000473:pathology*; D018242:Neuroectodermal Tumors, Primitive / Q000473:pathology*; D012512:Sarcoma, Ewing / Q000473:pathology*