Tracheal agenesis type B: further evidence to a lethal congenital tracheal malformation.
Tracheal agenesis is an extremely rare, typically fatal congenital tracheal malformation. Lack of prenatal symptoms and emergent presentation usually lead to a failure to arrive at the correct diagnosis and manage the airway properly before the onset of irreversible cerebral anoxia. We report the case history of an infant born with immediate respiratory failure who was diagnosed with tracheal agenesis. The clinical presentation, embryology, classification, and surgical management are discussed.
Pratap
Akshay
A
Department of Surgery, B.P. Koirala Institute of Health Sciences, Dharan, Nepal. akshay_pratap2000@yahoo.co.in
Saha
Gauri Shankar
GS
Bhattarai
Bal Krishna
BK
Yadav
Rohit Prasad
RP
Nepal
Ajit
A
Bajracharya
Amir
A
Kumar
Anand
A
Adhikary
Shailesh
S
D017809:Fatal Outcome; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D014132:Trachea / Q000002:abnormalities*; D014133:Tracheal Diseases / Q000151:congenital*