title: Adrenocorticotropin-secreting pancreatoblastoma.
abstract: We present a 3-year-old child with Cushing's syndrome due to an ACTH-secreting metastatic pancreatoblastoma. This malignancy is a rare cause of Cushing's syndrome, particularly at pediatric age. We describe her course including the use of ketoconazole to alleviate hypercortisolemia.
authors.affiliation: Pediatric Endocrine, Swedish Physician Division 1101 Madison, Suite # 800, Seattle, WA 98104, USA. gad.kletter@swedish.org
authors.forename: Gad B
authors.initials: GB
authors.lastname: Kletter
authors.forename: David A
authors.initials: DA
authors.lastname: Sweetser
authors.forename: Steven F
authors.initials: SF
authors.lastname: Wallace
authors.forename: Robert S
authors.initials: RS
authors.lastname: Sawin
authors.forename: Joe C
authors.initials: JC
authors.lastname: Rutledge
authors.forename: J Russell
authors.initials: JR
authors.lastname: Geyer
mesh_terms: D000182:ACTH Syndrome, Ectopic / Q000175:diagnosis*; D000324:Adrenocorticotropic Hormone / Q000378:metabolism*; D002675:Child, Preschool; D003480:Cushing Syndrome / Q000175:diagnosis*; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D018193:Neoplasms, Complex and Mixed / Q000175:diagnosis / Q000378:metabolism* / Q000473:pathology; D010190:Pancreatic Neoplasms / Q000175:diagnosis / Q000378:metabolism* / Q000473:pathology
chemical_list: D000324:Adrenocorticotropic Hormone