Anaesthetic management of a woman with autosomal recessive limb-girdle muscular dystrophy for emergency caesarean section.
We report the successful management of a 28-year-old parturient with an autosomal recessive limb-girdle muscular dystrophy with severe restrictive lung disease, who required non-invasive positive pressure ventilation in the third trimester of her pregnancy. At 37 weeks' gestation she had combined spinal-epidural anaesthesia for emergency caesarean section and had an uncomplicated intra- and postoperative course. The anaesthetic management is discussed and the literature briefly reviewed.
Allen
T
T
Department of Anaesthesia, South Manchester University Hospital, Manchester, UK. ticka98@btinternet.com
Maguire
S
S
D000328:Adult; D000767:Anesthesia, Epidural / Q000379:methods*; D000773:Anesthesia, Obstetrical / Q000379:methods*; D000775:Anesthesia, Spinal / Q000379:methods*; D019162:Anesthetics, Combined / Q000627:therapeutic use; D002585:Cesarean Section; D004638:Emergency Treatment; D005260:Female; D005808:Genes, Recessive; D006801:Humans; D008171:Lung Diseases / Q000150:complications / Q000628:therapy; D049288:Muscular Dystrophies, Limb-Girdle / Q000150:complications* / Q000235:genetics; D011175:Positive-Pressure Respiration; D011247:Pregnancy; D011248:Pregnancy Complications
D019162:Anesthetics, Combined