Management of urethral hemangiomas associated with Klippel-Trenaunay-Weber syndrome by endoscopic sclerotherapy.
Klippel-Trenaunay-Weber syndrome (KTS) is an unusual congenital anomaly characterized by cutaneous hemangiomas, varicosities and bony hypertrophy of the extremities. Herein the case is reported of a 24-year-old man with urethral bleeding from hemangiomas associated with KTS that were successfully managed by endoscopic sclerotherapy. A 23-G puncture needle was inserted into the bleeding vein to inject a 5% solution of monoethanolamine oleate (Oldamine), which is typically used for sclerotherapy of esophageal vasix. At a 4-month follow-up, the patient only had slightly bloodstained urethral discharge, and is doing well. This is the first case reporting endoscopic sclerotherapy for a KTS-associated urethral hemangioma.
Terada
Naoki
N
Department of Urology, Osaka Red Cross Hospital 5-30 Fudegasaki-cho, Tennoji-ku, Osaka 543-8555, Japan. nterado@kuhp.kyoto-u.ac.jp
Arakaki
Ryuichiro
R
Okada
Yoshiyuki
Y
Kaneko
Yoshiyuki
Y
Nishimura
Kazuo
K
D000328:Adult; D004724:Endoscopy; D006391:Hemangioma / Q000150:complications* / Q000628:therapy*; D006801:Humans; D007715:Klippel-Trenaunay-Weber Syndrome / Q000150:complications*; D008297:Male; D015911:Sclerotherapy / Q000379:methods*; D014523:Urethral Neoplasms / Q000150:complications* / Q000628:therapy*