Isolated pseudohypoplasia of the right ventricle.
We present a case of a 12-year-old girl with severe cyanosis due to abnormal moderator band producing a hidden trabecular component of the right ventricle, mimicking isolated hypoplasia of the right ventricle. A marked hypoplasia was confirmed by echocardiography and catheterization. At operation an anomalously thickened moderator band obstructing the apical infundibulum was found. Repair consisted of a section of the moderator band and closure of the atrial septal defect. Postoperatively the right ventricle showed normal dimension and function.
Pastor
Esteban
E
Division of Pediatric Cardiology, Hospital de Cruces, Barakaldo, Spain.
Aramendi
José I
JI
Luis
Maite
M
Voces
Roberto
R
Rodríguez
Miguel A
MA
Galdeano
José M
JM
D000328:Adult; D000741:Anemia, Aplastic / Q000209:etiology*; D006328:Cardiac Catheterization; D002648:Child; D003490:Cyanosis / Q000209:etiology; D003971:Diastole; D006344:Heart Septal Defects, Atrial / Q000601:surgery*; D006801:Humans; D011859:Radiography; D013599:Systole; D016896:Treatment Outcome; D018497:Ventricular Dysfunction, Right / Q000000981:diagnostic imaging / Q000503:physiopathology*