[Percutaneous closure of veno-venous fistulae after total cavopulmonary derivation: a case report].
The authors report the case of a boy with a complex congenital heart malformation with a dextro-isomerism or Ivemark's syndrome. After several palliative procedures, a total cavopulmonary derivation was performed at the age of 11 years with implantation of a fenestrated tube between the inferior vena cava and the right pulmonary artery. The fenestration was closed two years later. At about 15 years of age, progressive systemic desaturation was observed; cardiac catheterisation with angiography showed a large number of intra-hepatic veno-venous collaterals draining into a large left suprahepatic vein which drained into the right atrium connected to the systemic ventricle. The largest fistula was embolised with a 20 mm Amplatzer Duct Occluder and two others with 14 x 12 and 10 x 8 Amplatzer Duct Occluders. The saturation rose from 75% to 94%. After 6 months' follow-up, the child is asymptomatic and the systemic saturation is 90%.
Basquin
A
A
Service de cardiologie pédiatrique, Hôpital Necker Enfants Malades 149 rue de Sèvres 75743 Paris cedex 15.
Sidi
D
D
Boudjemline
Y
Y
D000293:Adolescent; D004621:Embolization, Therapeutic / Q000295:instrumentation / Q000379:methods*; D005500:Follow-Up Studies; D018610:Heart Bypass, Right; D006330:Heart Defects, Congenital / Q000601:surgery*; D006503:Hepatic Veins / Q000473:pathology*; D006801:Humans; D008099:Liver / Q000098:blood supply; D008297:Male; D012857:Situs Inversus / Q000473:pathology; D013577:Syndrome; D016157:Vascular Fistula / Q000628:therapy*; D014682:Vena Cava, Inferior / Q000473:pathology