Undifferentiated pleomorphic sarcoma of the orbital region.
Undifferentiated pleomorphic sarcoma (formerly known as malignant fibrous histiocytoma) has been established as an entity in the WHO-classification of soft tissue tumors since 2002. Before this the term "malignant fibrous histiocytoma" has been a collective term for soft tissue malignancies that had no distinct components and included most soft tissue sarcomas (40%). With the new classification they account for only about 5%, and tumors arising in the head and neck contribute only about 1-3% of all undifferentiated pleomorphic sarcomas. We report a rare case in which the orbital region was involved.
Müller-Richter
Urs D A
UD
Department of Oral and Maxillofacial Surgery, University Hospital Regensburg, Franz-Josef-Strauss-Allee 11, 93053 Regensburg, Germany. urs.mueller-richter@klinik.uni-regensburg.de
Kohlhof
Julia Katinka
JK
Reichert
Torsten E
TE
Roldán
J Camilo
JC
D000369:Aged, 80 and over; D005260:Female; D051677:Histiocytoma, Malignant Fibrous / Q000000981:diagnostic imaging / Q000473:pathology / Q000532:radiotherapy / Q000601:surgery; D006801:Humans; D009364:Neoplasm Recurrence, Local; D009918:Orbital Neoplasms / Q000000981:diagnostic imaging / Q000473:pathology / Q000532:radiotherapy / Q000601:surgery; D011859:Radiography; D012074:Remission Induction