Bilateral lens subluxation in a case of lipoid proteinosis.
We report a patient who presented with pain, redness, and diminution of vision in the right eye and low vision in the left eye. Ophthalmologic examination showed characteristic eyelid lesions, anterior dislocation of the crystalline lens in the right eye, and nasal subluxation in the left eye. The patient's voice was hoarse, and he had skin lesions. After histopathologic examination of the skin biopsy, lipoid proteinosis (LP) was diagnosed. Bilateral pars plana lensectomy was performed. The ophthalmic manifestations of LP are discussed.
Dr. Rajendra Prasad Centre for Ophthalmic Sciences, All India Institute of Medical Sciences, New Delhi, India. drsubratamandal@gmail.com
Subrata
S
Mandal
Paromita
P
Dutta
Pradeep
P
Venkatesh
Rajesh
R
Sinha
Manu
M
Kukreja
Satpal
S
Garg
D000328:Adult; D006801:Humans; D007906:Lens Subluxation / Q000209:etiology* / Q000601:surgery; D008065:Lipoid Proteinosis of Urbach and Wiethe / Q000150:complications* / Q000175:diagnosis; D008297:Male; D012867:Skin / Q000473:pathology