How not to do it: restrictive thoracic dystrophy after pectus excavatum repair.
The purpose of our paper is to call attention to acquired restrictive thoracic dystrophy (ARTD), an iatrogenic disease. The condition may occur following correction of pectus excavatum in young patients and is characterized by a reduced and restricted rib cage, usually with some recurrence of the deformity. The authors personal experience with five such patients includes analysis of their operative notes, radiographs, and long-term follow up. These, as well as literary, data indicate that the cause of ARTD is not that the operation is performed at an early age, but that inappropriate surgical technique was performed that may include radical chondrocostal resection, extirpation of growth centers, and suturing together of the perichondrial strips retrosternally, consequentially causing cartilaginous growth behind the sternum. A well-designed, conservative operation may be safely performed at any age, including in children less than 4 years old.
Robicsek
Francis
F
Department of Thoracic and Cardiovascular Surgery, Carolinas Heart Institute, Carolinas Medial Center, 1000 Blythe Blvd., Charlotte, NC 28203, USA. tjohn@sanger-clinic.com
Fokin
Alexander A
AA