Pulmonary atresia with intact ventricular septum coexisting with coarctation of the aorta.
A newborn with pulmonary atresia, intact ventricular septum, and a bicommissural aortic valve underwent percutaneous pulmonary valvotomy at 1 day of age. Severe coarctation of the aorta became apparent only after spontaneous closure of the ductus arteriosus at 5 weeks of age, requiring repair by surgical end-to-end anastomosis. This is the first report of a child with pulmonary atresia with intact ventricular septum in association with coarctation of the aorta.
Mackie
Andrew S
AS
Division of Cardiology, Montreal Children's Hospital, 2300 Tupper Street, Montreal, Quebec, Canada H3H 1P3. andrew.mackie@muhc.mcgill.ca
Lang
Peter
P
Powell
Andrew J
AJ
D001017:Aortic Coarctation / Q000453:epidemiology*; D002404:Catheterization; D015897:Comorbidity; D004200:Diseases in Twins / Q000000981:diagnostic imaging; D005260:Female; D005315:Fetal Diseases / Q000000981:diagnostic imaging; D006346:Heart Septum; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D011247:Pregnancy; D018633:Pulmonary Atresia / Q000453:epidemiology* / Q000628:therapy; D016216:Ultrasonography, Prenatal