Metastatic PEComa arising from renal angiomyolipoma: MRI findings.
The perivascular epithelioid cell tumor (PEComa) is a neoplasm composed primarily of HMB-45-positive epithelioid cells with a perivascular distribution. Both benign and malignant PEComas have been reported in diverse anatomic locations. We report the MRI features of a metastatic PEComa to the liver that originated within a renal angiomyolipoma (AML).
El Jack
Amr K
AK
Department of Radiology, Hospital of the University of Pennsylvania, Philadelphia, Pennsylvania 19104, USA. amr.eljack@uphs.upenn.edu
Tomaszewski
John E
JE
Haller
Daniel G
DG
Siegelman
Evan S
ES
D000328:Adult; D018207:Angiomyolipoma / Q000175:diagnosis* / Q000473:pathology*; D003937:Diagnosis, Differential; D015622:Epithelioid Cells / Q000473:pathology*; D006801:Humans; D007680:Kidney Neoplasms / Q000473:pathology*; D008113:Liver Neoplasms / Q000175:diagnosis* / Q000556:secondary*; D008279:Magnetic Resonance Imaging / Q000379:methods*; D008297:Male