[Single-stage laparoscopic adrenalectomy and pancreatic cyst exsicion in a patient with von Hippel-Lindau disease].
BACKGROUND
Von Hippel-Lindau disease is a dominant autosomic hereditary condition, characterized by cerebellar hemangioblastomas, retinal animas and visceral cysts and tumors. We report a case of a patient with Von Hippel-Lindau in which we performed a single-stage laparoscopic adrenalectomy for a pheochromocytoma and pancreatic cyst excision.


METHODS
A 20 year old male patient with Von Hippel Lindau disease underwent laparoscopic adrenalectomy for a 5 cm left adrenal mass. A 3 cm cystic lesion was found of the tail of the pancreas and was resected completely laparoscopically during the same operative procedure.


RESULTS
Total operative time was 120 minutes. There were no operative or postoperative complications. Blood loss was < 50 mL and hospital stay was 3 days. The histopathologic result was adrenal pheochromocytoma and pancreatic mucous microcystic cystoadenoma.


CONCLUSIONS
Laparoscopy allows surgical approach of patients with simultaneous lesions in several abdominal solid viscera, like Von Hippel Lindau disease. This case represents the first report of one-stage laparoscopic adrenalectomy and pancreatic cyst excision.
Unidad de Endourología y Laparoscopia Urológica Clínica Santa María, Universidad de Chile. octaviocastillo@vtr.net
O
O
Castillo
M
M
Kerkebe
G
G
Vitagliano
L
L
Arellano
D000310:Adrenal Gland Neoplasms / Q000150:complications* / Q000601:surgery*; D000315:Adrenalectomy / Q000379:methods*; D000328:Adult; D006801:Humans; D010535:Laparoscopy / Q000379:methods*; D008297:Male; D010181:Pancreatic Cyst / Q000150:complications* / Q000601:surgery*; D010673:Pheochromocytoma / Q000150:complications* / Q000601:surgery*; D006623:von Hippel-Lindau Disease / Q000150:complications*