Endovascular abdominal aortic aneurysm repair in a patient with Ehlers-Danlos syndrome.
Ehlers-Danlos syndrome is a connective tissue disorder caused by abnormal collagen synthesis. Vascular complications, including aneurysm formation and spontaneous arterial perforations, are difficult to manage surgically and result in significant operative mortality due to blood vessel fragility. We describe the first reported successful endovascular abdominal aortic aneurysm repair in a patient with Ehlers-Danlos syndrome. We discuss the advantages endovascular surgery offers over open surgery in these patients. We believe that endovascular repair of abdominal aortic aneurysms preferentially over open repair merits consideration in patients with Ehlers-Danlos syndrome.
Cardiac, Vascular, and Thoracic Surgery Associates, Falls Church, VA 22033, USA. maseerbade@hotmail.com
Maseer A
MA
Bade
Luis A
LA
Queral
Dipankar
D
Mukherjee
Li Sheng
LS
Kong
D000368:Aged; D017544:Aortic Aneurysm, Abdominal / Q000000981:diagnostic imaging / Q000209:etiology / Q000601:surgery*; D001027:Aortography; D019917:Blood Vessel Prosthesis Implantation; D004535:Ehlers-Danlos Syndrome / Q000150:complications* / Q000000981:diagnostic imaging; D005260:Female; D006801:Humans; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome