[Epidemiology and surveillance system of prion disease in Japan].
The current surveillance system by the Creutzfeldt-Jakob disease (CJD) Surveillance Committee, Japan, started in April 1999, and 836 patients with prion diseases had been registered until September 2006, including sporadic CJD (78 %), inherited prion disease (14 %), and infectious prion disease (8 %). The infectious prion disease included a patient with variant CJD and 68 patients with dura mater graft-associated CJD (dCJD). Combined with the dCJD patients identified by previous surveillance systems, the total number of dCJD was counted to be 124.
Noguchi-Shinohara
Moeko
M
Department of Neurology and Neurobiology of Aging, Kanazawa University Graduate School of Medical Science.
Hamaguchi
Tsuyoshi
T
Yamada
Masahito
M
D017668:Age of Onset; D007562:Creutzfeldt-Jakob Syndrome / Q000145:classification / Q000175:diagnosis / Q000453:epidemiology* / Q000635:transmission; D003430:Cross-Sectional Studies; D018563:Disease Notification; D005260:Female; D006801:Humans; D007564:Japan / Q000453:epidemiology; D008297:Male; D012015:Reference Standards; D012737:Sex Factors