title: Coeliac axis thrombosis after surgical correction of spinal deformity in type VI Ehlers-Danlos syndrome: a case report and review of the literature.
abstract: METHODS
  An unusual case of postoperative thrombosis of celiac artery in a patient of Type VI Ehlers-Danlos syndrome (EDS) with severe kyphotic deformity is reported.
  
  
  OBJECTIVE
  To describe an unusual complication of celiac artery thrombosis following surgical correction of kyphotic deformity in Type VI EDS.
  
  
  BACKGROUND
  Neurologic deficit following surgical correction for kyphoscoliotic deformities in patients with Type VI has been reported in 4 cases previously. There has been no previous report of combined celiac artery thrombosis leading to infarction of major abdominal organs along with quadriparesis below C7-C8.
  
  
  METHODS
  Case report and literature review.
  
  
  RESULTS
  Subsequent to a 2-stage surgical correction with posterior instrumentation and fusion of spine, this patient with Type VI EDS developed celiac artery thrombosis leading to infarction of major abdominal organs. At laparotomy, he required hemihepatectomy, splenectomy, cholecystectomy, and a repair of gastric perforation. Following his abdominal catastrophe, he developed quadriparesis possibly due to anterior spinal artery ischemia.
  
  
  CONCLUSIONS
  Spine surgeons treating Type VI EDS with progressive kyphoscoliosis should be aware of such an unusual complication of celiac artery occlusion in late postoperative period. Preoperative antithrombotic medication should be monitored carefully to avoid such catastrophic complication. The prognosis remains poor following anterior spinal artery ischemia due to infarction or thrombosis.
authors: University Hospital of Wales, Heath Park, Cardiff, UK. ukdeb86@hotmail.com
authors: Ujjwal K
authors: UK
authors: Debnath
authors: Hemant
authors: H
authors: Sharma
authors: Darren
authors: D
authors: Roberts
authors: N
authors: N
authors: Kumar
authors: Sashin
authors: S
authors: Ahuja
mesh_terms: D000328:Adult; D002445:Celiac Artery / Q000000981:diagnostic imaging*; D004535:Ehlers-Danlos Syndrome / Q000150:complications / Q000000981:diagnostic imaging* / Q000601:surgery; D006801:Humans; D007738:Kyphosis / Q000150:complications / Q000000981:diagnostic imaging* / Q000601:surgery; D008297:Male; D011183:Postoperative Complications / Q000000981:diagnostic imaging*; D011859:Radiography; D013927:Thrombosis / Q000000981:diagnostic imaging* / Q000209:etiology