Unilateral restrictive ophthalmoplegia and enophthalmos associated with an intraorbital tissue band.
Fibrosis of the extraocular muscles can be congenital or acquired. Acquired causes include trauma, myositis, thyroid eye disease, infection, and metastases. Congenital fibrosis of the extraocular muscles (CFEOM) runs in families and is known to have a genetic basis. It has been classified by Brown, Hansen, and Harley et al into the five following types: general fibrosis syndrome; fibrosis of the inferior rectus (IR) with blepharoptosis; strabismus fixus; vertical retraction syndrome; and unilateral fibrosis, blepharoptosis, and enophthalmos syndrome. In this report, a case of unilateral fibrosis with enophthalmos and blepharoptosis due to a fibrous band is described.
Murthy
Ramesh
R
Department of Pediatric Ophthalmology and Strabismus, LV Prasad Eye Institute, LV Prasad Marg, Banjara Hills, Hyderabad, Andhra Pradesh, India. rameshmurthy@lvpei.org
D000328:Adult; D001763:Blepharoptosis / Q000209:etiology; D015841:Enophthalmos / Q000209:etiology*; D005260:Female; D005355:Fibrosis / Q000151:congenital / Q000000981:diagnostic imaging; D006801:Humans; D009801:Oculomotor Muscles / Q000000981:diagnostic imaging / Q000473:pathology*; D009886:Ophthalmoplegia / Q000209:etiology*; D009916:Orbital Diseases / Q000150:complications* / Q000000981:diagnostic imaging; D014057:Tomography, X-Ray Computed