[Kartagener sindrome (primary ciliary dyskinesia). Report of a case and literature review].
Kartagener syndrome (a clinical variant of primary ciliary dyskinesia) is a recessive autossomical disease characterized by the triad of chronic sinusitis, bronchiectasis and situs inversus with dextrocardia. We report one case described in a 8 years old boy who besides presented a seromucous otitis and bronchitis of repetition. Finally we performed a short bibliographic review at respect of this uncommon pathology.
Pino Rivero
V
V
Hospital Campo Arañuelo, Navalmoral de la Mata, Cáceres. vicentepinorivero@terra.com
Pardo Romero
G
G
Iglesias González
R J
RJ
Rodríguez Carmona
M
M
del Castillo Beneyto
F
F
D001706:Biopsy; D001987:Bronchiectasis / Q000000981:diagnostic imaging; D001991:Bronchitis / Q000175:diagnosis; D002648:Child; D002908:Chronic Disease; D003914:Dextrocardia / Q000000981:diagnostic imaging; D006801:Humans; D007619:Kartagener Syndrome / Q000175:diagnosis / Q000000981:diagnostic imaging / Q000473:pathology; D008168:Lung / Q000473:pathology; D008297:Male; D010031:Otitis / Q000175:diagnosis; D013902:Radiography, Thoracic; D012852:Sinusitis / Q000175:diagnosis