Anesthesia management in a child with PHACE syndrome and agenesis of bilateral internal carotid arteries.
This is the first case report of successful anesthesia management in a high-risk neurological procedure in a patient with PHACE syndrome. PHACE syndrome is rare but an important clinical entity. Anesthesiologists should be aware of the neurological, otolaryngogical, and vascular risk associated with this syndrome.
Javault
Aurélia
A
Department of Anesthesiology and Intensive Care Unit, Hospices Civils de Lyon, Hôpital Louis Pradel, Claude Bernard University, Lyon, France.
Metton
Olivier
O
Raisky
Olivier
O
Bompard
Dominique
D
Hachemi
Mohamed
M
Gamondes
Delphine
D
Ninet
Jean
J
Neidecker
Jean
J
Lehot
Jean-Jacques
JJ
Cannesson
Maxime
M
D000015:Abnormalities, Multiple / Q000235:genetics / Q000473:pathology*; D000768:Anesthesia, General; D000769:Anesthesia, Inhalation; D001013:Aorta, Thoracic / Q000002:abnormalities* / Q000601:surgery; D002343:Carotid Artery, Internal / Q000002:abnormalities*; D002675:Child, Preschool; D005260:Female; D006801:Humans; D018810:Magnetic Resonance Angiography; D016343:Monitoring, Intraoperative / Q000295:instrumentation / Q000379:methods; D011229:Preanesthetic Medication; D013577:Syndrome