title: Hepatoblastoma with congenital absence of the portal vein - a case report.
abstract: A 17-month-old girl who had been followed up as an extremely-low-birth-weight infant presented with hepatoblastoma in the right lobe of her liver. Preoperative angiography revealed an absence of the portal vein, and the visceral venous return was through the left renal vein into the inferior vena cava. No liver dysfunction and no jaundice were found; however, a marked elevation of the alpha-fetoprotein level was noted. She underwent a typical right hepatic lobectomy successfully after chemotherapy and has no evidence of recurrence 6 months after surgery.
authors.affiliation: Department of Pediatric Surgery, Shizuoka Children's Hospital, Shizuoka, Japan. s_kawano@naa.att.ne.jp
authors.forename: S
authors.initials: S
authors.lastname: Kawano
authors.forename: S
authors.initials: S
authors.lastname: Hasegawa
authors.forename: N
authors.initials: N
authors.lastname: Urushihara
authors.forename: T
authors.initials: T
authors.lastname: Okazaki
authors.forename: A
authors.initials: A
authors.lastname: Yoshida
authors.forename: J
authors.initials: J
authors.lastname: Kusafuka
authors.forename: J
authors.initials: J
authors.lastname: Mimaya
authors.forename: Y
authors.initials: Y
authors.lastname: Horikoshi
authors.forename: K
authors.initials: K
authors.lastname: Aoki
authors.forename: M
authors.initials: M
authors.lastname: Hamazaki
mesh_terms: D000792:Angiography; D003937:Diagnosis, Differential; D005260:Female; D005500:Follow-Up Studies; D006498:Hepatectomy / Q000379:methods; D018197:Hepatoblastoma / Q000150:complications* / Q000175:diagnosis / Q000601:surgery; D006801:Humans; D007223:Infant; D008113:Liver Neoplasms / Q000150:complications* / Q000175:diagnosis / Q000601:surgery; D010690:Phlebography; D011169:Portal Vein / Q000002:abnormalities*; D014057:Tomography, X-Ray Computed; D054079:Vascular Malformations / Q000150:complications* / Q000175:diagnosis / Q000601:surgery