title: Associated malformations in Morgagni hernia.
abstract: Morgagni hernia (MH) is a congenital herniation of the abdominal organs through the subcostosternal portion of the diaphragm. It is a rare type of diaphragmatic hernia that has been associated with other congenital anomalies. The purpose of this clinical review was to determine the incidence of associated anomalies in patients with MH at a major pediatric referral center. The medical records of all patients with the diagnosis of MH were reviewed retrospectively between 1983 and 2006. The age, sex, side of herniation, presenting symptoms and signs, associated anomalies, radiologic features, intraoperative findings, postoperative course, complications, and mortality were recorded. There were 11 males and 5 females. The average age of the patients was 34.5 months (range 2 months-14 years). Twelve patients (75%) had at least one associated congenital malformation and eight (66.6%) of them had multiple anomalies. Six (37.5%) patients had a chromosomal anomaly, Down's syndrome in five and Turner syndrome in one. MH has a high incidence of associated congenital malformations.
authors.affiliation: Department of Pediatric Surgery, Dicle University Medical Faculty, 21280 Diyarbakir, Turkey. mkcigdem@hotmail.com
authors.forename: Murat Kemal
authors.initials: MK
authors.lastname: Cigdem
authors.forename: Abdurrahman
authors.initials: A
authors.lastname: Onen
authors.forename: Hanifi
authors.initials: H
authors.lastname: Okur
authors.forename: Selcuk
authors.initials: S
authors.lastname: Otcu
mesh_terms: D000015:Abnormalities, Multiple; D000293:Adolescent; D002648:Child; D002675:Child, Preschool; D013505:Digestive System Surgical Procedures / Q000379:methods; D004314:Down Syndrome / Q000175:diagnosis; D005260:Female; D005500:Follow-Up Studies; D006548:Hernia, Diaphragmatic / Q000000981:diagnostic imaging / Q000601:surgery; D065630:Hernias, Diaphragmatic, Congenital; D006801:Humans; D008297:Male; D011379:Prognosis; D013902:Radiography, Thoracic; D012189:Retrospective Studies; D014057:Tomography, X-Ray Computed; D014424:Turner Syndrome / Q000175:diagnosis*