Neurofibromatosis type 2 associated with multiple cranial nerve schwannomas: a case report.
A 16-year-old male patient complained of right-sided tinnitus and mild deafness of one-month history. He also had a family history of neurofibromatosis type 2 and a history of a prior operation for left vestibular schwannoma a year ago. Otoneurologic examination revealed moderate sensorineural hearing loss. Magnetic resonance imaging demonstrated multiple extra-axial enhancing masses in the vicinity of both hypoglossal nerves, the right vestibular nerve, the left vestibular nerve, the right trigeminal, the left occulomotor, and the right abducens nerves. These findings were evaluated as multiple cranial nerve schwannomas. The case was considered a rare manifestation of neurofibromatosis type 2 without any concomitant abnormality in the central nervous system. Symptomatic medical treatment was initiated and the patient was referred to the neurosurgery department.
Halefoğlu
Ahmet Mesrur
AM
Department of Radiology, Sişli Etfal Training and Research Hospital, Istanbul, Turkey. halefoglu@hotmail.com
D000293:Adolescent; D003056:Cochlear Nerve; D003390:Cranial Nerve Neoplasms / Q000150:complications / Q000175:diagnosis* / Q000473:pathology; D003638:Deafness / Q000209:etiology; D003937:Diagnosis, Differential; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D009442:Neurilemmoma / Q000150:complications / Q000175:diagnosis* / Q000473:pathology; D016518:Neurofibromatosis 2 / Q000150:complications / Q000175:diagnosis* / Q000473:pathology; D014012:Tinnitus / Q000209:etiology